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Biliary cystadenocarcinoma

MedGen UID:
473526
•Concept ID:
C2064409
•
Neoplastic Process
Synonyms: biliary cystadenocarcinoma; Intrahepatic Bile Duct Cystadenocarcinoma; Intrahepatic bile duct cystadenocarcinoma; intrahepatic bile duct cystadenocarcinoma; Intrahepatic Bile Duct MCN with an Associated Invasive Carcinoma; Intrahepatic Bile Duct Mucinous Cystic Neoplasm with an Associated Invasive Carcinoma
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0018535
Orphanet: ORPHA424982

Definition

A mucinous cystic neoplasm that arises from the intrahepatic bile ducts and it is associated with an invasive carcinomatous component. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBiliary cystadenocarcinoma

Professional guidelines

PubMed

Preoperative differential diagnosis between intrahepatic biliary cystadenoma and cystadenocarcinoma: a single-center experience.
Zhang FB, Zhang AM, Zhang ZB, Huang X, Wang XT, Dong JH
World J Gastroenterol 2014 Sep 21;20(35):12595-601. doi: 10.3748/wjg.v20.i35.12595. PMID: 25253963Free PMC Article
Effective treatment of biliary cystadenoma.
Thomas KT, Welch D, Trueblood A, Sulur P, Wise P, Gorden DL, Chari RS, Wright JK Jr, Washington K, Pinson CW
Ann Surg 2005 May;241(5):769-73; discussion 773-5. doi: 10.1097/01.sla.0000161982.57360.1b. PMID: 15849512Free PMC Article
Radiologic spectrum of cholangiocarcinoma: emphasis on unusual manifestations and differential diagnoses.
Lee WJ, Lim HK, Jang KM, Kim SH, Lee SJ, Lim JH, Choo IW
Radiographics 2001 Oct;21 Spec No:S97-S116. doi: 10.1148/radiographics.21.suppl_1.g01oc12s97. PMID: 11598251

Recent clinical studies

Etiology

Clinicopathological features and management of biliary cystic tumors of the liver: a single-center experience.
El-Magd EA, El-Shobari M, Abdelsalam RA, Abbas A, Elmahdy Y, Hamed H
Langenbecks Arch Surg 2023 Jul 11;408(1):273. doi: 10.1007/s00423-023-02994-2. PMID: 37430153Free PMC Article
Differentiation of mucinous cysts and simple cysts of the liver using preoperative imaging.
McIntyre CA, Girshman J, Goldman DA, Gonen M, Soares KC, Wei AC, Balachandran VP, Kingham TP, Drebin JA, Jarnagin WR, Gluskin JS, D'Angelica MI, Gerst SR
Abdom Radiol (NY) 2022 Apr;47(4):1333-1340. Epub 2022 Feb 21 doi: 10.1007/s00261-022-03436-1. PMID: 35188592Free PMC Article
Preoperative differential diagnosis between intrahepatic biliary cystadenoma and cystadenocarcinoma: a single-center experience.
Zhang FB, Zhang AM, Zhang ZB, Huang X, Wang XT, Dong JH
World J Gastroenterol 2014 Sep 21;20(35):12595-601. doi: 10.3748/wjg.v20.i35.12595. PMID: 25253963Free PMC Article
Intrahepatic biliary cystadenoma and cystadenocarcinoma: an experience of 30 cases.
Wang C, Miao R, Liu H, Du X, Liu L, Lu X, Zhao H
Dig Liver Dis 2012 May;44(5):426-31. Epub 2011 Dec 9 doi: 10.1016/j.dld.2011.11.007. PMID: 22169273
Biliary cystadenoma and cystadenocarcinoma of the liver: 10 cases of a single center experience.
Lee JH, Lee KG, Park HK, Lee KS
Hepatogastroenterology 2009 May-Jun;56(91-92):844-9. PMID: 19621714

Diagnosis

Hepatobiliary and Pancreatic: Degenerative hepatic hemangioma mimicking biliary cystadenocarcinoma.
Kaida T, Higashi T, Kitano Y, Yamamura K, Arima K, Taki K, Imai K, Nitta H, Hashimoto D, Chikamoto A, Namimoto T, Nakahara O, Beppu T, Baba H
J Gastroenterol Hepatol 2016 Aug;31(8):1385. doi: 10.1111/jgh.13325. PMID: 26896817
Cystic neoplasms of the liver: biliary cystadenoma and cystadenocarcinoma.
Soares KC, Arnaoutakis DJ, Kamel I, Anders R, Adams RB, Bauer TW, Pawlik TM
J Am Coll Surg 2014 Jan;218(1):119-28. Epub 2013 Sep 14 doi: 10.1016/j.jamcollsurg.2013.08.014. PMID: 24045144Free PMC Article
Education and imaging. Hepatobiliary and pancreatic: intrahepatic biliary cystadenocarcinoma.
Okano K, Oshima M, Yamamoto N, Yachida S, Suzuki Y
J Gastroenterol Hepatol 2013 Apr;28(4):753. doi: 10.1111/jgh.12127. PMID: 23527760
Biliary cystadenocarcinoma.
Seo DW, Kang GH
Gastrointest Endosc 2000 Jan;51(1):66. doi: 10.1016/s0016-5107(00)70139-8. PMID: 10625799
Primary hepatic malignant neoplasms.
Fernandez MP, Redvanly RD
Radiol Clin North Am 1998 Mar;36(2):333-48. doi: 10.1016/s0033-8389(05)70026-9. PMID: 9520986

Therapy

Contrast enhanced ultrasound features of hepatic cystadenoma and hepatic cystadenocarcinoma.
Dong Y, Wang WP, Mao F, Fan M, Ignee A, Serra C, Sparchez Z, Sporea I, Braden B, Dietrich CF
Scand J Gastroenterol 2017 Mar;52(3):365-372. Epub 2016 Nov 25 doi: 10.1080/00365521.2016.1259652. PMID: 27887203
Endoscopic ultrasonography-guided drainage of infected intracystic papillary adenocarcinoma of the liver.
Kodama R, Saegusa H, Ushimaru H, Ikeno T, Makino M, Kawaguchi K
Clin J Gastroenterol 2015 Oct;8(5):335-9. Epub 2015 Sep 28 doi: 10.1007/s12328-015-0607-6. PMID: 26412329
A case of biliary cystadenocarcinoma with malignant seeding of the tract after percutaneous catheter drainage.
Yuefeng M, Weili F, Jing L, Wenxiang T, Tianqing L, Liming W
Turk J Gastroenterol 2012;23(6):795-8. doi: 10.4318/tjg.2012.0644. PMID: 23864459
Biliary cystadenocarcinoma with mesenchymal stroma.
Gómez-Martín C, Rodríguez A, Malón D, Cortés-Funes H
Clin Transl Oncol 2010 Mar;12(3):234-7. doi: 10.1007/s12094-010-0495-7. PMID: 20231130
Successful complete resection of biliary cystadenocarcinoma after percutaneous transhepatic portal embolization.
Murakami Y, Kanehiro T, Yokoyama Y, Uemura K, Sasaki M, Morifuji M, Hayashidani Y, Sudo T, Sueda T
Surgery 2005 May;137(5):577-9. doi: 10.1016/j.surg.2003.12.006. PMID: 15855934

Prognosis

Clinicopathological features and management of biliary cystic tumors of the liver: a single-center experience.
El-Magd EA, El-Shobari M, Abdelsalam RA, Abbas A, Elmahdy Y, Hamed H
Langenbecks Arch Surg 2023 Jul 11;408(1):273. doi: 10.1007/s00423-023-02994-2. PMID: 37430153Free PMC Article
Management of Mucinous Cystic Neoplasms of the Liver.
Aziz H, Hamad A, Afyouni S, Kamel IR, Pawlik TM
J Gastrointest Surg 2023 Sep;27(9):1963-1970. Epub 2023 May 23 doi: 10.1007/s11605-023-05709-6. PMID: 37221388
Hepatobiliary and Pancreatic: Degenerative hepatic hemangioma mimicking biliary cystadenocarcinoma.
Kaida T, Higashi T, Kitano Y, Yamamura K, Arima K, Taki K, Imai K, Nitta H, Hashimoto D, Chikamoto A, Namimoto T, Nakahara O, Beppu T, Baba H
J Gastroenterol Hepatol 2016 Aug;31(8):1385. doi: 10.1111/jgh.13325. PMID: 26896817
Cystic neoplasms of the liver: biliary cystadenoma and cystadenocarcinoma.
Soares KC, Arnaoutakis DJ, Kamel I, Anders R, Adams RB, Bauer TW, Pawlik TM
J Am Coll Surg 2014 Jan;218(1):119-28. Epub 2013 Sep 14 doi: 10.1016/j.jamcollsurg.2013.08.014. PMID: 24045144Free PMC Article
Biliary cystadenocarcinoma complicated by intralesional haemorrhage.
Psaltis E, Prescott R, Chang D, Lapsia S
Br J Hosp Med (Lond) 2012 Oct;73(10):590-1. doi: 10.12968/hmed.2012.73.10.590. PMID: 23124292

Clinical prediction guides

Clinicopathological features and management of biliary cystic tumors of the liver: a single-center experience.
El-Magd EA, El-Shobari M, Abdelsalam RA, Abbas A, Elmahdy Y, Hamed H
Langenbecks Arch Surg 2023 Jul 11;408(1):273. doi: 10.1007/s00423-023-02994-2. PMID: 37430153Free PMC Article
Hepatobiliary and Pancreatic: Degenerative hepatic hemangioma mimicking biliary cystadenocarcinoma.
Kaida T, Higashi T, Kitano Y, Yamamura K, Arima K, Taki K, Imai K, Nitta H, Hashimoto D, Chikamoto A, Namimoto T, Nakahara O, Beppu T, Baba H
J Gastroenterol Hepatol 2016 Aug;31(8):1385. doi: 10.1111/jgh.13325. PMID: 26896817
Endoscopic ultrasonography-guided drainage of infected intracystic papillary adenocarcinoma of the liver.
Kodama R, Saegusa H, Ushimaru H, Ikeno T, Makino M, Kawaguchi K
Clin J Gastroenterol 2015 Oct;8(5):335-9. Epub 2015 Sep 28 doi: 10.1007/s12328-015-0607-6. PMID: 26412329
Preoperative differential diagnosis between intrahepatic biliary cystadenoma and cystadenocarcinoma: a single-center experience.
Zhang FB, Zhang AM, Zhang ZB, Huang X, Wang XT, Dong JH
World J Gastroenterol 2014 Sep 21;20(35):12595-601. doi: 10.3748/wjg.v20.i35.12595. PMID: 25253963Free PMC Article
Intrahepatic biliary cystadenoma and cystadenocarcinoma: an experience of 30 cases.
Wang C, Miao R, Liu H, Du X, Liu L, Lu X, Zhao H
Dig Liver Dis 2012 May;44(5):426-31. Epub 2011 Dec 9 doi: 10.1016/j.dld.2011.11.007. PMID: 22169273

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