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Abnormality of the vestibular nerve

MedGen UID:
868965
•Concept ID:
C4023379
•
Anatomical Abnormality
HPO: HP:0011392

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormality of the vestibular nerve

Professional guidelines

PubMed

CANVAS: A New Genetic Entity in the Otorhinolaryngologist's Differential Diagnosis.
Costales M, Casanueva R, Suárez V, Asensi JM, Cifuentes GA, Diñeiro M, Cadiñanos J, López F, Álvarez-Marcos C, Otero A, Gómez J, Llorente JL, Cabanillas R
Otolaryngol Head Neck Surg 2022 Jan;166(1):74-79. Epub 2021 May 4 doi: 10.1177/01945998211008398. PMID: 33940977
Diagnosis, Management, and New Therapeutic Options in Childhood Neurofibromatosis Type 2 and Related Forms.
Ruggieri M, Praticò AD, Evans DG
Semin Pediatr Neurol 2015 Dec;22(4):240-58. Epub 2015 Oct 28 doi: 10.1016/j.spen.2015.10.008. PMID: 26706012
CANVAS an update: clinical presentation, investigation and management.
Szmulewicz DJ, McLean CA, MacDougall HG, Roberts L, Storey E, Halmagyi GM
J Vestib Res 2014;24(5-6):465-74. doi: 10.3233/VES-140536. PMID: 25564090

Recent clinical studies

Etiology

The Results of Cochlear Implantation in the Inner Ear Malformations.
Onan E, Tuncer U, Surmelioglu O, Dagkiran M, Ozdemir S, Tarkan O, Kiroglu MM
J Int Adv Otol 2022 May;18(3):203-209. doi: 10.5152/iao.2022.20134. PMID: 35608487Free PMC Article
The auditory and vestibular toxicities induced by antiepileptic drugs.
Hamed SA
Expert Opin Drug Saf 2017 Nov;16(11):1281-1294. Epub 2017 Aug 29 doi: 10.1080/14740338.2017.1372420. PMID: 28838247
Inferior vestibular neuritis.
Kim JS, Kim HJ
J Neurol 2012 Aug;259(8):1553-60. Epub 2012 Jan 4 doi: 10.1007/s00415-011-6375-4. PMID: 22215238
Neurofibroma and schwannoma.
Ferner RE, O'Doherty MJ
Curr Opin Neurol 2002 Dec;15(6):679-84. doi: 10.1097/01.wco.0000044763.39452.aa. PMID: 12447105
Vestibular manifestations of cerebellar ectopia. (Sub-group of Chiari I).
Bertrand RA, Martinez SN, Robert F
Adv Otorhinolaryngol 1973;19:355-66. PMID: 4541599

Diagnosis

The Pathology of the Vestibular System in CANVAS.
Ishai R, Seyyedi M, Chancellor AM, McLean CA, Rodriguez ML, Halmagyi GM, Nadol JB Jr, Szmulewicz DJ, Quesnel AM
Otol Neurotol 2021 Mar 1;42(3):e332-e340. doi: 10.1097/MAO.0000000000002985. PMID: 33492056Free PMC Article
Neurofibromatosis type 2.
Slattery WH
Otolaryngol Clin North Am 2015 Jun;48(3):443-60. doi: 10.1016/j.otc.2015.02.005. PMID: 26043141
Neurofibroma and schwannoma.
Ferner RE, O'Doherty MJ
Curr Opin Neurol 2002 Dec;15(6):679-84. doi: 10.1097/01.wco.0000044763.39452.aa. PMID: 12447105
Vestibular neuritis.
Nadol JB Jr
Otolaryngol Head Neck Surg 1995 Jan;112(1):162-72. doi: 10.1016/S0194-59989570316-0. PMID: 7816452
Neuro-ophthalmology.
Agnetti V
Curr Opin Neurol Neurosurg 1991 Oct;4(5):783-7. PMID: 10148443

Therapy

The auditory and vestibular toxicities induced by antiepileptic drugs.
Hamed SA
Expert Opin Drug Saf 2017 Nov;16(11):1281-1294. Epub 2017 Aug 29 doi: 10.1080/14740338.2017.1372420. PMID: 28838247
Management of surgical difficulties during cochlear implant with inner ear anomalies.
Aldhafeeri AM, Alsanosi AA
Int J Pediatr Otorhinolaryngol 2017 Jan;92:45-49. Epub 2016 Nov 3 doi: 10.1016/j.ijporl.2016.11.001. PMID: 28012532
Vestibular paroxysmia: a treatable neurovascular cross-compression syndrome.
Brandt T, Strupp M, Dieterich M
J Neurol 2016 Apr;263 Suppl 1:S90-6. Epub 2016 Apr 15 doi: 10.1007/s00415-015-7973-3. PMID: 27083889Free PMC Article
Hemorrhagic vestibular schwannoma: review of the literature.
Niknafs YS, Wang AC, Than KD, Etame AB, Thompson BG, Sullivan SE
World Neurosurg 2014 Nov;82(5):751-6. Epub 2013 Feb 27 doi: 10.1016/j.wneu.2013.02.069. PMID: 23454397
Neuropharmacologic aspects of the ocular motor system and the treatment of abnormal eye movements.
Leigh RJ, Ramat S
Curr Opin Neurol 1999 Feb;12(1):21-7. doi: 10.1097/00019052-199902000-00004. PMID: 10097880

Prognosis

The Results of Cochlear Implantation in the Inner Ear Malformations.
Onan E, Tuncer U, Surmelioglu O, Dagkiran M, Ozdemir S, Tarkan O, Kiroglu MM
J Int Adv Otol 2022 May;18(3):203-209. doi: 10.5152/iao.2022.20134. PMID: 35608487Free PMC Article
Otopathologic Abnormalities in CHARGE Syndrome.
da Costa Monsanto R, Knoll RM, de Oliveira Penido N, Song G, Santos F, Paparella MM, Cureoglu S
Otolaryngol Head Neck Surg 2022 Feb;166(2):363-372. Epub 2021 Apr 20 doi: 10.1177/01945998211008911. PMID: 33874787
Vestibular and oculomotor function in patients with vestibular migraine.
Fu W, Wang Y, He F, Wei D, Bai Y, Han J, Wang X
Am J Otolaryngol 2021 Nov-Dec;42(6):103152. Epub 2021 Jun 29 doi: 10.1016/j.amjoto.2021.103152. PMID: 34218215
Neuro-Ophthalmic Manifestations of Sarcoidosis.
Henderson AD, Tian J, Carey AR
J Neuroophthalmol 2021 Dec 1;41(4):e591-e597. doi: 10.1097/WNO.0000000000001108. PMID: 33110001
Some Remarks on Imaging of the Inner Ear: Options and Limitations.
Giesemann A, Hofmann E
Clin Neuroradiol 2015 Oct;25 Suppl 2:197-203. Epub 2015 Jul 8 doi: 10.1007/s00062-015-0422-y. PMID: 26153464

Clinical prediction guides

The Results of Cochlear Implantation in the Inner Ear Malformations.
Onan E, Tuncer U, Surmelioglu O, Dagkiran M, Ozdemir S, Tarkan O, Kiroglu MM
J Int Adv Otol 2022 May;18(3):203-209. doi: 10.5152/iao.2022.20134. PMID: 35608487Free PMC Article
Vestibular and oculomotor function in patients with vestibular migraine.
Fu W, Wang Y, He F, Wei D, Bai Y, Han J, Wang X
Am J Otolaryngol 2021 Nov-Dec;42(6):103152. Epub 2021 Jun 29 doi: 10.1016/j.amjoto.2021.103152. PMID: 34218215
The Pathology of the Vestibular System in CANVAS.
Ishai R, Seyyedi M, Chancellor AM, McLean CA, Rodriguez ML, Halmagyi GM, Nadol JB Jr, Szmulewicz DJ, Quesnel AM
Otol Neurotol 2021 Mar 1;42(3):e332-e340. doi: 10.1097/MAO.0000000000002985. PMID: 33492056Free PMC Article
Audiovestibular manifestations of sarcoidosis: a review of the literature.
Colvin IB
Laryngoscope 2006 Jan;116(1):75-82. doi: 10.1097/01.mlg.0000184580.52723.9f. PMID: 16481814
Familial auditory neuropathy.
Wang Q, Gu R, Han D, Yang W
Laryngoscope 2003 Sep;113(9):1623-9. doi: 10.1097/00005537-200309000-00041. PMID: 12972945

Recent systematic reviews

Acute vestibular syndrome associated with anti-GQ1b antibody.
Lee SU, Kim HJ, Choi JY, Kim JK, Kim JS
Neurology 2019 Sep 10;93(11):e1085-e1092. Epub 2019 Aug 9 doi: 10.1212/WNL.0000000000008107. PMID: 31399495
Assessment of the Clinical Benefit of Imaging in Children With Unilateral Sensorineural Hearing Loss: A Systematic Review and Meta-analysis.
Ropers FG, Pham ENB, Kant SG, Rotteveel LJC, Rings EHHM, Verbist BM, Dekkers OM
JAMA Otolaryngol Head Neck Surg 2019 May 1;145(5):431-443. doi: 10.1001/jamaoto.2019.0121. PMID: 30946449Free PMC Article
Audiovestibular Function Deficits in Vestibular Schwannoma.
von Kirschbaum C, Gürkov R
Biomed Res Int 2016;2016:4980562. Epub 2016 Sep 22 doi: 10.1155/2016/4980562. PMID: 27747231Free PMC Article
Diagnostic yield of MRI for pediatric hearing loss: a systematic review.
Kachniarz B, Chen JX, Gilani S, Shin JJ
Otolaryngol Head Neck Surg 2015 Jan;152(1):5-22. Epub 2014 Nov 11 doi: 10.1177/0194599814555837. PMID: 25389321Free PMC Article
Cochlear implantation in children with anomalous cochleovestibular anatomy: a systematic review.
Pakdaman MN, Herrmann BS, Curtin HD, Van Beek-King J, Lee DJ
Otolaryngol Head Neck Surg 2012 Feb;146(2):180-90. Epub 2011 Dec 1 doi: 10.1177/0194599811429244. PMID: 22140206

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