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Complete deafness

MedGen UID:
108418
•Concept ID:
C0581883
•
Disease or Syndrome
Synonyms: Complete Hearing Loss; Hearing Loss, Complete
SNOMED CT: Complete deafness (8531006)

Definition

Total inability to hear sounds in one or both ears. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVComplete deafness

Professional guidelines

PubMed

Social and health factors associated with adverse treatment outcomes among people with multidrug-resistant tuberculosis in Sierra Leone: a national, retrospective cohort study.
Kamara RF, Saunders MJ, Sahr F, Losa-Garcia JE, Foray L, Davies G, Wingfield T
Lancet Glob Health 2022 Apr;10(4):e543-e554. doi: 10.1016/S2214-109X(22)00004-3. PMID: 35303463Free PMC Article
Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Autoimmune sensorineural hearing loss: clinical course and treatment outcome.
Loveman DM, de Comarmond C, Cepero R, Baldwin DM
Semin Arthritis Rheum 2004 Oct;34(2):538-43. doi: 10.1016/j.semarthrit.2003.10.002. PMID: 15505769

Recent clinical studies

Etiology

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Surgical treatment of adult cholesteatoma: long-term follow-up using total reconstruction procedure without staging.
Edfeldt L, Strömbäck K, Kinnefors A, Rask-Andersen H
Acta Otolaryngol 2013 Jan;133(1):28-34. Epub 2012 Oct 31 doi: 10.3109/00016489.2012.707333. PMID: 23113656
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828
Cavernous angiomas within the internal auditory canal.
Samii M, Nakamura M, Mirzai S, Vorkapic P, Cervio A
J Neurosurg 2006 Oct;105(4):581-7. doi: 10.3171/jns.2006.105.4.581. PMID: 17044562

Diagnosis

Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Early canakinumab therapy for the sensorineural deafness in a family with Muckle-Wells syndrome due to a novel mutation of NLRP3 gene.
Iida Y, Wakiguchi H, Okazaki F, Nakamura T, Yasudo H, Kubo M, Sugahara K, Yamashita H, Suehiro Y, Okayama N, Hashimoto K, Iwamoto N, Kawakami A, Aoki Y, Takada H, Ohga S, Hasegawa S
Clin Rheumatol 2019 Mar;38(3):943-948. Epub 2018 Oct 18 doi: 10.1007/s10067-018-4331-8. PMID: 30338413
Neurosyphilis and classical music: the great composers and "The Great Imitator".
Pedro MKF, Germiniani FMB, Teive HAG
Arq Neuropsiquiatr 2018 Nov;76(11):791-794. doi: 10.1590/0004-282X20180122. PMID: 30570024
Surgical treatment of adult cholesteatoma: long-term follow-up using total reconstruction procedure without staging.
Edfeldt L, Strömbäck K, Kinnefors A, Rask-Andersen H
Acta Otolaryngol 2013 Jan;133(1):28-34. Epub 2012 Oct 31 doi: 10.3109/00016489.2012.707333. PMID: 23113656
Cavernous angiomas within the internal auditory canal.
Samii M, Nakamura M, Mirzai S, Vorkapic P, Cervio A
J Neurosurg 2006 Oct;105(4):581-7. doi: 10.3171/jns.2006.105.4.581. PMID: 17044562

Therapy

Clinical characteristics, the diagnostic criteria and management recommendation of otitis media with antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (OMAAV) proposed by Japan Otological Society.
Harabuchi Y, Kishibe K, Tateyama K, Morita Y, Yoshida N, Okada M, Kunimoto Y, Watanabe T, Inagaki A, Yoshida T, Imaizumi M, Nakamura T, Matsunobu T, Kobayashi S, Iino Y, Murakami S, Takahashi H, Tono T
Auris Nasus Larynx 2021 Feb;48(1):2-14. Epub 2020 Aug 5 doi: 10.1016/j.anl.2020.07.004. PMID: 32768313
Early canakinumab therapy for the sensorineural deafness in a family with Muckle-Wells syndrome due to a novel mutation of NLRP3 gene.
Iida Y, Wakiguchi H, Okazaki F, Nakamura T, Yasudo H, Kubo M, Sugahara K, Yamashita H, Suehiro Y, Okayama N, Hashimoto K, Iwamoto N, Kawakami A, Aoki Y, Takada H, Ohga S, Hasegawa S
Clin Rheumatol 2019 Mar;38(3):943-948. Epub 2018 Oct 18 doi: 10.1007/s10067-018-4331-8. PMID: 30338413
Threshold monitoring of intraoperative auditory steady-state responses for ossiculoplasty surgery.
Liu Q, Feng G, Shang Y, Chi C, Qiao Y, Gao Z
Acta Otolaryngol 2018 Jul;138(7):625-632. Epub 2018 Mar 5 doi: 10.1080/00016489.2018.1436767. PMID: 29504434
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828
Intravenous azithromycin-induced ototoxicity.
Bizjak ED, Haug MT 3rd, Schilz RJ, Sarodia BD, Dresing JM
Pharmacotherapy 1999 Feb;19(2):245-8. doi: 10.1592/phco.19.3.245.30930. PMID: 10030778

Prognosis

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Suggested deafness during hypnosis and simulation of hypnosis compared to a distraction and control condition: A study on subjective experience and cortical brain responses.
Franz M, Schmidt B, Hecht H, Naumann E, Miltner WHR
PLoS One 2020;15(10):e0240832. Epub 2020 Oct 29 doi: 10.1371/journal.pone.0240832. PMID: 33119665Free PMC Article
Surgical treatment of adult cholesteatoma: long-term follow-up using total reconstruction procedure without staging.
Edfeldt L, Strömbäck K, Kinnefors A, Rask-Andersen H
Acta Otolaryngol 2013 Jan;133(1):28-34. Epub 2012 Oct 31 doi: 10.3109/00016489.2012.707333. PMID: 23113656
Chemotherapy: present and future.
Terry AR, Plotkin SR
Otolaryngol Clin North Am 2012 Apr;45(2):471-86, x. doi: 10.1016/j.otc.2011.12.013. PMID: 22483828
Autoimmune sensorineural hearing loss: clinical course and treatment outcome.
Loveman DM, de Comarmond C, Cepero R, Baldwin DM
Semin Arthritis Rheum 2004 Oct;34(2):538-43. doi: 10.1016/j.semarthrit.2003.10.002. PMID: 15505769

Clinical prediction guides

Analysis of Clinical Prognosis of Totally Deaf Idiopathic Sudden Sensorineural Hearing Loss in Different Ages.
You D, You Q, Liu Y
Altern Ther Health Med 2023 Nov;29(8):506-511. PMID: 37652422
Neuromonitoring of the cochlear nerve during vestibular schwannoma resection and simultaneous cochlear implantation.
Weiss NM, Großmann W, Schraven SP, Oberhoffner T, Mlynski R
HNO 2021 Aug;69(Suppl 2):82-87. Epub 2021 May 21 doi: 10.1007/s00106-021-00997-3. PMID: 34019139
High rifampicin-resistant TB cure rates and prevention of severe ototoxicity after replacing the injectable by linezolid in early stage of hearing loss.
Souleymane MB, Piubello A, Lawan IM, Hassane-Harouna S, Assao-Neino MM, Soumana A, Hamidou-Harouna Z, Gagara-Issoufou A, Ortuño-Gutiérrez N, Roggi A, Schwoebel V, Mamadou S, Lynen L, De Jong B, Van Deun A, Decroo T
Eur Respir J 2021 Jan;57(1) Epub 2021 Jan 21 doi: 10.1183/13993003.02250-2020. PMID: 32703777
A Subjective Rating Scale for Initial Assessment of Sudden Unilateral Sensorineural Hearing Loss.
Ungar OJ, Cavel O, Oron Y, Wengier A, Wasserzug O, Handzel O
Audiol Neurootol 2017;22(3):154-159. Epub 2017 Oct 10 doi: 10.1159/000479723. PMID: 28992622
Targeted disruption of the Kvlqt1 gene causes deafness and gastric hyperplasia in mice.
Lee MP, Ravenel JD, Hu RJ, Lustig LR, Tomaselli G, Berger RD, Brandenburg SA, Litzi TJ, Bunton TE, Limb C, Francis H, Gorelikow M, Gu H, Washington K, Argani P, Goldenring JR, Coffey RJ, Feinberg AP
J Clin Invest 2000 Dec;106(12):1447-55. doi: 10.1172/JCI10897. PMID: 11120752Free PMC Article

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