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Primary bone dysplasia with increased bone density

MedGen UID:
1842790
Concept ID:
C5680274
Disease or Syndrome
Synonym: Sclerosing Bone Dysplasias
 
Orphanet: ORPHA93444

Professional guidelines

PubMed

Sridharan K, Sivaramakrishnan G
Curr Clin Pharmacol 2018;13(3):190-198. doi: 10.2174/1574884713666180829143927. PMID: 30160216
O'Shea FD, Boyle E, Salonen DC, Ammendolia C, Peterson C, Hsu W, Inman RD
Arthritis Care Res (Hoboken) 2010 Apr;62(4):447-54. doi: 10.1002/acr.20168. PMID: 20391497
Armstrong DG, Newfield JT, Gillespie R
J Pediatr Orthop 1999 Jan-Feb;19(1):122-32. PMID: 9890301

Recent clinical studies

Etiology

Glorieux FH, Langdahl B, Chapurlat R, De Beur SJ, Sutton VR, Poole KES, Dahir KM, Orwoll ES, Willie BM, Mikolajewicz N, Zimmermann E, Hosseinitabatabaei S, Ominsky MS, Saville C, Clancy J, MacKinnon A, Mistry A, Javaid MK
J Bone Miner Res 2024 Sep 2;39(9):1215-1228. doi: 10.1093/jbmr/zjae112. PMID: 39012717Free PMC Article
McGill K, Motamedi D, Azimi N, Horvai A, O'Donnell R
J Radiol Case Rep 2020 Jul;14(7):1-9. Epub 2020 Jul 31 doi: 10.3941/jrcr.v14i7.3920. PMID: 33088414Free PMC Article
Savarirayan R, Tofts L, Irving M, Wilcox W, Bacino CA, Hoover-Fong J, Ullot Font R, Harmatz P, Rutsch F, Bober MB, Polgreen LE, Ginebreda I, Mohnike K, Charrow J, Hoernschemeyer D, Ozono K, Alanay Y, Arundel P, Kagami S, Yasui N, White KK, Saal HM, Leiva-Gea A, Luna-González F, Mochizuki H, Basel D, Porco DM, Jayaram K, Fisheleva E, Huntsman-Labed A, Day J
Lancet 2020 Sep 5;396(10252):684-692. doi: 10.1016/S0140-6736(20)31541-5. PMID: 32891212
Dwan K, Phillipi CA, Steiner RD, Basel D
Cochrane Database Syst Rev 2016 Oct 19;10(10):CD005088. doi: 10.1002/14651858.CD005088.pub4. PMID: 27760454Free PMC Article
Stark Z, Savarirayan R
Orphanet J Rare Dis 2009 Feb 20;4:5. doi: 10.1186/1750-1172-4-5. PMID: 19232111Free PMC Article

Diagnosis

Glorieux FH, Langdahl B, Chapurlat R, De Beur SJ, Sutton VR, Poole KES, Dahir KM, Orwoll ES, Willie BM, Mikolajewicz N, Zimmermann E, Hosseinitabatabaei S, Ominsky MS, Saville C, Clancy J, MacKinnon A, Mistry A, Javaid MK
J Bone Miner Res 2024 Sep 2;39(9):1215-1228. doi: 10.1093/jbmr/zjae112. PMID: 39012717Free PMC Article
McGill K, Motamedi D, Azimi N, Horvai A, O'Donnell R
J Radiol Case Rep 2020 Jul;14(7):1-9. Epub 2020 Jul 31 doi: 10.3941/jrcr.v14i7.3920. PMID: 33088414Free PMC Article
Savarirayan R, Tofts L, Irving M, Wilcox W, Bacino CA, Hoover-Fong J, Ullot Font R, Harmatz P, Rutsch F, Bober MB, Polgreen LE, Ginebreda I, Mohnike K, Charrow J, Hoernschemeyer D, Ozono K, Alanay Y, Arundel P, Kagami S, Yasui N, White KK, Saal HM, Leiva-Gea A, Luna-González F, Mochizuki H, Basel D, Porco DM, Jayaram K, Fisheleva E, Huntsman-Labed A, Day J
Lancet 2020 Sep 5;396(10252):684-692. doi: 10.1016/S0140-6736(20)31541-5. PMID: 32891212
Shaw NJ
Endocr Dev 2015;28:84-100. Epub 2015 Jun 12 doi: 10.1159/000380997. PMID: 26138837
Stark Z, Savarirayan R
Orphanet J Rare Dis 2009 Feb 20;4:5. doi: 10.1186/1750-1172-4-5. PMID: 19232111Free PMC Article

Therapy

Glorieux FH, Langdahl B, Chapurlat R, De Beur SJ, Sutton VR, Poole KES, Dahir KM, Orwoll ES, Willie BM, Mikolajewicz N, Zimmermann E, Hosseinitabatabaei S, Ominsky MS, Saville C, Clancy J, MacKinnon A, Mistry A, Javaid MK
J Bone Miner Res 2024 Sep 2;39(9):1215-1228. doi: 10.1093/jbmr/zjae112. PMID: 39012717Free PMC Article
Leerling AT, Clunie G, Koutrouba E, Dekkers OM, Appelman-Dijkstra NM, Winter EM
Orphanet J Rare Dis 2023 Jul 21;18(1):206. doi: 10.1186/s13023-023-02831-1. PMID: 37480122Free PMC Article
Arshad F, Bishop N
Bone 2021 Jul;148:115914. Epub 2021 Mar 17 doi: 10.1016/j.bone.2021.115914. PMID: 33722772
Savarirayan R, Tofts L, Irving M, Wilcox W, Bacino CA, Hoover-Fong J, Ullot Font R, Harmatz P, Rutsch F, Bober MB, Polgreen LE, Ginebreda I, Mohnike K, Charrow J, Hoernschemeyer D, Ozono K, Alanay Y, Arundel P, Kagami S, Yasui N, White KK, Saal HM, Leiva-Gea A, Luna-González F, Mochizuki H, Basel D, Porco DM, Jayaram K, Fisheleva E, Huntsman-Labed A, Day J
Lancet 2020 Sep 5;396(10252):684-692. doi: 10.1016/S0140-6736(20)31541-5. PMID: 32891212
Dwan K, Phillipi CA, Steiner RD, Basel D
Cochrane Database Syst Rev 2016 Oct 19;10(10):CD005088. doi: 10.1002/14651858.CD005088.pub4. PMID: 27760454Free PMC Article

Prognosis

Ivell R, Heng K, Severn K, Antonio L, Bartfai G, Casanueva FF, Huhtaniemi IT, Giwercman A, Maggi M, O'Connor DB, O'Neill TW, Punab M, Rastrelli G, Slowikowska-Hilczer J, Tournoy J, Vanderschueren D, Wu FCW, Anand-Ivell R
Front Endocrinol (Lausanne) 2022;13:1016107. Epub 2022 Nov 8 doi: 10.3389/fendo.2022.1016107. PMID: 36425465Free PMC Article
Arshad F, Bishop N
Bone 2021 Jul;148:115914. Epub 2021 Mar 17 doi: 10.1016/j.bone.2021.115914. PMID: 33722772
Katugampola H, Saraff V, Kumaran A, Allgrove J, Shaw NJ
Endocr Dev 2015;28:319-413. Epub 2015 Jun 12 doi: 10.1159/000381571. PMID: 26138850
Vergara-Lluri ME, Piatek CI, Pullarkat V, Siddiqi IN, O'Connell C, Feinstein DI, Brynes RK
Hum Pathol 2014 Nov;45(11):2183-91. Epub 2014 Aug 13 doi: 10.1016/j.humpath.2014.07.017. PMID: 25282037
Bradbury LA, Barlow S, Geoghegan F, Hannon RA, Stuckey SL, Wass JA, Russell RG, Brown MA, Duncan EL
Osteoporos Int 2012 Jan;23(1):285-94. Epub 2011 Jul 8 doi: 10.1007/s00198-011-1658-2. PMID: 21739105

Clinical prediction guides

Al Kaissi A, Misof BM, Laccone F, Blouin S, Roschger P, Kircher SG, Shboul M, Mindler GT, Girsch W, Ganger R
Calcif Tissue Int 2021 Nov;109(5):586-595. Epub 2021 May 18 doi: 10.1007/s00223-021-00862-z. PMID: 34003338
Spampinato M, Giallongo C, Romano A, Longhitano L, La Spina E, Avola R, Scandura G, Dulcamare I, Bramanti V, Di Rosa M, Vicario N, Parenti R, Li Volti G, Tibullo D, Palumbo GA
Biomolecules 2021 Jan 19;11(1) doi: 10.3390/biom11010122. PMID: 33477816Free PMC Article
Sridharan K, Sivaramakrishnan G
Curr Clin Pharmacol 2018;13(3):190-198. doi: 10.2174/1574884713666180829143927. PMID: 30160216
Dwan K, Phillipi CA, Steiner RD, Basel D
Cochrane Database Syst Rev 2016 Oct 19;10(10):CD005088. doi: 10.1002/14651858.CD005088.pub4. PMID: 27760454Free PMC Article
Gelman MI
Radiology 1977 Nov;125(2):289-96. doi: 10.1148/125.2.289. PMID: 198844

Recent systematic reviews

Dwan K, Phillipi CA, Steiner RD, Basel D
Cochrane Database Syst Rev 2016 Oct 19;10(10):CD005088. doi: 10.1002/14651858.CD005088.pub4. PMID: 27760454Free PMC Article
Dwan K, Phillipi CA, Steiner RD, Basel D
Cochrane Database Syst Rev 2014 Jul 23;(7):CD005088. doi: 10.1002/14651858.CD005088.pub3. PMID: 25054949
Phillipi CA, Remmington T, Steiner RD
Cochrane Database Syst Rev 2008 Oct 8;(4):CD005088. doi: 10.1002/14651858.CD005088.pub2. PMID: 18843680
MacDonald-Jankowski DS
Dentomaxillofac Radiol 1999 Nov;28(6):357-63. doi: 10.1038/sj/dmfr/4600485. PMID: 10578190

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