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Congenital intestinal transport defect

MedGen UID:
1826131
Concept ID:
C5681747
Disease or Syndrome
Orphanet: ORPHA104003

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital intestinal transport defect

Professional guidelines

PubMed

Avitzur Y, Jimenez L, Martincevic I, Acra S, Courtney-Martin G, Gray M, Hope K, Muise A, Prieto Jimenez PM, Taylor N, Thiagarajah JR, Martín MG; PediCODE Consortium
Am J Clin Nutr 2024 Jul;120(1):17-33. Epub 2024 May 9 doi: 10.1016/j.ajcnut.2024.05.004. PMID: 38734141Free PMC Article
Berni Canani R, Terrin G, Cardillo G, Tomaiuolo R, Castaldo G
J Pediatr Gastroenterol Nutr 2010 Apr;50(4):360-6. doi: 10.1097/MPG.0b013e3181d135ef. PMID: 20216094
Nadler HL, Hazinski T
Compr Ther 1979 Jun;5(6):7-12. PMID: 156613

Recent clinical studies

Etiology

Simmonds NJ, Southern KW, De Wachter E, De Boeck K, Bodewes F, Mainz JG, Middleton PG, Schwarz C, Vloeberghs V, Wilschanski M, Bourrat E, Chalmers JD, Ooi CY, Debray D, Downey DG, Eschenhagen P, Girodon E, Hickman G, Koitschev A, Nazareth D, Nick JA, Peckham D, VanDevanter D, Raynal C, Scheers I, Waller MD, Sermet-Gaudelus I, Castellani C; ECFS Diagnostic Network Working Group
J Cyst Fibros 2024 Jul;23(4):590-602. Epub 2024 Mar 19 doi: 10.1016/j.jcf.2024.03.008. PMID: 38508949
Younis M, Rastogi R, Chugh A, Rastogi S, Aly H
Clin Perinatol 2020 Jun;47(2):301-321. Epub 2020 Mar 5 doi: 10.1016/j.clp.2020.02.007. PMID: 32439113
Chouikh T, Mottet N, Lenoir M, Chaussy Y
J Pediatr 2017 Nov;190:284-284.e1. Epub 2017 Sep 13 doi: 10.1016/j.jpeds.2017.07.003. PMID: 28917956
Terrin G, Tomaiuolo R, Passariello A, Elce A, Amato F, Di Costanzo M, Castaldo G, Canani RB
Int J Mol Sci 2012;13(4):4168-4185. Epub 2012 Mar 29 doi: 10.3390/ijms13044168. PMID: 22605972Free PMC Article
Grunewald S, Matthijs G, Jaeken J
Pediatr Res 2002 Nov;52(5):618-24. doi: 10.1203/00006450-200211000-00003. PMID: 12409504

Diagnosis

Younis M, Rastogi R, Chugh A, Rastogi S, Aly H
Clin Perinatol 2020 Jun;47(2):301-321. Epub 2020 Mar 5 doi: 10.1016/j.clp.2020.02.007. PMID: 32439113
Thiagarajah JR, Kamin DS, Acra S, Goldsmith JD, Roland JT, Lencer WI, Muise AM, Goldenring JR, Avitzur Y, Martín MG; PediCODE Consortium
Gastroenterology 2018 Jun;154(8):2045-2059.e6. Epub 2018 Apr 12 doi: 10.1053/j.gastro.2018.03.067. PMID: 29654747Free PMC Article
Chouikh T, Mottet N, Lenoir M, Chaussy Y
J Pediatr 2017 Nov;190:284-284.e1. Epub 2017 Sep 13 doi: 10.1016/j.jpeds.2017.07.003. PMID: 28917956
Terrin G, Tomaiuolo R, Passariello A, Elce A, Amato F, Di Costanzo M, Castaldo G, Canani RB
Int J Mol Sci 2012;13(4):4168-4185. Epub 2012 Mar 29 doi: 10.3390/ijms13044168. PMID: 22605972Free PMC Article
Grunewald S, Matthijs G, Jaeken J
Pediatr Res 2002 Nov;52(5):618-24. doi: 10.1203/00006450-200211000-00003. PMID: 12409504

Therapy

Li Y, Salfelder A, Schwab KO, Grünert SC, Velten T, Lütjohann D, Villavicencio-Lorini P, Matysiak-Scholze U, Zabel B, Köttgen A, Lausch E
Eur J Hum Genet 2016 Aug;24(9):1274-9. Epub 2016 Jan 27 doi: 10.1038/ejhg.2015.285. PMID: 26813946Free PMC Article
Cools E, Missant C
Acta Anaesthesiol Belg 2014;65(1):1-8. PMID: 24988822
Wang Z, Cao L, Su Y, Wang G, Wang R, Yu Z, Bai X, Ruan C
Am J Hematol 2014 Mar;89(3):320-4. doi: 10.1002/ajh.23619. PMID: 24166850
Nyborg WL
Health Phys 2002 May;82(5):578-87. doi: 10.1097/00004032-200205000-00004. PMID: 12003010
Corbeel L, Van den Berghe G, Jaeken J, Van Tornout J, Eeckels R
Eur J Pediatr 1985 Mar;143(4):284-90. doi: 10.1007/BF00442302. PMID: 3987728

Prognosis

Duclaux-Loras R, Lebreton C, Berthelet J, Charbit-Henrion F, Nicolle O, Revenu des Courtils C, Waich S, Valovka T, Khiat A, Rabant M, Racine C, Guerrera IC, Baptista J, Mahe MM, Hess MW, Durel B, Lefort N, Banal C, Parisot M, Talbotec C, Lacaille F, Ecochard-Dugelay E, Demir AM, Vogel GF, Faivre L, Rodrigues A, Fowler D, Janecke AR, Müller T, Huber LA, Rodrigues-Lima F, Ruemmele FM, Uhlig HH, Del Bene F, Michaux G, Cerf-Bensussan N, Parlato M
J Clin Invest 2022 May 16;132(10) doi: 10.1172/JCI154997. PMID: 35575086Free PMC Article
Chouikh T, Mottet N, Lenoir M, Chaussy Y
J Pediatr 2017 Nov;190:284-284.e1. Epub 2017 Sep 13 doi: 10.1016/j.jpeds.2017.07.003. PMID: 28917956
Canani RB, Terrin G
Curr Gastroenterol Rep 2011 Jun;13(3):257-64. doi: 10.1007/s11894-011-0188-6. PMID: 21494839
Miro J, Bard H
Am J Obstet Gynecol 1988 Mar;158(3 Pt 1):555-9. doi: 10.1016/0002-9378(88)90024-5. PMID: 3279785
Holmberg C
Clin Gastroenterol 1986 Jul;15(3):583-602. PMID: 3527496

Clinical prediction guides

Duclaux-Loras R, Lebreton C, Berthelet J, Charbit-Henrion F, Nicolle O, Revenu des Courtils C, Waich S, Valovka T, Khiat A, Rabant M, Racine C, Guerrera IC, Baptista J, Mahe MM, Hess MW, Durel B, Lefort N, Banal C, Parisot M, Talbotec C, Lacaille F, Ecochard-Dugelay E, Demir AM, Vogel GF, Faivre L, Rodrigues A, Fowler D, Janecke AR, Müller T, Huber LA, Rodrigues-Lima F, Ruemmele FM, Uhlig HH, Del Bene F, Michaux G, Cerf-Bensussan N, Parlato M
J Clin Invest 2022 May 16;132(10) doi: 10.1172/JCI154997. PMID: 35575086Free PMC Article
Brusq C, Mieusset R, Hamdi SM
Andrology 2022 Feb;10(2):262-269. Epub 2021 Sep 27 doi: 10.1111/andr.13106. PMID: 34510807
Yagi M, Kohno M, Asagiri K, Ikeda T, Okada T, Kanada S, Kawashima S, Goto Y, Takano S, Yasufuku M, Wada M
Pediatr Surg Int 2015 Oct;31(10):955-62. Epub 2015 Aug 30 doi: 10.1007/s00383-015-3775-z. PMID: 26319695
Umaña LA, Magoulas P, Bi W, Bacino CA
Am J Med Genet A 2011 Dec;155A(12):3071-4. Epub 2011 Nov 3 doi: 10.1002/ajmg.a.34296. PMID: 22052692
Kere J
Novartis Found Symp 2006;273:2-11; discussion 11-8, 261-4. PMID: 17120758

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