U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Choroidal hemangioma

MedGen UID:
83424
Concept ID:
C0346390
Neoplastic Process
Synonym: Choroidal hemangiomata
SNOMED CT: Choroidal hemangioma (255022003); Hemangioma of choroid (255022003)
 
HPO: HP:0007872
Monarch Initiative: MONDO:0021542

Definition

The presence of multiple hemangiomas in the choroid. These are generally reddish or orange or can have increased pigmentation maiking them difficult to distinguish from choroidal melanomas. [from HPO]

Term Hierarchy

Conditions with this feature

Sturge-Weber syndrome
MedGen UID:
21361
Concept ID:
C0038505
Disease or Syndrome
Sturge-Weber syndrome (SWS) is characterized by an intracranial vascular anomaly, leptomeningeal angiomatosis, most often involving the occipital and posterior parietal lobes. The most common symptoms and signs are facial cutaneous vascular malformations (port-wine stains), seizures, and glaucoma. Stasis results in ischemia underlying the leptomeningeal angiomatosis, leading to calcification and laminar cortical necrosis. The clinical course is highly variable and some children experience intractable seizures, mental retardation, and recurrent stroke-like episodes (review by Thomas-Sohl et al., 2004).

Professional guidelines

PubMed

García Caride S, Fernández-Vigo JI, Valverde-Megías A
Arch Soc Esp Oftalmol (Engl Ed) 2023 May;98(5):281-291. Epub 2023 Apr 14 doi: 10.1016/j.oftale.2023.04.006. PMID: 37062411
Durrani AF, Zhou Y, Musch DC, Demirci H
Ophthalmol Retina 2022 Jun;6(6):533-535. Epub 2022 Feb 1 doi: 10.1016/j.oret.2022.01.015. PMID: 35114415
Jurklies B, Bornfeld N
Graefes Arch Clin Exp Ophthalmol 2005 May;243(5):393-6. Epub 2005 Feb 8 doi: 10.1007/s00417-004-1100-y. PMID: 15700182

Recent clinical studies

Etiology

Franco JJ, Liu KX, Ioakeim-Ioannidou M, Davila JR, Chen YL, Kim IK, Gragoudas ES, Mukai S, MacDonald SM
Pediatr Blood Cancer 2022 Dec;69(12):e29925. Epub 2022 Aug 21 doi: 10.1002/pbc.29925. PMID: 35989464
Hao Z, Lai X
Neurologist 2019 Jan;24(1):13-16. doi: 10.1097/NRL.0000000000000207. PMID: 30586028
Merritt H, Pfeiffer ML, Phillips ME, Richani K
Orbit 2017 Feb;36(1):48-51. Epub 2017 Feb 1 doi: 10.1080/01676830.2017.1279643. PMID: 28146369
Baselga E
Semin Cutan Med Surg 2004 Jun;23(2):87-98. doi: 10.1016/j.sder.2004.01.002. PMID: 15295918
Sanborn GE, Augsburger JJ, Shields JA
Ophthalmology 1982 Dec;89(12):1374-80. doi: 10.1016/s0161-6420(82)34635-7. PMID: 6891765

Diagnosis

Torres G, Kini AT, Al Othman B, Lee AG
J Neuroophthalmol 2020 Jun;40(2):262-264. doi: 10.1097/WNO.0000000000000778. PMID: 30893269
Merritt H, Pfeiffer ML, Phillips ME, Richani K
Orbit 2017 Feb;36(1):48-51. Epub 2017 Feb 1 doi: 10.1080/01676830.2017.1279643. PMID: 28146369
Singh AD, Kaiser PK, Sears JE
Ophthalmol Clin North Am 2005 Mar;18(1):151-61, ix. doi: 10.1016/j.ohc.2004.07.004. PMID: 15763200
Shields CL, Shields JA, Augsburger JJ
Surv Ophthalmol 1988 Jul-Aug;33(1):17-27. doi: 10.1016/0039-6257(88)90069-0. PMID: 3051466
Coston TO, Wilkinson CP
Am J Ophthalmol 1978 Sep;86(3):368-72. doi: 10.1016/0002-9394(78)90241-6. PMID: 717501

Therapy

Zhang W, Peng J, Zhao P
Ophthalmology 2024 Aug;131(8):891. Epub 2023 Oct 19 doi: 10.1016/j.ophtha.2023.09.017. PMID: 37855777
Kumar A, Shankar S, Singh A, Mishra S, Kumar P, Arora A
Photodiagnosis Photodyn Ther 2022 Sep;39:103000. Epub 2022 Jul 3 doi: 10.1016/j.pdpdt.2022.103000. PMID: 35793781
Durrani AF, Zhou Y, Musch DC, Demirci H
Ophthalmol Retina 2022 Jun;6(6):533-535. Epub 2022 Feb 1 doi: 10.1016/j.oret.2022.01.015. PMID: 35114415
Lewis GD, Li HK, Quan EM, Scarboro SB, Teh BS
Pract Radiat Oncol 2019 Sep-Oct;9(5):e452-e456. Epub 2019 May 22 doi: 10.1016/j.prro.2019.05.007. PMID: 31128304
Jurklies B, Bornfeld N
Graefes Arch Clin Exp Ophthalmol 2005 May;243(5):393-6. Epub 2005 Feb 8 doi: 10.1007/s00417-004-1100-y. PMID: 15700182

Prognosis

García Caride S, Fernández-Vigo JI, Valverde-Megías A
Arch Soc Esp Oftalmol (Engl Ed) 2023 May;98(5):281-291. Epub 2023 Apr 14 doi: 10.1016/j.oftale.2023.04.006. PMID: 37062411
Ganz JC
Prog Brain Res 2022;268(1):315-327. Epub 2021 Dec 14 doi: 10.1016/bs.pbr.2021.10.039. PMID: 35074088
Merritt H, Pfeiffer ML, Phillips ME, Richani K
Orbit 2017 Feb;36(1):48-51. Epub 2017 Feb 1 doi: 10.1080/01676830.2017.1279643. PMID: 28146369
Singh AD, Kaiser PK, Sears JE
Ophthalmol Clin North Am 2005 Mar;18(1):151-61, ix. doi: 10.1016/j.ohc.2004.07.004. PMID: 15763200
Shields CL, Shields JA, Augsburger JJ
Surv Ophthalmol 1988 Jul-Aug;33(1):17-27. doi: 10.1016/0039-6257(88)90069-0. PMID: 3051466

Clinical prediction guides

Goto H, Umazume K, Usui Y, Nishikawa N
Jpn J Ophthalmol 2024 Nov;68(6):722-730. Epub 2024 Sep 28 doi: 10.1007/s10384-024-01102-1. PMID: 39340726
Franco JJ, Liu KX, Ioakeim-Ioannidou M, Davila JR, Chen YL, Kim IK, Gragoudas ES, Mukai S, MacDonald SM
Pediatr Blood Cancer 2022 Dec;69(12):e29925. Epub 2022 Aug 21 doi: 10.1002/pbc.29925. PMID: 35989464
Jorge R, Chaves L, Cunha ADS, Correa ZM
Retin Cases Brief Rep 2022 Jan 1;16(1):106-110. doi: 10.1097/ICB.0000000000000917. PMID: 31517744
Campagnoli TR, Medina CA, Singh AD
Retin Cases Brief Rep 2016 Spring;10(2):175-82. doi: 10.1097/ICB.0000000000000220. PMID: 26448544
Mashayekhi A, Shields CL
Curr Opin Ophthalmol 2003 Jun;14(3):142-9. doi: 10.1097/00055735-200306000-00006. PMID: 12777933

Recent systematic reviews

Zamir A, Hussain I, Ur Rehman A, Ashraf W, Imran I, Saeed H, Majeed A, Alqahtani F, Rasool MF
Clin Pharmacokinet 2022 Aug;61(8):1095-1114. Epub 2022 Jun 28 doi: 10.1007/s40262-022-01145-y. PMID: 35764772

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...