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Idiopathic cardiomyopathy

MedGen UID:
18634
•Concept ID:
C0033141
•
Disease or Syndrome
Synonyms: Cardiomyopathies, Primary; Cardiomyopathy, Primary; Disease, Primary Myocardial; Diseases, Primary Myocardial; Myocardial Disease, Primary; Myocardial Diseases, Primary; Primary Cardiomyopathies; Primary Cardiomyopathy; Primary Myocardial Disease; Primary Myocardial Diseases
SNOMED CT: Primary cardiomyopathy (89461002)
 
Monarch Initiative: MONDO:0005110

Definition

Disease of the heart muscle associated with electrical or mechanical dysfunction, in which the heart is the sole or predominantly involved organ. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • Idiopathic cardiomyopathy

Professional guidelines

PubMed

Genetic profile and genotype-phenotype correlations in childhood cardiomyopathy.
Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Anesthetic management of peripartum cardiomyopathy.
Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article

Recent clinical studies

Etiology

Genetic Contribution to End-Stage Cardiomyopathy Requiring Heart Transplantation.
Kim Y, Gunnarsdóttir OB, Viveiros A, Reichart D, Quiat D, Willcox JAL, Zhang H, Chen H, Curran JJ, Kim DH, Urschel S, McDonough B, Gorham J, DePalma SR, Seidman JG, Seidman CE, Oudit GY
Circ Genom Precis Med 2023 Oct;16(5):452-461. Epub 2023 Sep 28 doi: 10.1161/CIRCGEN.123.004062. PMID: 37767697Free PMC Article
Genetic profile and genotype-phenotype correlations in childhood cardiomyopathy.
Wanert C, El Louali F, Al Dybiat S, Nguyen K, Zaffran S, Ovaert C
Arch Cardiovasc Dis 2023 Jun-Jul;116(6-7):309-315. Epub 2023 May 16 doi: 10.1016/j.acvd.2023.04.008. PMID: 37246080
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Panic disorder and idiopathic cardiomyopathy.
Griez EJ, Mammar N, Loirat JC, Djega N, Trochut JN, Bouhour JB
J Psychosom Res 2000 Jun;48(6):585-7. doi: 10.1016/s0022-3999(00)00140-9. PMID: 11033378

Diagnosis

Genetic Contribution to End-Stage Cardiomyopathy Requiring Heart Transplantation.
Kim Y, Gunnarsdóttir OB, Viveiros A, Reichart D, Quiat D, Willcox JAL, Zhang H, Chen H, Curran JJ, Kim DH, Urschel S, McDonough B, Gorham J, DePalma SR, Seidman JG, Seidman CE, Oudit GY
Circ Genom Precis Med 2023 Oct;16(5):452-461. Epub 2023 Sep 28 doi: 10.1161/CIRCGEN.123.004062. PMID: 37767697Free PMC Article
Mechanisms of toxic cardiomyopathy.
Hantson P
Clin Toxicol (Phila) 2019 Jan;57(1):1-9. Epub 2018 Sep 27 doi: 10.1080/15563650.2018.1497172. PMID: 30260248
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Molecular approaches to enteroviral diagnosis in idiopathic cardiomyopathy and myocarditis.
Tracy S, Wiegand V, McManus B, Gauntt C, Pallansch M, Beck M, Chapman N
J Am Coll Cardiol 1990 Jun;15(7):1688-94. doi: 10.1016/0735-1097(90)92846-t. PMID: 2161026

Therapy

Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
Alcoholic cardiomyopathy : The result of dosage and individual predisposition.
Maisch B
Herz 2016 Sep;41(6):484-93. doi: 10.1007/s00059-016-4469-6. PMID: 27582365Free PMC Article
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Molecular approaches to enteroviral diagnosis in idiopathic cardiomyopathy and myocarditis.
Tracy S, Wiegand V, McManus B, Gauntt C, Pallansch M, Beck M, Chapman N
J Am Coll Cardiol 1990 Jun;15(7):1688-94. doi: 10.1016/0735-1097(90)92846-t. PMID: 2161026

Prognosis

Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
Practical management of peripartum cardiomyopathy.
Kim MJ, Shin MS
Korean J Intern Med 2017 May;32(3):393-403. Epub 2017 Apr 14 doi: 10.3904/kjim.2016.360. PMID: 28407464Free PMC Article
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Myocardial biopsy.
Kawai C, Matsumori A, Kawamura K
Annu Rev Med 1980;31:139-57. doi: 10.1146/annurev.me.31.020180.001035. PMID: 6994601

Clinical prediction guides

Anesthetic management of peripartum cardiomyopathy.
Turnbull D
Minerva Anestesiol 2021 Mar;87(3):334-340. Epub 2020 Dec 10 doi: 10.23736/S0375-9393.20.14703-5. PMID: 33300322
Cardiomyopathy and Preeclampsia.
Gammill HS, Chettier R, Brewer A, Roberts JM, Shree R, Tsigas E, Ward K
Circulation 2018 Nov 20;138(21):2359-2366. doi: 10.1161/CIRCULATIONAHA.117.031527. PMID: 30021846
Catheter Ablation Versus Medical Rate Control in Atrial Fibrillation and Systolic Dysfunction: The CAMERA-MRI Study.
Prabhu S, Taylor AJ, Costello BT, Kaye DM, McLellan AJA, Voskoboinik A, Sugumar H, Lockwood SM, Stokes MB, Pathik B, Nalliah CJ, Wong GR, Azzopardi SM, Gutman SJ, Lee G, Layland J, Mariani JA, Ling LH, Kalman JM, Kistler PM
J Am Coll Cardiol 2017 Oct 17;70(16):1949-1961. Epub 2017 Aug 27 doi: 10.1016/j.jacc.2017.08.041. PMID: 28855115
The natural history of acute dilated cardiomyopathy.
Dec GW
Trans Am Clin Climatol Assoc 2014;125:76-86; discussion 86-7. PMID: 25125720Free PMC Article
Cardiomyopathy: molecular and immunological aspects (review).
Takeda N
Int J Mol Med 2003 Jan;11(1):13-6. PMID: 12469210

Recent systematic reviews

Pentoxifylline for heart failure: a systematic review.
Batchelder K, Mayosi BM
S Afr Med J 2005 Mar;95(3):171-5. PMID: 15832667

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