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Pulmonary sequestration

MedGen UID:
669
•Concept ID:
C0006288
•
Congenital Abnormality
Synonyms: Bronchopulmonary Sequestration; Bronchopulmonary Sequestrations; Pulmonary Sequestration; Pulmonary Sequestrations; Sequestration, Bronchopulmonary; Sequestration, Pulmonary; Sequestrations, Bronchopulmonary; Sequestrations, Pulmonary
SNOMED CT: Sequestration of lung (18620009); Pulmonary sequestration (18620009); Congenital sequestration of lung (18620009)
 
HPO: HP:0100632

Definition

The presence of a piece lung tissue which is not attached to the pulmonary blood supply and does not communicate with the other lung tissue (not connected to the standard bronchial airways and not performing a function in respiration). [from HPO]

Conditions with this feature

Global developmental delay with or without impaired intellectual development
MedGen UID:
1675328
•Concept ID:
C5193032
•
Disease or Syndrome
See: Condition Record
Global developmental delay with or without impaired intellectual development

Professional guidelines

PubMed

Clinical Outcomes of Transarterial Embolization in the Treatment of Pulmonary Sequestration.
Bi Y, Li J, Yi M, Ren J, Han X
Cardiovasc Intervent Radiol 2021 Sep;44(9):1491-1496. Epub 2021 Jun 15 doi: 10.1007/s00270-021-02885-3. PMID: 34131775
The clinical management of extralobar pulmonary sequestration in children.
Huang D, Habuding A, Yuan M, Yang G, Cheng K, Luo D, Xu C
Pediatr Pulmonol 2021 Jul;56(7):2322-2327. Epub 2021 Apr 30 doi: 10.1002/ppul.25433. PMID: 33930250
Prenatal Imaging Diagnosis of Suprarenal Lesions.
Lazow SP, Richman DM, Dionigi B, Staffa SJ, Benson CB, Buchmiller TL
Fetal Diagn Ther 2021;48(3):235-242. Epub 2021 Mar 17 doi: 10.1159/000512689. PMID: 33730724

Recent clinical studies

Etiology

Imaging of congenital lung malformations.
Chowdhury MM, Chakraborty S
Semin Pediatr Surg 2015 Aug;24(4):168-75. Epub 2015 Feb 27 doi: 10.1053/j.sempedsurg.2015.02.001. PMID: 26051049
Bronchopulmonary foregut malformation.
Katayama Y, Kusagawa H, Komada T, Shomura S, Tenpaku H
Gen Thorac Cardiovasc Surg 2011 Nov;59(11):767-70. Epub 2011 Nov 15 doi: 10.1007/s11748-010-0763-z. PMID: 22083698
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Pulmonary sequestration.
Salmons S
Neonatal Netw 2000 Oct;19(7):27-31. doi: 10.1891/0730-0832.19.7.27. PMID: 11949021
Adrenal masses in the newborn.
Nadler EP, Barksdale EM
Semin Pediatr Surg 2000 Aug;9(3):156-64. doi: 10.1053/spsu.2000.7560. PMID: 10949426

Diagnosis

Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Pulmonary sequestration.
Savić B, Birtel FJ, Knoche R, Tholen W, Schild H
Ergeb Inn Med Kinderheilkd 1979;43:57-92. doi: 10.1007/978-3-642-67379-5_2. PMID: 394961
Pulmonary sequestration.
O'Mara CS, Baker RR, Jeyasingham K
Surg Gynecol Obstet 1978 Oct;147(4):609-16. PMID: 360452
Pseudosequestration.
Macpherson RI, Whytehead L
J Can Assoc Radiol 1977 Mar;28(1):17-25. PMID: 838752
Pulmonary sequestration.
Carter R
Ann Thorac Surg 1969 Jan;7(1):68-88. doi: 10.1016/s0003-4975(10)66147-4. PMID: 4883836

Therapy

Hybrid minimally invasive treatment of intralobar pulmonary sequestration: a single-centre experience.
Grossi W, Londero F, Vit A, De Franceschi E, Masullo G, Sponza M, Morelli A
Interact Cardiovasc Thorac Surg 2022 Jan 18;34(2):255-257. doi: 10.1093/icvts/ivab245. PMID: 34480559Free PMC Article
Pulmonary sequestration in adults: a retrospective review of resected and unresected cases.
Alsumrain M, Ryu JH
BMC Pulm Med 2018 Jun 5;18(1):97. doi: 10.1186/s12890-018-0663-z. PMID: 29871620Free PMC Article
Carcinoid tumor and pulmonary sequestration.
Westphal FL, Lima LC, Lima Netto JC, Cardoso Mdo S, Silva Mdos S, Westphal DC
J Bras Pneumol 2012 Jan-Feb;38(1):133-7. doi: 10.1590/s1806-37132012000100018. PMID: 22407050
Early and late outcomes of coil embolization of pulmonary sequestration in children.
Chien KJ, Huang TC, Lin CC, Lee CL, Hsieh KS, Weng KP
Circ J 2009 May;73(5):938-42. Epub 2009 Mar 11 doi: 10.1253/circj.cj-08-0914. PMID: 19276609
Dialysis-induced eosinophilia.
Bodner G, Peer G, Zakuth V, Spirer ZH, Aviram A
Nephron 1982;32(1):63-6. doi: 10.1159/000182805. PMID: 7177280

Prognosis

Imaging and pathological characteristics, treatment, and prognosis of pulmonary sequestration-A retrospective study of 13 cases.
Liu X, Wu R, Zhu S, Gu L, Tang Z
Clin Respir J 2023 Sep;17(9):865-873. Epub 2023 Aug 2 doi: 10.1111/crj.13672. PMID: 37533295Free PMC Article
Surgical management of the scimitar syndrome.
Chowdhury UK, Anderson RH, Sankhyan LK, George N, Pandey NN, Chauhan AS, Arora Y, Goja S
J Card Surg 2021 Oct;36(10):3770-3795. Epub 2021 Aug 16 doi: 10.1111/jocs.15857. PMID: 34396590
Eponym. Scimitar syndrome.
Midyat L, Demir E, Aşkin M, Gülen F, Ulger Z, Tanaç R, Bayraktaroğlu S
Eur J Pediatr 2010 Oct;169(10):1171-7. Epub 2010 Mar 12 doi: 10.1007/s00431-010-1152-4. PMID: 20225123
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Pulmonary sequestration.
Salmons S
Neonatal Netw 2000 Oct;19(7):27-31. doi: 10.1891/0730-0832.19.7.27. PMID: 11949021

Clinical prediction guides

Pulmonary sequestration in adulthood: clinical-morphological study.
Muri J, Makovicky P, Kamarad V, Durcova B, Vecanova J, Hvizdosova N
Bratisl Lek Listy 2024;125(3):153-158. doi: 10.4149/BLL_2023_140. PMID: 38385540
Epidemiology and prevalence of pulmonary sequestration in Chinese population, 2010-2019.
Gao Y, Xu W, Li W, Chen Z, Li Q, Liu Z, Liu H, Dai L
BMC Pulm Med 2023 Jan 9;23(1):8. doi: 10.1186/s12890-023-02308-8. PMID: 36624419Free PMC Article
The clinical management of extralobar pulmonary sequestration in children.
Huang D, Habuding A, Yuan M, Yang G, Cheng K, Luo D, Xu C
Pediatr Pulmonol 2021 Jul;56(7):2322-2327. Epub 2021 Apr 30 doi: 10.1002/ppul.25433. PMID: 33930250
Imaging findings in fetal diaphragmatic abnormalities.
Alamo L, Gudinchet F, Meuli R
Pediatr Radiol 2015 Dec;45(13):1887-900. Epub 2015 Aug 9 doi: 10.1007/s00247-015-3418-5. PMID: 26255159
Intra-abdominal pulmonary sequestration: a case report and literature review.
Liu L, Han P, Zhu Y, Gong J, Xu Y, Wei X, Li X, Dong Q, Wei Q
Urol Int 2012;88(1):121-4. Epub 2011 Sep 28 doi: 10.1159/000331688. PMID: 21967921

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