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Pulmonary fibrosis, idiopathic, susceptibility to

MedGen UID:
865126
Concept ID:
C4016689
Finding
Synonym: PULMONARY FIBROSIS, IDIOPATHIC, SUSCEPTIBILITY TO
 
OMIM®: 600770

Professional guidelines

PubMed

Aryal S, Nathan SD
Expert Opin Emerg Drugs 2018 Jun;23(2):159-172. Epub 2018 May 8 doi: 10.1080/14728214.2018.1471465. PMID: 29718783
Sgalla G, Iovene B, Calvello M, Ori M, Varone F, Richeldi L
Respir Res 2018 Feb 22;19(1):32. doi: 10.1186/s12931-018-0730-2. PMID: 29471816Free PMC Article
Elmufdi F, Henke CA, Perlman DM, Tomic R, Kim HJ
Discov Med 2015 Sep;20(109):145-53. PMID: 26463096

Recent clinical studies

Etiology

Cui F, Sun Y, Xie J, Li D, Wu M, Song L, Hu Y, Tian Y
Eur Respir J 2023 Feb;61(2) Epub 2023 Feb 2 doi: 10.1183/13993003.00777-2022. PMID: 36137588
Saint-Criq V, Lugo-Villarino G, Thomas M
Ageing Res Rev 2021 Mar;66:101235. Epub 2020 Dec 13 doi: 10.1016/j.arr.2020.101235. PMID: 33321253
Bueno M, Calyeca J, Rojas M, Mora AL
Redox Biol 2020 Jun;33:101509. Epub 2020 Mar 19 doi: 10.1016/j.redox.2020.101509. PMID: 32234292Free PMC Article
Allen RJ, Guillen-Guio B, Oldham JM, Ma SF, Dressen A, Paynton ML, Kraven LM, Obeidat M, Li X, Ng M, Braybrooke R, Molina-Molina M, Hobbs BD, Putman RK, Sakornsakolpat P, Booth HL, Fahy WA, Hart SP, Hill MR, Hirani N, Hubbard RB, McAnulty RJ, Millar AB, Navaratnam V, Oballa E, Parfrey H, Saini G, Whyte MKB, Zhang Y, Kaminski N, Adegunsoye A, Strek ME, Neighbors M, Sheng XR, Gudmundsson G, Gudnason V, Hatabu H, Lederer DJ, Manichaikul A, Newell JD Jr, O'Connor GT, Ortega VE, Xu H, Fingerlin TE, Bossé Y, Hao K, Joubert P, Nickle DC, Sin DD, Timens W, Furniss D, Morris AP, Zondervan KT, Hall IP, Sayers I, Tobin MD, Maher TM, Cho MH, Hunninghake GM, Schwartz DA, Yaspan BL, Molyneaux PL, Flores C, Noth I, Jenkins RG, Wain LV
Am J Respir Crit Care Med 2020 Mar 1;201(5):564-574. doi: 10.1164/rccm.201905-1017OC. PMID: 31710517Free PMC Article
Sgalla G, Iovene B, Calvello M, Ori M, Varone F, Richeldi L
Respir Res 2018 Feb 22;19(1):32. doi: 10.1186/s12931-018-0730-2. PMID: 29471816Free PMC Article

Diagnosis

Leavy OC, Kawano-Dourado L, Stewart ID, Quint JK, Solomon JJ, Borie R, Crestani B, Wain LV, Jenkins G, Dieudé P, Minelli C
Thorax 2024 May 20;79(6):538-544. doi: 10.1136/thorax-2023-220856. PMID: 38649271Free PMC Article
Alder JK, Armanios M
Physiol Rev 2022 Oct 1;102(4):1703-1720. Epub 2022 May 9 doi: 10.1152/physrev.00046.2021. PMID: 35532056Free PMC Article
Chanda D, Otoupalova E, Smith SR, Volckaert T, De Langhe SP, Thannickal VJ
Mol Aspects Med 2019 Feb;65:56-69. Epub 2018 Aug 23 doi: 10.1016/j.mam.2018.08.004. PMID: 30130563Free PMC Article
Sgalla G, Iovene B, Calvello M, Ori M, Varone F, Richeldi L
Respir Res 2018 Feb 22;19(1):32. doi: 10.1186/s12931-018-0730-2. PMID: 29471816Free PMC Article
Martinez FJ, Collard HR, Pardo A, Raghu G, Richeldi L, Selman M, Swigris JJ, Taniguchi H, Wells AU
Nat Rev Dis Primers 2017 Oct 20;3:17074. doi: 10.1038/nrdp.2017.74. PMID: 29052582

Therapy

Leavy OC, Kawano-Dourado L, Stewart ID, Quint JK, Solomon JJ, Borie R, Crestani B, Wain LV, Jenkins G, Dieudé P, Minelli C
Thorax 2024 May 20;79(6):538-544. doi: 10.1136/thorax-2023-220856. PMID: 38649271Free PMC Article
Cui F, Sun Y, Xie J, Li D, Wu M, Song L, Hu Y, Tian Y
Eur Respir J 2023 Feb;61(2) Epub 2023 Feb 2 doi: 10.1183/13993003.00777-2022. PMID: 36137588
Assad N, Sood A, Campen MJ, Zychowski KE
Curr Environ Health Rep 2018 Dec;5(4):486-498. doi: 10.1007/s40572-018-0219-7. PMID: 30298344Free PMC Article
Sgalla G, Iovene B, Calvello M, Ori M, Varone F, Richeldi L
Respir Res 2018 Feb 22;19(1):32. doi: 10.1186/s12931-018-0730-2. PMID: 29471816Free PMC Article
Liu T, De Los Santos FG, Phan SH
Methods Mol Biol 2017;1627:27-42. doi: 10.1007/978-1-4939-7113-8_2. PMID: 28836192

Prognosis

Wang T, Duan W, Jia X, Huang X, Liu Y, Meng F, Ni C
Eur Respir J 2024 Feb;63(2) Epub 2024 Feb 22 doi: 10.1183/13993003.01720-2023. PMID: 38061785Free PMC Article
Moll M, Peljto AL, Kim JS, Xu H, Debban CL, Chen X, Menon A, Putman RK, Ghosh AJ, Saferali A, Nishino M, Hatabu H, Hobbs BD, Hecker J, McDermott G, Sparks JA, Wain LV, Allen RJ, Tobin MD, Raby BA, Chun S, Silverman EK, Zamora AC, Ortega VE, Garcia CK, Barr RG, Bleecker ER, Meyers DA, Kaner RJ, Rich SS, Manichaikul A, Rotter JI, Dupuis J, O'Connor GT, Fingerlin TE, Hunninghake GM, Schwartz DA, Cho MH
Am J Respir Crit Care Med 2023 Oct 1;208(7):791-801. doi: 10.1164/rccm.202212-2257OC. PMID: 37523715Free PMC Article
Alder JK, Armanios M
Physiol Rev 2022 Oct 1;102(4):1703-1720. Epub 2022 May 9 doi: 10.1152/physrev.00046.2021. PMID: 35532056Free PMC Article
Assad N, Sood A, Campen MJ, Zychowski KE
Curr Environ Health Rep 2018 Dec;5(4):486-498. doi: 10.1007/s40572-018-0219-7. PMID: 30298344Free PMC Article
Sgalla G, Iovene B, Calvello M, Ori M, Varone F, Richeldi L
Respir Res 2018 Feb 22;19(1):32. doi: 10.1186/s12931-018-0730-2. PMID: 29471816Free PMC Article

Clinical prediction guides

Cui F, Sun Y, Xie J, Li D, Wu M, Song L, Hu Y, Tian Y
Eur Respir J 2023 Feb;61(2) Epub 2023 Feb 2 doi: 10.1183/13993003.00777-2022. PMID: 36137588
Silveyra P, Fuentes N, Rodriguez Bauza DE
Adv Exp Med Biol 2021;1304:227-258. doi: 10.1007/978-3-030-68748-9_14. PMID: 34019273Free PMC Article
Saint-Criq V, Lugo-Villarino G, Thomas M
Ageing Res Rev 2021 Mar;66:101235. Epub 2020 Dec 13 doi: 10.1016/j.arr.2020.101235. PMID: 33321253
Allen RJ, Guillen-Guio B, Oldham JM, Ma SF, Dressen A, Paynton ML, Kraven LM, Obeidat M, Li X, Ng M, Braybrooke R, Molina-Molina M, Hobbs BD, Putman RK, Sakornsakolpat P, Booth HL, Fahy WA, Hart SP, Hill MR, Hirani N, Hubbard RB, McAnulty RJ, Millar AB, Navaratnam V, Oballa E, Parfrey H, Saini G, Whyte MKB, Zhang Y, Kaminski N, Adegunsoye A, Strek ME, Neighbors M, Sheng XR, Gudmundsson G, Gudnason V, Hatabu H, Lederer DJ, Manichaikul A, Newell JD Jr, O'Connor GT, Ortega VE, Xu H, Fingerlin TE, Bossé Y, Hao K, Joubert P, Nickle DC, Sin DD, Timens W, Furniss D, Morris AP, Zondervan KT, Hall IP, Sayers I, Tobin MD, Maher TM, Cho MH, Hunninghake GM, Schwartz DA, Yaspan BL, Molyneaux PL, Flores C, Noth I, Jenkins RG, Wain LV
Am J Respir Crit Care Med 2020 Mar 1;201(5):564-574. doi: 10.1164/rccm.201905-1017OC. PMID: 31710517Free PMC Article
Thannickal VJ, Toews GB, White ES, Lynch JP 3rd, Martinez FJ
Annu Rev Med 2004;55:395-417. doi: 10.1146/annurev.med.55.091902.103810. PMID: 14746528

Recent systematic reviews

Ren Y, Zhang Y, Cheng Y, Qin H, Zhao H
Front Cell Infect Microbiol 2024;14:1348685. Epub 2024 May 22 doi: 10.3389/fcimb.2024.1348685. PMID: 38841114Free PMC Article
Hu Y, Li Z, Ren Y, Dai H
Mol Genet Genomic Med 2023 Nov;11(11):e2279. Epub 2023 Oct 2 doi: 10.1002/mgg3.2279. PMID: 37786320Free PMC Article
Luo S, Liang Y, Wong THT, Schooling CM, Au Yeung SL
Int J Epidemiol 2022 Aug 10;51(4):1088-1105. doi: 10.1093/ije/dyac076. PMID: 35445260Free PMC Article
Wu X, Li W, Luo Z, Chen Y
Sci Rep 2021 Dec 14;11(1):24007. doi: 10.1038/s41598-021-03533-z. PMID: 34907291Free PMC Article
Klay D, Hoffman TW, Harmsze AM, Grutters JC, van Moorsel CHM
Eur Respir Rev 2018 Sep 30;27(149) Epub 2018 Jul 11 doi: 10.1183/16000617.0135-2017. PMID: 29997245Free PMC Article

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