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Abnormal atrioventricular connection

MedGen UID:: 488858
•Concept ID:: C0344612
•: Congenital Abnormality

Synonyms:	Abnormal atrioventricular connexion; AV - Abnormal atrioventricular connection
SNOMED CT:	AV - Abnormal atrioventricular connection (253274005); Abnormal atrioventricular connection (253274005)

HPO:	HP:0011546

Definition

An abnormality of the circulatory connection between atria and ventricles. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVAbnormal atrioventricular connection

Disorder by Site
- Disorder of cardiovascular system
  - Abnormality of the cardiovascular system
    - Abnormal cardiovascular system morphology
      - Abnormal heart morphology
        Abnormal connection of the cardiac segments
        Abnormal atrioventricular connection
        Absent left sided atrioventricular connection
        Biventricular heart with straddling right sided atrioventricular valve and absent left sided atrioventricular connection
        Right sided atrium to left ventricle and absent left sided atrioventricular connection
        Univentricular heart with absent left sided atrioventricular connection
        Absent right sided atrioventricular connection
        Ambiguous atrioventricular connection
        Discordant atrioventricular connection
        Double inlet atrioventricular connection
        Double inlet left ventricle
        Double inlet right ventricle
        Double inlet to single ventricle of indeterminate morphology
        Double inlet to single ventricle with common atrioventricular orifice
        Double inlet to single ventricle with two atrioventricular valves
        Mitral atresia disorder
        Overriding atrioventricular valve
        Straddling atrioventricular valve

Professional guidelines

PubMed

Management of the adult Fontan patient.

Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332

Postnatal Outcome Following Prenatal Diagnosis of Discordant Atrioventricular and Ventriculoarterial Connections.

Day TG, Woodgate T, Knee O, Zidere V, Vigneswaran T, Charakida M, Miller O, Sharland G, Simpson J
Pediatr Cardiol 2019 Oct;40(7):1509-1515. Epub 2019 Jul 25 doi: 10.1007/s00246-019-02176-2. PMID: 31342118

Neonatal management and outcomes of prenatally diagnosed CHDs.

Bensemlali M, Bajolle F, Laux D, Parisot P, Ladouceur M, Fermont L, Lévy M, Le Bidois J, Raimondi F, Ville Y, Salomon LJ, Boudjemline Y, Bonnet D
Cardiol Young 2017 Mar;27(2):344-353. Epub 2016 May 26 doi: 10.1017/S1047951116000639. PMID: 27225605

See all (18)

Recent clinical studies

Etiology

The clinical relevance of the abdominal fetal electrocardiogram.

Pardi G, Ferrazzi E, Cetin I, Rampello S, Baselli G, Cerutti S, Civardi S
J Perinat Med 1986;14(6):371-7. PMID: 3546668

See all (1)

Diagnosis

The clinical relevance of the abdominal fetal electrocardiogram.

Pardi G, Ferrazzi E, Cetin I, Rampello S, Baselli G, Cerutti S, Civardi S
J Perinat Med 1986;14(6):371-7. PMID: 3546668

Double outlet from chambers of left ventricular morphology.

Coto EO, Jimenez MQ, Castaneda AR, Rufilanchas JJ, Deverall PB
Br Heart J 1979 Jul;42(1):15-21. doi: 10.1136/hrt.42.1.15. PMID: 475930 Free PMC Article

See all (2)

Clinical prediction guides

The clinical relevance of the abdominal fetal electrocardiogram.

Pardi G, Ferrazzi E, Cetin I, Rampello S, Baselli G, Cerutti S, Civardi S
J Perinat Med 1986;14(6):371-7. PMID: 3546668

See all (1)

MedGen

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Abnormal atrioventricular connection

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Clinical prediction guides

Supplemental Content

Table of contents

Clinical resources

Practice guidelines

Consumer resources

Reviews

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