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Congenital stenosis of pulmonary artery

MedGen UID:
472996
•Concept ID:
C0265911
•
Congenital Abnormality
Synonym: Congenital Pulmonary Artery Stenosis
SNOMED CT: Congenital stenosis of pulmonary artery (449125001)

Definition

A congenital cardiovascular abnormality characterized by the narrowing of the lumen of the main pulmonary artery or its branches. It may be associated with other congenital heart malformations. Signs and symptoms include dyspnea, tachypnea, tachycardia, fatigue, and edema. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCongenital stenosis of pulmonary artery

Professional guidelines

PubMed

Treatment approach to unilateral branch pulmonary artery stenosis.
Hiremath G, Qureshi AM, Meadows J, Aggarwal V
Trends Cardiovasc Med 2021 Apr;31(3):179-184. Epub 2020 Feb 10 doi: 10.1016/j.tcm.2020.02.001. PMID: 32081565
Treatment of Peripheral Pulmonary Artery Stenosis.
Kim CW, Aronow WS, Dutta T, Spevack DM, Frishman WH
Cardiol Rev 2021 May-Jun 01;29(3):115-119. doi: 10.1097/CRD.0000000000000300. PMID: 32053544
Management of the adult Fontan patient.
Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332

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