U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Idiopathic pneumonitis syndrome

MedGen UID:
265378
•Concept ID:
C1504431
•
Disease or Syndrome
Synonym: Idiopathic Pneumonia Syndrome
SNOMED CT: Idiopathic pneumonitis syndrome (12381000132107)

Definition

An inflammatory lung disease characterized by diffuse interstitial pneumonitis and alveolitis leading to interstitial fibrosis in the absence of an identifiable infectious agent. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIdiopathic pneumonitis syndrome

Professional guidelines

PubMed

Diagnosis and Management of Myositis-Associated Lung Disease.
Hallowell RW, Danoff SK
Chest 2023 Jun;163(6):1476-1491. Epub 2023 Feb 9 doi: 10.1016/j.chest.2023.01.031. PMID: 36764512
Consensus statement on blocking interleukin-6 receptor and interleukin-6 in inflammatory conditions: an update.
Aletaha D, Kerschbaumer A, Kastrati K, Dejaco C, Dougados M, McInnes IB, Sattar N, Stamm TA, Takeuchi T, Trauner M, van der Heijde D, Voshaar M, Winthrop KL, Ravelli A, Betteridge N, Burmester GR, Bijlsma JW, Bykerk V, Caporali R, Choy EH, Codreanu C, Combe B, Crow MK, de Wit M, Emery P, Fleischmann RM, Gabay C, Hetland ML, Hyrich KL, Iagnocco A, Isaacs JD, Kremer JM, Mariette X, Merkel PA, Mysler EF, Nash P, Nurmohamed MT, Pavelka K, Poor G, Rubbert-Roth A, Schulze-Koops H, Strangfeld A, Tanaka Y, Smolen JS
Ann Rheum Dis 2023 Jun;82(6):773-787. Epub 2022 Aug 11 doi: 10.1136/ard-2022-222784. PMID: 35953263
Acute Eosinophilic Pneumonia. Causes, Diagnosis, and Management.
De Giacomi F, Vassallo R, Yi ES, Ryu JH
Am J Respir Crit Care Med 2018 Mar 15;197(6):728-736. doi: 10.1164/rccm.201710-1967CI. PMID: 29206477

Recent clinical studies

Etiology

Idiopathic Pneumonitis Syndrome After Total Body Irradiation in Pediatric Patients Undergoing Myeloablative Hematopoietic Stem Cell Transplantation: A PENTEC Comprehensive Review.
Ehler ED, Turcotte LM, Skamene S, Baker KS, Das SK, Constine LS, Yuan J, Dusenbery KE
Int J Radiat Oncol Biol Phys 2024 Jun 1;119(2):625-639. Epub 2023 Mar 26 doi: 10.1016/j.ijrobp.2023.02.037. PMID: 36973099
Thiotepa, Etoposide, Cyclophosphamide, Cytarabine, and Melphalan (TECAM) Conditioning Regimen for Autologous Stem Cell Transplantation in Lymphoma.
Grisariu S, Shapira MY, Or R, Avni B
Clin Lymphoma Myeloma Leuk 2018 Apr;18(4):272-279. Epub 2018 Feb 15 doi: 10.1016/j.clml.2018.02.008. PMID: 29500148

Therapy

Idiopathic Pneumonitis Syndrome After Total Body Irradiation in Pediatric Patients Undergoing Myeloablative Hematopoietic Stem Cell Transplantation: A PENTEC Comprehensive Review.
Ehler ED, Turcotte LM, Skamene S, Baker KS, Das SK, Constine LS, Yuan J, Dusenbery KE
Int J Radiat Oncol Biol Phys 2024 Jun 1;119(2):625-639. Epub 2023 Mar 26 doi: 10.1016/j.ijrobp.2023.02.037. PMID: 36973099
Thiotepa, Etoposide, Cyclophosphamide, Cytarabine, and Melphalan (TECAM) Conditioning Regimen for Autologous Stem Cell Transplantation in Lymphoma.
Grisariu S, Shapira MY, Or R, Avni B
Clin Lymphoma Myeloma Leuk 2018 Apr;18(4):272-279. Epub 2018 Feb 15 doi: 10.1016/j.clml.2018.02.008. PMID: 29500148

Prognosis

Idiopathic Pneumonitis Syndrome After Total Body Irradiation in Pediatric Patients Undergoing Myeloablative Hematopoietic Stem Cell Transplantation: A PENTEC Comprehensive Review.
Ehler ED, Turcotte LM, Skamene S, Baker KS, Das SK, Constine LS, Yuan J, Dusenbery KE
Int J Radiat Oncol Biol Phys 2024 Jun 1;119(2):625-639. Epub 2023 Mar 26 doi: 10.1016/j.ijrobp.2023.02.037. PMID: 36973099
Thiotepa, Etoposide, Cyclophosphamide, Cytarabine, and Melphalan (TECAM) Conditioning Regimen for Autologous Stem Cell Transplantation in Lymphoma.
Grisariu S, Shapira MY, Or R, Avni B
Clin Lymphoma Myeloma Leuk 2018 Apr;18(4):272-279. Epub 2018 Feb 15 doi: 10.1016/j.clml.2018.02.008. PMID: 29500148

Clinical prediction guides

Idiopathic Pneumonitis Syndrome After Total Body Irradiation in Pediatric Patients Undergoing Myeloablative Hematopoietic Stem Cell Transplantation: A PENTEC Comprehensive Review.
Ehler ED, Turcotte LM, Skamene S, Baker KS, Das SK, Constine LS, Yuan J, Dusenbery KE
Int J Radiat Oncol Biol Phys 2024 Jun 1;119(2):625-639. Epub 2023 Mar 26 doi: 10.1016/j.ijrobp.2023.02.037. PMID: 36973099

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...