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Autosomal hypohidrotic ectodermal dysplasia

MedGen UID:
468426
Concept ID:
CN118829
Disease or Syndrome
Related genes: EDARADD, EDAR

Professional guidelines

PubMed

Güven Y, Bal E, Altunoglu U, Yücel E, Hadj-Rabia S, Koruyucu M, Bahar Tuna E, Çıldır Ş, Aktören O, Bodemer C, Uyguner ZO, Smahi A, Kayserili H
Cytogenet Genome Res 2019;157(4):189-196. Epub 2019 Apr 12 doi: 10.1159/000499325. PMID: 30974434
Petersheim D, Massaad MJ, Lee S, Scarselli A, Cancrini C, Moriya K, Sasahara Y, Lankester AC, Dorsey M, Di Giovanni D, Bezrodnik L, Ohnishi H, Nishikomori R, Tanita K, Kanegane H, Morio T, Gelfand EW, Jain A, Secord E, Picard C, Casanova JL, Albert MH, Torgerson TR, Geha RS
J Allergy Clin Immunol 2018 Mar;141(3):1060-1073.e3. Epub 2017 Jun 17 doi: 10.1016/j.jaci.2017.05.030. PMID: 28629746Free PMC Article

Recent clinical studies

Etiology

Yapijakis C, Douka A, Gintoni I, Agiannitopoulos K, Vlachakis D, Chrousos GP
Adv Exp Med Biol 2023;1423:181-186. doi: 10.1007/978-3-031-31978-5_15. PMID: 37525042
Reyes-Reali J, Mendoza-Ramos MI, Garrido-Guerrero E, Méndez-Catalá CF, Méndez-Cruz AR, Pozo-Molina G
Int J Dermatol 2018 Aug;57(8):965-972. Epub 2018 May 31 doi: 10.1111/ijd.14048. PMID: 29855039
Blüschke G, Nüsken KD, Schneider H
Early Hum Dev 2010 Jul;86(7):397-9. Epub 2010 Jun 1 doi: 10.1016/j.earlhumdev.2010.04.008. PMID: 20682465
Clauss F, Chassaing N, Smahi A, Vincent MC, Calvas P, Molla M, Lesot H, Alembik Y, Hadj-Rabia S, Bodemer C, Manière MC, Schmittbuhl M
Clin Genet 2010 Sep;78(3):257-66. Epub 2010 Feb 24 doi: 10.1111/j.1399-0004.2010.01376.x. PMID: 20236127
Etzioni A, Ochs HD
Pediatr Res 2004 Oct;56(4):519-25. Epub 2004 Aug 19 doi: 10.1203/01.PDR.0000139318.65842.4A. PMID: 15319456

Diagnosis

Yapijakis C, Douka A, Gintoni I, Agiannitopoulos K, Vlachakis D, Chrousos GP
Adv Exp Med Biol 2023;1423:181-186. doi: 10.1007/978-3-031-31978-5_15. PMID: 37525042
Ahmad F, Ahmad T, Umair M, Abdullah, Ahmad W
Congenit Anom (Kyoto) 2019 Jul;59(4):145-147. Epub 2018 Aug 22 doi: 10.1111/cga.12307. PMID: 30079503
Reyes-Reali J, Mendoza-Ramos MI, Garrido-Guerrero E, Méndez-Catalá CF, Méndez-Cruz AR, Pozo-Molina G
Int J Dermatol 2018 Aug;57(8):965-972. Epub 2018 May 31 doi: 10.1111/ijd.14048. PMID: 29855039
Henningsen E, Svendsen MT, Lildballe DL, Jensen PK
Am J Med Genet A 2014 Aug;164A(8):2059-61. Epub 2014 Apr 24 doi: 10.1002/ajmg.a.36582. PMID: 24764207
Jorgenson RJ, Dowben JS, Dowben SL
J Craniofac Genet Dev Biol 1987;7(4):403-12. PMID: 3429615

Therapy

Madana J, Yolmo D, Gopalakrishnan S, Saxena SK, Nath AK, Ilamaran V
Int J Pediatr Otorhinolaryngol 2009 Oct;73(10):1467-9. Epub 2009 Jul 18 doi: 10.1016/j.ijporl.2009.06.012. PMID: 19616858

Prognosis

Sreenivasan V, Karunakar P, Madhileti S, Govindaswamy Ramamoorthy J, Gulati R
Paediatr Int Child Health 2024 Aug;44(2):59-62. Epub 2024 Apr 24 doi: 10.1080/20469047.2024.2344879. PMID: 38659257
Dubey S, Bhoot M, Jain K
J Glaucoma 2019 Apr;28(4):e58-e60. doi: 10.1097/IJG.0000000000001156. PMID: 30540672
Singh R, Rohilla RK, Siwach R, Sen R, Kaur K
Orthop Surg 2011 Feb;3(1):78-81. doi: 10.1111/j.1757-7861.2010.00111.x. PMID: 22009985Free PMC Article
Blüschke G, Nüsken KD, Schneider H
Early Hum Dev 2010 Jul;86(7):397-9. Epub 2010 Jun 1 doi: 10.1016/j.earlhumdev.2010.04.008. PMID: 20682465
Monreal AW, Ferguson BM, Headon DJ, Street SL, Overbeek PA, Zonana J
Nat Genet 1999 Aug;22(4):366-9. doi: 10.1038/11937. PMID: 10431241

Clinical prediction guides

Sreenivasan V, Karunakar P, Madhileti S, Govindaswamy Ramamoorthy J, Gulati R
Paediatr Int Child Health 2024 Aug;44(2):59-62. Epub 2024 Apr 24 doi: 10.1080/20469047.2024.2344879. PMID: 38659257
Petersheim D, Massaad MJ, Lee S, Scarselli A, Cancrini C, Moriya K, Sasahara Y, Lankester AC, Dorsey M, Di Giovanni D, Bezrodnik L, Ohnishi H, Nishikomori R, Tanita K, Kanegane H, Morio T, Gelfand EW, Jain A, Secord E, Picard C, Casanova JL, Albert MH, Torgerson TR, Geha RS
J Allergy Clin Immunol 2018 Mar;141(3):1060-1073.e3. Epub 2017 Jun 17 doi: 10.1016/j.jaci.2017.05.030. PMID: 28629746Free PMC Article
Clauss F, Chassaing N, Smahi A, Vincent MC, Calvas P, Molla M, Lesot H, Alembik Y, Hadj-Rabia S, Bodemer C, Manière MC, Schmittbuhl M
Clin Genet 2010 Sep;78(3):257-66. Epub 2010 Feb 24 doi: 10.1111/j.1399-0004.2010.01376.x. PMID: 20236127
Sandhu K, Handa S, Kanwar AJ
Int J Dermatol 2007 Jun;46(6):631-3. doi: 10.1111/j.1365-4632.2007.02432.x. PMID: 17550568
Cambiaghi S, Restano L, Pääkkönen K, Caputo R, Kere J
Arch Dermatol 2000 Feb;136(2):217-24. doi: 10.1001/archderm.136.2.217. PMID: 10677098

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