U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Restrictive lung disease

MedGen UID:
43209
•Concept ID:
C0085581
•
Disease or Syndrome
Synonym: Restrictive pulmonary disease
SNOMED CT: Restrictive lung disease (36485005)
 
Monarch Initiative: MONDO:0600029

Definition

Decreased lung volume and inadequate ventilation due to parenchymal lung disorders (e.g., interstitial pulmonary fibrosis) or extrapulmonary disorders (e.g., scoliosis). Patients present with shortness of breath and cough. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRestrictive lung disease

Professional guidelines

PubMed

Physiotherapy management of interstitial lung disease.
Holland AE
J Physiother 2022 Jul;68(3):158-164. Epub 2022 Jun 23 doi: 10.1016/j.jphys.2022.06.006. PMID: 35753970
Respiratory management of children with spinal muscular atrophy (SMA).
Fauroux B, Griffon L, Amaddeo A, Stremler N, Mazenq J, Khirani S, Baravalle-Einaudi M
Arch Pediatr 2020 Dec;27(7S):7S29-7S34. doi: 10.1016/S0929-693X(20)30274-8. PMID: 33357594
Early-onset scoliosis: current treatment.
Cunin V
Orthop Traumatol Surg Res 2015 Feb;101(1 Suppl):S109-18. Epub 2015 Jan 23 doi: 10.1016/j.otsr.2014.06.032. PMID: 25623270

Recent clinical studies

Etiology

Post-Tuberculosis Lung Disease: Clinical Review of an Under-Recognised Global Challenge.
Allwood BW, Byrne A, Meghji J, Rachow A, van der Zalm MM, Schoch OD
Respiration 2021;100(8):751-763. Epub 2021 Jan 5 doi: 10.1159/000512531. PMID: 33401266
Extracardiac complications in adults with congenital heart disease.
Cohen SB, Ginde S, Bartz PJ, Earing MG
Congenit Heart Dis 2013 Sep-Oct;8(5):370-80. Epub 2013 May 13 doi: 10.1111/chd.12080. PMID: 23663434
Alström syndrome.
Marshall JD, Beck S, Maffei P, Naggert JK
Eur J Hum Genet 2007 Dec;15(12):1193-202. Epub 2007 Oct 17 doi: 10.1038/sj.ejhg.5201933. PMID: 17940554
Anti-scl-70.
Basu D, Reveille JD
Autoimmunity 2005 Feb;38(1):65-72. doi: 10.1080/08916930400022947. PMID: 15804707
Obstructive and restrictive lung disease and markers of inflammation: data from the Third National Health and Nutrition Examination.
Mannino DM, Ford ES, Redd SC
Am J Med 2003 Jun 15;114(9):758-62. doi: 10.1016/s0002-9343(03)00185-2. PMID: 12829203

Diagnosis

Post-Tuberculosis Lung Disease: Clinical Review of an Under-Recognised Global Challenge.
Allwood BW, Byrne A, Meghji J, Rachow A, van der Zalm MM, Schoch OD
Respiration 2021;100(8):751-763. Epub 2021 Jan 5 doi: 10.1159/000512531. PMID: 33401266
Respiratory management of children with spinal muscular atrophy (SMA).
Fauroux B, Griffon L, Amaddeo A, Stremler N, Mazenq J, Khirani S, Baravalle-Einaudi M
Arch Pediatr 2020 Dec;27(7S):7S29-7S34. doi: 10.1016/S0929-693X(20)30274-8. PMID: 33357594
A stepwise approach to the interpretation of pulmonary function tests.
Johnson JD, Theurer WM
Am Fam Physician 2014 Mar 1;89(5):359-66. PMID: 24695507
Loosening the bonds of restrictive lung disease.
Pruitt B
Nursing 2008 Aug;38(8):34-9; quiz 39-40. doi: 10.1097/01.NURSE.0000327490.70569.bc. PMID: 18648298
Beals-Hecht syndrome.
Jones JL, Lane JE, Logan JJ, Vanegas ME
South Med J 2002 Jul;95(7):753-5. PMID: 12144083

Therapy

Matrix metalloproteinases as therapeutic targets for idiopathic pulmonary fibrosis.
Craig VJ, Zhang L, Hagood JS, Owen CA
Am J Respir Cell Mol Biol 2015 Nov;53(5):585-600. doi: 10.1165/rcmb.2015-0020TR. PMID: 26121236Free PMC Article
Spinal muscular atrophy.
Iannaccone ST, Smith SA, Simard LR
Curr Neurol Neurosci Rep 2004 Jan;4(1):74-80. doi: 10.1007/s11910-004-0016-6. PMID: 14683633
Obstructive sarcoidosis.
Laohaburanakit P, Chan A
Clin Rev Allergy Immunol 2003 Oct;25(2):115-29. doi: 10.1385/CRIAI:25:2:115. PMID: 14573880
Fluoxetine hydrochloride (Prozac)-induced pulmonary disease.
Gonzalez-Rothi RJ, Zander DS, Ros PR
Chest 1995 Jun;107(6):1763-5. doi: 10.1378/chest.107.6.1763. PMID: 7781383
Effects of hydrocodone bitartrate on breathing pattern of patients with chronic obstructive pulmonary disease and restrictive lung disease.
Sackner MA
Mt Sinai J Med 1984 Apr;51(2):222-6. PMID: 6610123

Prognosis

Post-Tuberculosis Lung Disease: Clinical Review of an Under-Recognised Global Challenge.
Allwood BW, Byrne A, Meghji J, Rachow A, van der Zalm MM, Schoch OD
Respiration 2021;100(8):751-763. Epub 2021 Jan 5 doi: 10.1159/000512531. PMID: 33401266
Respiratory management of children with spinal muscular atrophy (SMA).
Fauroux B, Griffon L, Amaddeo A, Stremler N, Mazenq J, Khirani S, Baravalle-Einaudi M
Arch Pediatr 2020 Dec;27(7S):7S29-7S34. doi: 10.1016/S0929-693X(20)30274-8. PMID: 33357594
A stepwise approach to the interpretation of pulmonary function tests.
Johnson JD, Theurer WM
Am Fam Physician 2014 Mar 1;89(5):359-66. PMID: 24695507
Extracardiac complications in adults with congenital heart disease.
Cohen SB, Ginde S, Bartz PJ, Earing MG
Congenit Heart Dis 2013 Sep-Oct;8(5):370-80. Epub 2013 May 13 doi: 10.1111/chd.12080. PMID: 23663434
Adolescent idiopathic scoliosis.
Rinsky LA, Gamble JG
West J Med 1988 Feb;148(2):182-91. PMID: 3279708Free PMC Article

Clinical prediction guides

Post-Tuberculosis Lung Disease: Clinical Review of an Under-Recognised Global Challenge.
Allwood BW, Byrne A, Meghji J, Rachow A, van der Zalm MM, Schoch OD
Respiration 2021;100(8):751-763. Epub 2021 Jan 5 doi: 10.1159/000512531. PMID: 33401266
Respiratory management of children with spinal muscular atrophy (SMA).
Fauroux B, Griffon L, Amaddeo A, Stremler N, Mazenq J, Khirani S, Baravalle-Einaudi M
Arch Pediatr 2020 Dec;27(7S):7S29-7S34. doi: 10.1016/S0929-693X(20)30274-8. PMID: 33357594
A stepwise approach to the interpretation of pulmonary function tests.
Johnson JD, Theurer WM
Am Fam Physician 2014 Mar 1;89(5):359-66. PMID: 24695507
Anti-scl-70.
Basu D, Reveille JD
Autoimmunity 2005 Feb;38(1):65-72. doi: 10.1080/08916930400022947. PMID: 15804707
Adolescent idiopathic scoliosis.
Rinsky LA, Gamble JG
West J Med 1988 Feb;148(2):182-91. PMID: 3279708Free PMC Article

Recent systematic reviews

Pulmonary function sequelae after respiratory syncytial virus lower respiratory tract infection in children: A systematic review.
Verwey C, Nunes MC, Dangor Z, Madhi SA
Pediatr Pulmonol 2020 Jul;55(7):1567-1583. Epub 2020 May 4 doi: 10.1002/ppul.24804. PMID: 32364320
Risk stratification of pulmonary toxicities in the combination of whole lung irradiation and high-dose chemotherapy for Ewing sarcoma patients with lung metastases: a review.
Scobioala S, Eich HT
Strahlenther Onkol 2020 Jun;196(6):495-504. Epub 2020 Mar 12 doi: 10.1007/s00066-020-01599-8. PMID: 32166453Free PMC Article
Incidence, Predictors, and Outcomes of Early Atrial Arrhythmias After Lung Transplant: A Systematic Review and Meta-Analysis.
Saad M, Elgendy IY, Mentias A, Abdelaziz HK, Barakat AF, Abuzaid A, Elgendy AY, Mojadidi MK, Chandrashekaran S, Mahmoud AN
JACC Clin Electrophysiol 2017 Jul;3(7):718-726. Epub 2017 Mar 1 doi: 10.1016/j.jacep.2016.12.009. PMID: 29759540
Long term sequelae from childhood pneumonia; systematic review and meta-analysis.
Edmond K, Scott S, Korczak V, Ward C, Sanderson C, Theodoratou E, Clark A, Griffiths U, Rudan I, Campbell H
PLoS One 2012;7(2):e31239. Epub 2012 Feb 22 doi: 10.1371/journal.pone.0031239. PMID: 22384005Free PMC Article
Diagnosis and prognostic value of restrictive ventilatory disorders in the elderly: a systematic review of the literature.
Scarlata S, Costanzo L, Giua R, Pedone C, Incalzi RA
Exp Gerontol 2012 Apr;47(4):281-9. Epub 2012 Feb 19 doi: 10.1016/j.exger.2012.02.001. PMID: 22370614

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...