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Meningeal Central Nervous System Solitary Fibrous Tumor, Grade 3

MedGen UID:
457460
•Concept ID:
C2985234
•
Neoplastic Process
Synonyms: Meningeal CNS Solitary Fibrous Tumor, Grade 3; Meningeal Solitary Fibrous Tumor/Hemangiopericytoma, Grade 3

Definition

A solitary fibrous tumor that arises from the meninges. It most often corresponds to the tumor previously diagnosed as anaplastic hemangiopericytoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMeningeal Central Nervous System Solitary Fibrous Tumor, Grade 3

Recent clinical studies

Etiology

Surgical Management of Craniospinal Axis Solitary Fibrous Tumors: A Single-Institution Case Series and Comprehensive Review of the Literature.
Piscopo AJ, Chowdhury AJ, Teferi N, Lee S, Challa M, Petronek M, Eschbacher K, Bathla G, Buatti JM, Hitchon P
Neurosurgery 2024 Feb 1;94(2):358-368. Epub 2023 Sep 25 doi: 10.1227/neu.0000000000002692. PMID: 37747216
Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.
Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676
Solitary fibrous tumours and haemangiopericytoma of the meninges. A retrospective study for outcome and prognostic factor assessment.
Champeaux C, Rousseau P, Devaux B, Nataf F, Tauziède-Espariat A
Neurochirurgie 2018 Mar;64(1):37-43. Epub 2018 Feb 21 doi: 10.1016/j.neuchi.2017.10.004. PMID: 29475608
Meningial perineurioma: a benign peripheral nerve sheath tumor in a previously unrecognized central nervous system location, mimicking meningioma.
Vajtai I, Hewer E, Andres R, Neuenschwander M, Kappeler A, Gugger M
Pathol Res Pract 2011 Sep 15;207(9):592-6. Epub 2011 Aug 9 doi: 10.1016/j.prp.2011.07.003. PMID: 21831532

Diagnosis

Meningioma and Other Meningeal Tumors.
Bailo M, Gagliardi F, Boari N, Spina A, Piloni M, Castellano A, Mortini P
Adv Exp Med Biol 2023;1405:73-97. doi: 10.1007/978-3-031-23705-8_3. PMID: 37452935
Rare magnetic resonance imaging findings of intracranial solitary fibrous tumor: A case report.
Huang Z, Dai D, Tang G
Medicine (Baltimore) 2022 Oct 21;101(42):e31355. doi: 10.1097/MD.0000000000031355. PMID: 36281132Free PMC Article
Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.
Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676
Solitary fibrous tumours and haemangiopericytoma of the meninges. A retrospective study for outcome and prognostic factor assessment.
Champeaux C, Rousseau P, Devaux B, Nataf F, Tauziède-Espariat A
Neurochirurgie 2018 Mar;64(1):37-43. Epub 2018 Feb 21 doi: 10.1016/j.neuchi.2017.10.004. PMID: 29475608
Solitary fibrous tumor of the meninges: a lesion distinct from fibrous meningioma. A clinicopathologic and immunohistochemical study.
Carneiro SS, Scheithauer BW, Nascimento AG, Hirose T, Davis DH
Am J Clin Pathol 1996 Aug;106(2):217-24. doi: 10.1093/ajcp/106.2.217. PMID: 8712177

Prognosis

NAB2::STAT6 fusions and genome-wide DNA methylation profiling: Predictors of patient outcomes in meningeal solitary fibrous tumors.
Eschbacher KL, Tran QT, Moskalev EA, Jenkins S, Fritchie K, Stoehr R, Caron A, Link MJ, Brown PD, Guajardo A, Brat DJ, Wu A, Santagata S, Louis DN, Brastianos PK, Kaplan AB, Alexander B, Rossi S, Ferrarese F, Raleigh DR, Nguyen MP, Gross J, Velazquez Vega J, Rodriguez F, Perry A, Martinez-Lage M, Orr BA, Haller F, Giannini C
Brain Pathol 2024 Nov;34(6):e13256. Epub 2024 Mar 24 doi: 10.1111/bpa.13256. PMID: 38523251Free PMC Article
Surgical Management of Craniospinal Axis Solitary Fibrous Tumors: A Single-Institution Case Series and Comprehensive Review of the Literature.
Piscopo AJ, Chowdhury AJ, Teferi N, Lee S, Challa M, Petronek M, Eschbacher K, Bathla G, Buatti JM, Hitchon P
Neurosurgery 2024 Feb 1;94(2):358-368. Epub 2023 Sep 25 doi: 10.1227/neu.0000000000002692. PMID: 37747216
Meningioma and Other Meningeal Tumors.
Bailo M, Gagliardi F, Boari N, Spina A, Piloni M, Castellano A, Mortini P
Adv Exp Med Biol 2023;1405:73-97. doi: 10.1007/978-3-031-23705-8_3. PMID: 37452935
Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.
Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676
Solitary fibrous tumours and haemangiopericytoma of the meninges. A retrospective study for outcome and prognostic factor assessment.
Champeaux C, Rousseau P, Devaux B, Nataf F, Tauziède-Espariat A
Neurochirurgie 2018 Mar;64(1):37-43. Epub 2018 Feb 21 doi: 10.1016/j.neuchi.2017.10.004. PMID: 29475608

Clinical prediction guides

NAB2::STAT6 fusions and genome-wide DNA methylation profiling: Predictors of patient outcomes in meningeal solitary fibrous tumors.
Eschbacher KL, Tran QT, Moskalev EA, Jenkins S, Fritchie K, Stoehr R, Caron A, Link MJ, Brown PD, Guajardo A, Brat DJ, Wu A, Santagata S, Louis DN, Brastianos PK, Kaplan AB, Alexander B, Rossi S, Ferrarese F, Raleigh DR, Nguyen MP, Gross J, Velazquez Vega J, Rodriguez F, Perry A, Martinez-Lage M, Orr BA, Haller F, Giannini C
Brain Pathol 2024 Nov;34(6):e13256. Epub 2024 Mar 24 doi: 10.1111/bpa.13256. PMID: 38523251Free PMC Article
Surgical Management of Craniospinal Axis Solitary Fibrous Tumors: A Single-Institution Case Series and Comprehensive Review of the Literature.
Piscopo AJ, Chowdhury AJ, Teferi N, Lee S, Challa M, Petronek M, Eschbacher K, Bathla G, Buatti JM, Hitchon P
Neurosurgery 2024 Feb 1;94(2):358-368. Epub 2023 Sep 25 doi: 10.1227/neu.0000000000002692. PMID: 37747216
Rare magnetic resonance imaging findings of intracranial solitary fibrous tumor: A case report.
Huang Z, Dai D, Tang G
Medicine (Baltimore) 2022 Oct 21;101(42):e31355. doi: 10.1097/MD.0000000000031355. PMID: 36281132Free PMC Article
Aggressive Behavior Predictors in Solitary Fibrous Tumor: Demographic, Clinical, and Histopathologic Characteristics of 81 Cases.
Hassani M, Jung S, Garzia L, Ghodsi E, Alcindor T, Turcotte RE
Ann Surg Oncol 2021 Oct;28(11):6861-6867. Epub 2021 Jan 29 doi: 10.1245/s10434-021-09592-w. PMID: 33512676
Meningial perineurioma: a benign peripheral nerve sheath tumor in a previously unrecognized central nervous system location, mimicking meningioma.
Vajtai I, Hewer E, Andres R, Neuenschwander M, Kappeler A, Gugger M
Pathol Res Pract 2011 Sep 15;207(9):592-6. Epub 2011 Aug 9 doi: 10.1016/j.prp.2011.07.003. PMID: 21831532

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