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Progressive retinal degeneration

MedGen UID:
343224
Concept ID:
C1854888
Finding

Professional guidelines

PubMed

Schlegel J, Hoffmann J, Röll D, Müller B, Günther S, Zhang W, Janise A, Vössing C, Fühler B, Neidhardt J, Khanna H, Lorenz B, Stieger K
Transl Res 2019 Jan;203:57-72. Epub 2018 Aug 24 doi: 10.1016/j.trsl.2018.08.006. PMID: 30213530Free PMC Article
Gardner JC, Liew G, Quan YH, Ermetal B, Ueyama H, Davidson AE, Schwarz N, Kanuga N, Chana R, Maher ER, Webster AR, Holder GE, Robson AG, Cheetham ME, Liebelt J, Ruddle JB, Moore AT, Michaelides M, Hardcastle AJ
Hum Mutat 2014 Nov;35(11):1354-62. doi: 10.1002/humu.22679. PMID: 25168334Free PMC Article
Valverde D, Pereiro I, Vallespín E, Ayuso C, Borrego S, Baiget M
Invest Ophthalmol Vis Sci 2009 Mar;50(3):1065-8. Epub 2008 Nov 14 doi: 10.1167/iovs.08-2083. PMID: 19011012

Recent clinical studies

Etiology

Balfoort BM, Van Den Broeck F, Brands MM, van Karnebeek CD, Bergen AA, van den Born LI, Houtkooper RH, Wagenmakers MAEM, De Zaeytijd J, Leroy BP, Boon CJF, Diederen RMH
Graefes Arch Clin Exp Ophthalmol 2024 Nov;262(11):3589-3596. Epub 2024 Jun 7 doi: 10.1007/s00417-024-06540-8. PMID: 38847892Free PMC Article
Suga A, Yoshitake K, Minematsu N, Tsunoda K, Fujinami K, Miyake Y, Kuniyoshi K, Hayashi T, Mizobuchi K, Ueno S, Terasaki H, Kominami T, Nao-I N, Mawatari G, Mizota A, Shinoda K, Kondo M, Kato K, Sekiryu T, Nakamura M, Kusuhara S, Yamamoto H, Yamamoto S, Mochizuki K, Kondo H, Matsushita I, Kameya S, Fukuchi T, Hatase T, Horiguchi M, Shimada Y, Tanikawa A, Yamamoto S, Miura G, Ito N, Murakami A, Fujimaki T, Hotta Y, Tanaka K, Iwata T
Hum Mutat 2022 Dec;43(12):2251-2264. Epub 2022 Nov 7 doi: 10.1002/humu.24492. PMID: 36284460
Mayer SK, Thomas J, Helms M, Kothapalli A, Cherascu I, Salesevic A, Stalter E, Wang K, Datta P, Searby C, Seo S, Hsu Y, Bhattarai S, Sheffield VC, Drack AV
Dis Model Mech 2022 Sep 1;15(9) Epub 2022 Sep 20 doi: 10.1242/dmm.049473. PMID: 36125046Free PMC Article
Zernant J, Lee W, Nagasaki T, Collison FT, Fishman GA, Bertelsen M, Rosenberg T, Gouras P, Tsang SH, Allikmets R
Cold Spring Harb Mol Case Stud 2018 Aug;4(4) Epub 2018 Aug 1 doi: 10.1101/mcs.a002733. PMID: 29848554Free PMC Article
Heckenlively JR
Trans Am Ophthalmol Soc 1987;85:438-70. PMID: 3447340Free PMC Article

Diagnosis

Suga A, Yoshitake K, Minematsu N, Tsunoda K, Fujinami K, Miyake Y, Kuniyoshi K, Hayashi T, Mizobuchi K, Ueno S, Terasaki H, Kominami T, Nao-I N, Mawatari G, Mizota A, Shinoda K, Kondo M, Kato K, Sekiryu T, Nakamura M, Kusuhara S, Yamamoto H, Yamamoto S, Mochizuki K, Kondo H, Matsushita I, Kameya S, Fukuchi T, Hatase T, Horiguchi M, Shimada Y, Tanikawa A, Yamamoto S, Miura G, Ito N, Murakami A, Fujimaki T, Hotta Y, Tanaka K, Iwata T
Hum Mutat 2022 Dec;43(12):2251-2264. Epub 2022 Nov 7 doi: 10.1002/humu.24492. PMID: 36284460
Bonì F, Marino V, Bidoia C, Mastrangelo E, Barbiroli A, Dell'Orco D, Milani M
Biomolecules 2020 Oct 5;10(10) doi: 10.3390/biom10101408. PMID: 33027977Free PMC Article
Weigelt CM, Hahn O, Arlt K, Gruhn M, Jahn AJ, Eßer J, Werner JA, Klein C, Büschges A, Grönke S, Partridge L
Life Sci Alliance 2019 Feb;2(1) Epub 2019 Jan 22 doi: 10.26508/lsa.201800149. PMID: 30670478Free PMC Article
Hofmann L, Palczewski K
Methods Mol Biol 2015;1271:3-18. doi: 10.1007/978-1-4939-2330-4_1. PMID: 25697513Free PMC Article
Friedman TB, Schultz JM, Ahmed ZM, Tsilou ET, Brewer CC
Adv Otorhinolaryngol 2011;70:56-65. Epub 2011 Feb 24 doi: 10.1159/000322473. PMID: 21358186

Therapy

Chan CK, Beaulieu WT, Lujan BJ, Lalezary M, Lent-Schochet D, Lo T, Yiu G
Transl Vis Sci Technol 2023 Sep 1;12(9):1. doi: 10.1167/tvst.12.9.1. PMID: 37656449Free PMC Article
Eltony SA, Mohaseb HS, Ahmed AA, Sayed MM
Tissue Cell 2022 Jun;76:101786. Epub 2022 Mar 16 doi: 10.1016/j.tice.2022.101786. PMID: 35325673
Kumaran N, Michaelides M, Smith AJ, Ali RR, Bainbridge JWB
Br Med Bull 2018 Jun 1;126(1):13-25. doi: 10.1093/bmb/ldy005. PMID: 29506236
Hayasaka S, Kodama T, Ohira A
Br J Nutr 2011 Sep;106(6):801-11. Epub 2011 Jul 18 doi: 10.1017/S0007114511003291. PMID: 21767450
Santos L, Fiona WJ, Walter JH
J Inherit Metab Dis 2006 Feb;29(1):240. doi: 10.1007/s10545-006-0286-z. PMID: 16601905

Prognosis

Balfoort BM, Van Den Broeck F, Brands MM, van Karnebeek CD, Bergen AA, van den Born LI, Houtkooper RH, Wagenmakers MAEM, De Zaeytijd J, Leroy BP, Boon CJF, Diederen RMH
Graefes Arch Clin Exp Ophthalmol 2024 Nov;262(11):3589-3596. Epub 2024 Jun 7 doi: 10.1007/s00417-024-06540-8. PMID: 38847892Free PMC Article
Biswas P, Borooah S, Matsui H, Voronchikhina M, Zhou J, Zawaydeh Q, Raghavendra PB, Ferreyra H, Riazuddin SA, Wahlin K, Frazer KA, Ayyagari R
Hum Mutat 2021 Feb;42(2):189-199. Epub 2020 Dec 13 doi: 10.1002/humu.24146. PMID: 33252167Free PMC Article
Nassisi M, Wohlschlegel J, Liu B, Letellier C, Michiels C, Aubois A, Mohand-Said S, Habas C, Sahel JA, Zeitz C, Audo I
Retina 2021 Apr 1;41(4):872-881. doi: 10.1097/IAE.0000000000002953. PMID: 32826790
Al-Hujaili H, Taskintuna I, Neuhaus C, Bergmann C, Schatz P
Mol Vis 2019;25:851-858. Epub 2019 Dec 19 PMID: 31908403Free PMC Article
Zernant J, Lee W, Nagasaki T, Collison FT, Fishman GA, Bertelsen M, Rosenberg T, Gouras P, Tsang SH, Allikmets R
Cold Spring Harb Mol Case Stud 2018 Aug;4(4) Epub 2018 Aug 1 doi: 10.1101/mcs.a002733. PMID: 29848554Free PMC Article

Clinical prediction guides

Shen C, Yang Q, Chen K, Ma H, Wang X, Tong J, Shen Y, Cui H
Cell Commun Signal 2024 Jul 11;22(1):359. doi: 10.1186/s12964-024-01710-x. PMID: 38992691Free PMC Article
Harripaul R, Morini E, Salani M, Logan E, Kirchner E, Bolduc J, Chekuri A, Currall B, Yadav R, Erdin S, Talkowski ME, Gao D, Slaugenhaupt S
Sci Rep 2024 Jan 4;14(1):570. doi: 10.1038/s41598-023-51137-6. PMID: 38177237Free PMC Article
Suga A, Yoshitake K, Minematsu N, Tsunoda K, Fujinami K, Miyake Y, Kuniyoshi K, Hayashi T, Mizobuchi K, Ueno S, Terasaki H, Kominami T, Nao-I N, Mawatari G, Mizota A, Shinoda K, Kondo M, Kato K, Sekiryu T, Nakamura M, Kusuhara S, Yamamoto H, Yamamoto S, Mochizuki K, Kondo H, Matsushita I, Kameya S, Fukuchi T, Hatase T, Horiguchi M, Shimada Y, Tanikawa A, Yamamoto S, Miura G, Ito N, Murakami A, Fujimaki T, Hotta Y, Tanaka K, Iwata T
Hum Mutat 2022 Dec;43(12):2251-2264. Epub 2022 Nov 7 doi: 10.1002/humu.24492. PMID: 36284460
Satue M, Fuentes JL, Vilades E, Orduna E, Vicente MJ, Cordon B, Perez-Velilla J, Garcia-Campayo J, Garcia-Martin E
Curr Eye Res 2022 Jul;47(7):1061-1067. Epub 2022 Apr 29 doi: 10.1080/02713683.2022.2064513. PMID: 35438020
Biswas P, Borooah S, Matsui H, Voronchikhina M, Zhou J, Zawaydeh Q, Raghavendra PB, Ferreyra H, Riazuddin SA, Wahlin K, Frazer KA, Ayyagari R
Hum Mutat 2021 Feb;42(2):189-199. Epub 2020 Dec 13 doi: 10.1002/humu.24146. PMID: 33252167Free PMC Article

Recent systematic reviews

Paunescu K, Preising MN, Janke B, Wissinger B, Lorenz B
Ophthalmology 2007 Jul;114(7):1348-1357.e1. Epub 2007 Feb 22 doi: 10.1016/j.ophtha.2006.10.034. PMID: 17320181

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