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Abnormal fourth ventricle morphology

MedGen UID:
869208
•Concept ID:
C4023630
•
Anatomical Abnormality
Synonym: Abnormality of the fourth ventricle
 
HPO: HP:0010950

Definition

An abnormality of the fourth ventricle. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal fourth ventricle morphology

Professional guidelines

PubMed

Prenatal Diagnosis and Clinical Outcomes of Isolated Mega Cisterna Magna.
Kim O, Hong S, Jung YM, Seol HJ, Na S, Bae JG, Ahn KH, Lee MY, Kwon HY, Sung JH, Choi SR, Kim SC, Lee KA, Kim HS, Kim MJ, Song JE, Hwang HS, Won HS, Jun JK, Ko HS
J Child Neurol 2024 Nov;39(13-14):481-486. Epub 2024 Oct 3 doi: 10.1177/08830738241282037. PMID: 39360439
Prenatal diagnosis of rhombencephalosynapsis: neuroimaging features and severity of vermian anomaly.
Krajden Haratz K, Oliveira Szejnfeld P, Govindaswamy M, Leibovitz Z, Gindes L, Severino M, Rossi A, Paladini D, Garcia Rodriguez R, Ben-Sira L, Borkowski Tillman T, Gupta R, Lotem G, Raz N, Hamamoto TENK, Kidron D, Arad A, Birnbaum R, Brussilov M, Pomar L, Vial Y, Leventer RJ, McGillivray G, Fink M, Krzeszowski W, Fernandes Moron A, Lev D, Tamarkin M, Shalev J, Har Toov J, Lerman-Sagie T, Malinger G
Ultrasound Obstet Gynecol 2021 Dec;58(6):864-874. doi: 10.1002/uog.23660. PMID: 33942916
Prenatal neurologic anomalies: sonographic diagnosis and treatment.
De Catte L, De Keersmaeker B, Claus F
Paediatr Drugs 2012 Jun 1;14(3):143-55. doi: 10.2165/11597030-000000000-00000. PMID: 22242843

Recent clinical studies

Etiology

'Choroid bar': easy-to-seek marker of normal posterior fossa at 12-14 weeks' gestation.
Paladini D, Biancotto G, Della Sala F, Acharya PV
Ultrasound Obstet Gynecol 2024 Apr;63(4):497-501. Epub 2024 Mar 13 doi: 10.1002/uog.27566. PMID: 38145551
Rhomboencephalosynapsis: Review of the Literature.
Fouda MA, Kim TY, Cohen AR
World Neurosurg 2022 Mar;159:48-53. Epub 2021 Dec 22 doi: 10.1016/j.wneu.2021.12.062. PMID: 34954057
Intracranial translucency assessment at first trimester nuchal translucency ultrasound.
Lane A, Lee L, Traves D, Lee A
J Med Imaging Radiat Oncol 2017 Apr;61(2):185-189. Epub 2016 Oct 21 doi: 10.1111/1754-9485.12548. PMID: 27766742
Medulloblastoma.
Bartlett F, Kortmann R, Saran F
Clin Oncol (R Coll Radiol) 2013 Jan;25(1):36-45. Epub 2012 Dec 11 doi: 10.1016/j.clon.2012.09.008. PMID: 23245832
Borrelia rhombencephalomyelopathy.
Kuntzer T, Bogousslavsky J, Miklossy J, Steck AJ, Janzer R, Regli F
Arch Neurol 1991 Aug;48(8):832-6. doi: 10.1001/archneur.1991.00530200072021. PMID: 1898257

Diagnosis

Rhomboencephalosynapsis: Review of the Literature.
Fouda MA, Kim TY, Cohen AR
World Neurosurg 2022 Mar;159:48-53. Epub 2021 Dec 22 doi: 10.1016/j.wneu.2021.12.062. PMID: 34954057
Dilated fourth ventricle on brain computed tomography scan in the diagnosis of Chiari I malformation with syringomyelia.
Suzuki K, Miyamoto T, Miyamoto M, Nishibayashi M, Hirata K
Intern Med 2008;47(3):185-6. Epub 2008 Feb 1 doi: 10.2169/internalmedicine.47.0561. PMID: 18239332
Gomez-Lopez-Hernandez syndrome.
Whetsell W, Saigal G, Godinho S
Pediatr Radiol 2006 Jun;36(6):552-4. Epub 2006 Apr 11 doi: 10.1007/s00247-006-0150-1. PMID: 16607507
Aventriculy: a new entity?
Garfinkle WB
AJNR Am J Neuroradiol 1996 Oct;17(9):1649-50. PMID: 8896616Free PMC Article
Borrelia rhombencephalomyelopathy.
Kuntzer T, Bogousslavsky J, Miklossy J, Steck AJ, Janzer R, Regli F
Arch Neurol 1991 Aug;48(8):832-6. doi: 10.1001/archneur.1991.00530200072021. PMID: 1898257

Therapy

Fourth ventricle to spinal subarachnoid space stenting in pediatric patients with refractory syringomyelia: case series and systematic review.
Spennato P, Vitulli F, Tafuto R, Imperato A, Mirone G, Cinalli G
Neurosurg Rev 2023 Mar 11;46(1):67. doi: 10.1007/s10143-023-01972-y. PMID: 36905420
Fourth ventricle tumors in children: complications and influence of surgical approach.
Toescu SM, Samarth G, Layard Horsfall H, Issitt R, Margetts B, Phipps KP, Jeelani NU, Thompson DNP, Aquilina K
J Neurosurg Pediatr 2021 Jan 1;27(1):52-61. Epub 2020 Oct 23 doi: 10.3171/2020.6.PEDS2089. PMID: 33096529
A colloid cyst in the fourth ventricle complicated with aseptic meningitis: a case report.
Wang Z, Yan H, Wang D, Wang S, Liu R, Zhang Y
Clin Neurol Neurosurg 2012 Sep;114(7):1095-8. Epub 2012 Mar 7 doi: 10.1016/j.clineuro.2012.02.016. PMID: 22405542
Clinical reasoning: a 36-year-old man with vertical diplopia.
Prasad S, Volpe NJ, Tamhankar MA
Neurology 2009 May 12;72(19):e93-9. doi: 10.1212/WNL.0b013e3181a55ee3. PMID: 19433734
Rhinorrhoea from a frontal encephalocele after reduction of high intracranial pressure.
Yilmaz C, Gulsen S, Altinors N, Caner H
Acta Neurochir (Wien) 2008 Dec;150(12):1307-8. Epub 2008 Nov 18 doi: 10.1007/s00701-008-0157-5. PMID: 19015807

Prognosis

Dandy-Walker Malformation.
Society for Maternal-Fetal Medicine (SMFM), Monteagudo A
Am J Obstet Gynecol 2020 Dec;223(6):B38-B41. Epub 2020 Nov 7 doi: 10.1016/j.ajog.2020.08.184. PMID: 33168220
Noninvasive Multimodality Imaging in ARVD/C.
Te Riele ASJM, Tandri H, Sanborn DM, Bluemke DA
JACC Cardiovasc Imaging 2015 May;8(5):597-611. doi: 10.1016/j.jcmg.2015.02.007. PMID: 25937197Free PMC Article
Medulloblastoma.
Bartlett F, Kortmann R, Saran F
Clin Oncol (R Coll Radiol) 2013 Jan;25(1):36-45. Epub 2012 Dec 11 doi: 10.1016/j.clon.2012.09.008. PMID: 23245832
Endoscopic aqueductoplasty and stenting.
Fritsch MJ, Schroeder HW
World Neurosurg 2013 Feb;79(2 Suppl):S20.e15-8. Epub 2012 Feb 10 doi: 10.1016/j.wneu.2012.02.013. PMID: 22381819
Joubert syndrome: monozygotic twins with discordant phenotypes.
Raynes HR, Shanske A, Goldberg S, Burde R, Rapin I
J Child Neurol 1999 Oct;14(10):649-54; discussion 669-72 discussio. doi: 10.1177/088307389901401005. PMID: 10511337

Clinical prediction guides

Combined Cerebrospinal Fluid Hydrodynamics and Fourth Ventricle Outlet Morphology to Improve Predictive Efficiency of Prognosis for Chiari Malformation Type I Decompression.
Xiao Y, Liu Y, Wang Z, He K, Zhang Z, Chen S, Dai J, Luo Y, Gui Y, Xiao X
World Neurosurg 2023 Aug;176:e208-e218. Epub 2023 May 13 doi: 10.1016/j.wneu.2023.05.031. PMID: 37187345
Investigating cerebral oedema using poroelasticity.
Vardakis JC, Chou D, Tully BJ, Hung CC, Lee TH, Tsui PH, Ventikos Y
Med Eng Phys 2016 Jan;38(1):48-57. Epub 2015 Dec 31 doi: 10.1016/j.medengphy.2015.09.006. PMID: 26749338
Noninvasive Multimodality Imaging in ARVD/C.
Te Riele ASJM, Tandri H, Sanborn DM, Bluemke DA
JACC Cardiovasc Imaging 2015 May;8(5):597-611. doi: 10.1016/j.jcmg.2015.02.007. PMID: 25937197Free PMC Article
Joubert syndrome: a clinico-radiological study.
Kendall B, Kingsley D, Lambert SR, Taylor D, Finn P
Neuroradiology 1990;31(6):502-6. doi: 10.1007/BF00340131. PMID: 2352633
Bruns bidirectional nystagmus in cerebellopontine angle tumours.
Croxson GR, Moffat DA, Baguley D
Clin Otolaryngol Allied Sci 1988 Apr;13(2):153-7. doi: 10.1111/j.1365-2273.1988.tb00756.x. PMID: 3262024

Recent systematic reviews

Fourth ventricle to spinal subarachnoid space stenting in pediatric patients with refractory syringomyelia: case series and systematic review.
Spennato P, Vitulli F, Tafuto R, Imperato A, Mirone G, Cinalli G
Neurosurg Rev 2023 Mar 11;46(1):67. doi: 10.1007/s10143-023-01972-y. PMID: 36905420
Brainstem cavernous malformations.
Gross BA, Batjer HH, Awad IA, Bendok BR
Neurosurgery 2009 May;64(5):E805-18; discussion E818. doi: 10.1227/01.NEU.0000343668.44288.18. PMID: 19404127

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