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GTR Home > Conditions/Phenotypes > Rhizomelic dysplasia, Ain-Naz type

Summary

The Ain-Naz type of rhizomelic dysplasia (RHZDAN) is characterized by severe short stature with marked rhizomelic shortening of the limbs, platyspondyly, and large hands and feet relative to height (Ain et al., 2021). [from OMIM]

Genes See tests for all associated and related genes

  • Also known as: GNA1, GNPNAT, Gpnat1, RHZDAN, GNPNAT1
    Summary: glucosamine-phosphate N-acetyltransferase 1

Clinical features

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