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Meningioangiomatosis

MedGen UID:
890255
•Concept ID:
C4054534
•
Disease or Syndrome

Definition

A rare vascular malformation in the cerebral cortex and overlying leptomeninges. It can occur sporadically or in association with neurofibromatosis type 2. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMeningioangiomatosis

Professional guidelines

PubMed

Diagnosis and surgical treatment of sporadic meningioangiomatosis.
Feng R, Hu J, Che X, Pan L, Wang Z, Zhang M, Huang F, Xu B, Mao R, Sun A, Bao W, Zhong P, Wang Y
Clin Neurol Neurosurg 2013 Aug;115(8):1407-14. Epub 2013 Feb 26 doi: 10.1016/j.clineuro.2013.01.021. PMID: 23485253

Recent clinical studies

Etiology

Pure and non-pure meningioangiomatosis of 36 Chinese patients: an analysis of clinical presentation, diagnosis, histopathology and prognosis.
Zhang GB, Ying YZ, Huang HW, Yu WJ, Li HY, Zhang XK, Wang YG, Cui Y, Chen Y, Jiang ZL, Lin S
Neurosurg Rev 2022 Oct;45(5):3405-3415. Epub 2022 Sep 5 doi: 10.1007/s10143-022-01855-8. PMID: 36063221
Focal cortical dysplasia in meningioangiomatosis.
Grabowski MM, Prayson RA
Clin Neuropathol 2015 Mar-Apr;34(2):76-82. doi: 10.5414/NP300820. PMID: 25601060
Frozen section discrepancy in the evaluation of nonneoplastic central nervous system samples.
Plesec TP, Prayson RA
Ann Diagn Pathol 2009 Dec;13(6):359-66. Epub 2009 Sep 8 doi: 10.1016/j.anndiagpath.2009.05.006. PMID: 19917470
Intraparenchymal meningioma originating from underlying meningioangiomatosis. Case report and review of the literature.
Mut M, Söylemezoğlu F, Firat MM, Palaoğlu S
J Neurosurg 2000 Apr;92(4):706-10. doi: 10.3171/jns.2000.92.4.0706. PMID: 10761664
Multifocal meningioangiomatosis: a report of two cases.
Park MS, Suh DC, Choi WS, Lee SY, Kang GH
AJNR Am J Neuroradiol 1999 Apr;20(4):677-80. PMID: 10319980Free PMC Article

Diagnosis

An update on the CNS manifestations of neurofibromatosis type 2.
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Teaching NeuroImages: Meningioangiomatosis.
Aw-Zoretic J, Burrowes D, Wadhwani N, Ryan M
Neurology 2015 Jan 13;84(2):e9-e10. doi: 10.1212/WNL.0000000000001125. PMID: 25583831
Multicystic meningioangiomatosis.
Li P, Cui G, Wang Y, Geng M, Wang Z
BMC Neurol 2014 Feb 20;14:32. doi: 10.1186/1471-2377-14-32. PMID: 24555776Free PMC Article
Meningioangiomatosis in a patient with progressive focal neurological deficit-case report and review of literature.
Abdulazim A, Samis Zella MA, Rapp M, Gierga K, Langen KJ, Steiger HJ, Sabel M
Br J Neurosurg 2013 Apr;27(2):253-5. Epub 2012 Nov 20 doi: 10.3109/02688697.2012.741737. PMID: 23167668
Meningioangiomatosis.
Partington CR, Graves VB, Hegstrand LR
AJNR Am J Neuroradiol 1991 May-Jun;12(3):549-52. PMID: 2058512Free PMC Article

Therapy

Progressive diffuse meningioangiomatosis: Response to bevacizumab treatment.
Yust-Katz S, Fuller G, Fichman-Horn S, Michaeli N, Inbar E, Lukman J, Limon D, Steiner I, Siegal T
Neurology 2016 Apr 26;86(17):1643-4. Epub 2016 Mar 30 doi: 10.1212/WNL.0000000000002610. PMID: 27029633Free PMC Article

Prognosis

Meningioangiomatosis: Multimodal Analysis and Insights From a Systematic Review.
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
An update on the CNS manifestations of neurofibromatosis type 2.
Coy S, Rashid R, Stemmer-Rachamimov A, Santagata S
Acta Neuropathol 2020 Apr;139(4):643-665. Epub 2019 Jun 4 doi: 10.1007/s00401-019-02029-5. PMID: 31161239Free PMC Article
Insights into meningioangiomatosis with and without meningioma: a clinicopathologic and genetic series of 24 cases with review of the literature.
Perry A, Kurtkaya-Yapicier O, Scheithauer BW, Robinson S, Prayson RA, Kleinschmidt-DeMasters BK, Stemmer-Rachamimov AO, Gutmann DH
Brain Pathol 2005 Jan;15(1):55-65. doi: 10.1111/j.1750-3639.2005.tb00100.x. PMID: 15779237Free PMC Article
Intraparenchymal meningioma originating from underlying meningioangiomatosis. Case report and review of the literature.
Mut M, Söylemezoğlu F, Firat MM, Palaoğlu S
J Neurosurg 2000 Apr;92(4):706-10. doi: 10.3171/jns.2000.92.4.0706. PMID: 10761664
Multifocal meningioangiomatosis: a report of two cases.
Park MS, Suh DC, Choi WS, Lee SY, Kang GH
AJNR Am J Neuroradiol 1999 Apr;20(4):677-80. PMID: 10319980Free PMC Article

Clinical prediction guides

Meningioangiomatosis: Multimodal Analysis and Insights From a Systematic Review.
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
Left Frontal Meningioangiomatosis Associated with Type IIIc Focal Cortical Dysplasia Causing Refractory Epilepsy and Literature Review.
Roux A, Mellerio C, Lechapt-Zalcman E, Still M, Zerah M, Bourgeois M, Pallud J
World Neurosurg 2018 Jun;114:281-288. Epub 2018 Mar 30 doi: 10.1016/j.wneu.2018.03.145. PMID: 29605698
Intraparenchymal meningioma originating from underlying meningioangiomatosis. Case report and review of the literature.
Mut M, Söylemezoğlu F, Firat MM, Palaoğlu S
J Neurosurg 2000 Apr;92(4):706-10. doi: 10.3171/jns.2000.92.4.0706. PMID: 10761664
Meningioma with meningioangiomatosis: a condition mimicking invasive meningiomas in children and young adults: report of two cases and review of the literature.
Giangaspero F, Guiducci A, Lenz FA, Mastronardi L, Burger PC
Am J Surg Pathol 1999 Aug;23(8):872-5. doi: 10.1097/00000478-199908000-00002. PMID: 10435554
A case of meningioangiomatosis without von Recklinghausen's disease. Report of a case and review of 13 cases.
Harada K, Inagawa T, Nagasako R
Childs Nerv Syst 1994 Mar;10(2):126-30. doi: 10.1007/BF00302777. PMID: 8033161

Recent systematic reviews

Meningioangiomatosis: Multimodal Analysis and Insights From a Systematic Review.
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266

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