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GTR Home > Conditions/Phenotypes > Erythrokeratodermia variabilis et progressiva 5

Summary

Erythrokeratodermia variabilis et progressiva-5 (EKVP5) is an autosomal recessive skin disorder characterized by progressive development of symmetrically distributed hyperkeratotic plaques with palmoplantar hyperkeratosis and nail thickening (Shah et al., 2017). [from OMIM]

Available tests

6 tests are in the database for this condition.

Genes See tests for all associated and related genes

  • Also known as: EKVP5, HB3, Hb-3, KRTHB3, MNLIX, KRT83
    Summary: keratin 83

Clinical features

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