U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Marchiafava-Bignami disease

MedGen UID:
65955
Concept ID:
C0238265
Disease or Syndrome
Synonyms: Acute Marchiafava-Bignami disease; Chronic Marchiafava-Bignami syndrome
SNOMED CT: Marchiafava-Bignami disease (386766007); Marchiafava disease (386766007); Central demyelination of corpus callosum (386766007)
 
Monarch Initiative: MONDO:0016370
Orphanet: ORPHA221074

Definition

A rare neurologic disease most prominently characterized by progressive demyelination and necrosis of the corpus callosum. It is in most cases associated with chronic alcoholism and malnutrition. Speed of onset and clinical presentation are very variable with a range of possible symptoms, including dementia, seizures, gait abnormalities, dysarthria, aphasia, athetosis, as well as stupor and coma. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMarchiafava-Bignami disease
Follow this link to review classifications for Marchiafava-Bignami disease in Orphanet.

Professional guidelines

PubMed

Hillbom M, Saloheimo P, Fujioka S, Wszolek ZK, Juvela S, Leone MA
J Neurol Neurosurg Psychiatry 2014 Feb;85(2):168-73. Epub 2013 Aug 26 doi: 10.1136/jnnp-2013-305979. PMID: 23978380Free PMC Article

Recent clinical studies

Etiology

Li W, Ran C, Ma J
Acta Radiol 2021 Jul;62(7):904-908. Epub 2020 Jul 27 doi: 10.1177/0284185120943040. PMID: 32718180
Shen YY, Zhou CG, Han N, Liang XM, Deng YQ
Chin Med J (Engl) 2019 Aug 5;132(15):1887-1889. doi: 10.1097/CM9.0000000000000334. PMID: 31283655Free PMC Article
Dong X, Bai C, Nao J
Medicine (Baltimore) 2018 Feb;97(5):e9626. doi: 10.1097/MD.0000000000009626. PMID: 29384842Free PMC Article
Logan C, Asadi H, Kok HK, Looby ST, Brennan P, O'Hare A, Thornton J
J Med Imaging Radiat Oncol 2017 Aug;61(4):435-440. Epub 2016 Dec 16 doi: 10.1111/1754-9485.12572. PMID: 27987266
Kashiwagi Y, Horiuchi T, Harashima C, Matsubara F, Harashima S
BMJ Case Rep 2010 Nov 29;2010 doi: 10.1136/bcr.08.2010.3269. PMID: 22798099Free PMC Article

Diagnosis

Li H, Zeng M, Tang W
Neurol Sci 2024 Jan;45(1):369-372. Epub 2023 Sep 19 doi: 10.1007/s10072-023-07068-1. PMID: 37723370
Nishioka H, Kamei H
Balkan Med J 2023 Oct 20;40(6):445-446. Epub 2023 Sep 20 doi: 10.4274/balkanmedj.galenos.2023.2023-7-68. PMID: 37728371Free PMC Article
Haralur Y, Mechtler LL
Neurol Clin 2020 Feb;38(1):149-170. Epub 2019 Oct 24 doi: 10.1016/j.ncl.2019.09.002. PMID: 31761056
Pinto MV, Bon A, Costa VC, Noro F, Lima MA
Arq Neuropsiquiatr 2016 Feb;74(2):180. Epub 2015 Oct 20 doi: 10.1590/0004-282X20150173. PMID: 26486496
Hathaway BM, Ch'ien L
South Med J 1971 May;64(5):602-6. doi: 10.1097/00007611-197105000-00021. PMID: 5573080

Therapy

Patel S, Lambert K
Am J Emerg Med 2024 Dec;86:190.e1-190.e3. Epub 2024 Sep 28 doi: 10.1016/j.ajem.2024.09.058. PMID: 39366786
Kim TE, Lee EJ, Young JB, Shin DJ, Kim JH
Semin Ultrasound CT MR 2014 Apr;35(2):85-96. doi: 10.1053/j.sult.2013.09.004. PMID: 24745886
Hillbom M, Saloheimo P, Fujioka S, Wszolek ZK, Juvela S, Leone MA
J Neurol Neurosurg Psychiatry 2014 Feb;85(2):168-73. Epub 2013 Aug 26 doi: 10.1136/jnnp-2013-305979. PMID: 23978380Free PMC Article
Demaerel P, Van Paesschen W
N Engl J Med 2004 Sep 9;351(11):e10. doi: 10.1056/NEJMicm030414. PMID: 15356319
Pore G, Gulhane S, Joshi AK, Barve JS
J Assoc Physicians India 1995 Oct;43(10):718-9. PMID: 8773015

Prognosis

Zhou Z, Zeng L, Zhou H, Xu Z, Xu P
Ann Clin Transl Neurol 2023 Nov;10(11):2013-2024. Epub 2023 Aug 30 doi: 10.1002/acn3.51888. PMID: 37649317Free PMC Article
Buesa-Lorenzo JB, Rojo-Bofill LMR, Plumed-Domingo JP, Rubio-Granero T, Rojo-Moreno L
Actas Esp Psiquiatr 2021 Sep;49(5):228-231. Epub 2021 Sep 1 PMID: 34533206
Hillbom M, Saloheimo P, Fujioka S, Wszolek ZK, Juvela S, Leone MA
J Neurol Neurosurg Psychiatry 2014 Feb;85(2):168-73. Epub 2013 Aug 26 doi: 10.1136/jnnp-2013-305979. PMID: 23978380Free PMC Article
Ménégon P, Sibon I, Pachai C, Orgogozo JM, Dousset V
Neurology 2005 Aug 9;65(3):475-7. doi: 10.1212/01.wnl.0000171348.55820.89. PMID: 16087921
Naeije R, Franken L, Jacobovitz D, Flament-Durand J
Eur Neurol 1978;17(3):155-9. doi: 10.1159/000114939. PMID: 658060

Clinical prediction guides

Zhang YL, Ran C, Xu C, Li W
Sci Rep 2023 Oct 28;13(1):18516. doi: 10.1038/s41598-023-45431-6. PMID: 37898646Free PMC Article
Dong X, Bai C, Nao J
Medicine (Baltimore) 2018 Feb;97(5):e9626. doi: 10.1097/MD.0000000000009626. PMID: 29384842Free PMC Article
Hillbom M, Saloheimo P, Fujioka S, Wszolek ZK, Juvela S, Leone MA
J Neurol Neurosurg Psychiatry 2014 Feb;85(2):168-73. Epub 2013 Aug 26 doi: 10.1136/jnnp-2013-305979. PMID: 23978380Free PMC Article
Namekawa M, Nakamura Y, Nakano I
Intern Med 2013;52(7):811-3. Epub 2013 Apr 1 doi: 10.2169/internalmedicine.52.9336. PMID: 23545681
Machado A, Soares-Fernandes J, Ribeiro M, Rodrigues M, Cerqueira J, Ferreira C
J Clin Neurosci 2009 Jun;16(6):811, 859. doi: 10.1016/j.jocn.2008.08.040. PMID: 19548340

Recent systematic reviews

Deví-Bastida J, Xifré-Passols M, Oviedo-Penuela LM, Teresa Abellán-Vidal M, Dolores López-Villegas M
Rev Colomb Psiquiatr (Engl Ed) 2024 Jul-Sep;53(3):385-395. Epub 2024 Oct 28 doi: 10.1016/j.rcpeng.2024.10.004. PMID: 39472222

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...