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Gm2-gangliosidosis, chronic

MedGen UID:
865425
Concept ID:
C4016988
Finding
Synonym: GM2-GANGLIOSIDOSIS, CHRONIC
 
OMIM®: 606869

Professional guidelines

PubMed

Kaback MM
Eur J Pediatr 2000 Dec;159 Suppl 3:S192-5. doi: 10.1007/pl00014401. PMID: 11216898

Recent clinical studies

Etiology

Kaback MM
Eur J Pediatr 2000 Dec;159 Suppl 3:S192-5. doi: 10.1007/pl00014401. PMID: 11216898
Zelnik N, Khazanov V, Sheinkman A, Karpati AM, Peleg L
Neuropsychobiology 2000;41(3):127-31. doi: 10.1159/000026644. PMID: 10754426
Palmeri S, Mangano L, Battisti C, Malandrini A, Federico A
J Neurol Sci 1992 Jul;110(1-2):215-21. doi: 10.1016/0022-510x(92)90030-o. PMID: 1506862
Paw BH, Tieu PT, Kaback MM, Lim J, Neufeld EF
Am J Hum Genet 1990 Oct;47(4):698-705. PMID: 2220809Free PMC Article
Janz NK, Becker MH
Health Educ Q 1984 Spring;11(1):1-47. doi: 10.1177/109019818401100101. PMID: 6392204

Diagnosis

Pereira CS, Ribeiro H, Pérez-Cabezas B, Cardoso MT, Alegrete N, Gaspar A, Leão-Teles E, Macedo MF
Mol Genet Metab 2018 Sep;125(1-2):161-167. Epub 2018 Jul 18 doi: 10.1016/j.ymgme.2018.07.005. PMID: 30030044
Jamrozik Z, Lugowska A, Gołębiowski M, Królicki L, Mączewska J, Kuźma-Kozakiewicz M
Gene 2013 Sep 25;527(2):679-82. Epub 2013 Jun 29 doi: 10.1016/j.gene.2013.06.030. PMID: 23820084
Walterfang M, Bonnot O, Mocellin R, Velakoulis D
J Inherit Metab Dis 2013 Jul;36(4):687-702. Epub 2013 May 23 doi: 10.1007/s10545-013-9618-y. PMID: 23700255
Federico A, Palmeri S, Malandrini A, Fabrizi G, Mondelli M, Guazzi GC
Dev Neurosci 1991;13(4-5):280-7. doi: 10.1159/000112174. PMID: 1840098
Musarella MA, Raab EL, Rudolph SH, Grabowski GA, Desnick RJ
J Pediatr Ophthalmol Strabismus 1982 Mar-Apr;19(2):80-9. doi: 10.3928/0191-3913-19820301-05. PMID: 6808109

Therapy

Regier DS, Proia RL, D'Azzo A, Tifft CJ
Pediatr Endocrinol Rev 2016 Jun;13 Suppl 1(Suppl 1):663-73. PMID: 27491214Free PMC Article
Clarke JT, Mahuran DJ, Sathe S, Kolodny EH, Rigat BA, Raiman JA, Tropak MB
Mol Genet Metab 2011 Jan;102(1):6-12. Epub 2010 Sep 17 doi: 10.1016/j.ymgme.2010.09.004. PMID: 20926324Free PMC Article
Masciullo M, Santoro M, Modoni A, Ricci E, Guitton J, Tonali P, Silvestri G
J Inherit Metab Dis 2010 Dec;33 Suppl 3:S355-61. Epub 2010 Sep 4 doi: 10.1007/s10545-010-9186-3. PMID: 20821051
Janz NK, Becker MH
Health Educ Q 1984 Spring;11(1):1-47. doi: 10.1177/109019818401100101. PMID: 6392204

Prognosis

Abo-Ouf H, Hooper AW, White EJ, Janse van Rensburg HJ, Trigatti BL, Igdoura SA
Hum Mol Genet 2013 Oct 1;22(19):3960-75. Epub 2013 May 31 doi: 10.1093/hmg/ddt250. PMID: 23727835
Masciullo M, Santoro M, Modoni A, Ricci E, Guitton J, Tonali P, Silvestri G
J Inherit Metab Dis 2010 Dec;33 Suppl 3:S355-61. Epub 2010 Sep 4 doi: 10.1007/s10545-010-9186-3. PMID: 20821051
Kornfeld M
Clin Neuropathol 2008 Sep-Oct;27(5):302-8. doi: 10.5414/npp27302. PMID: 18808061
Sakuraba H, Matsuzawa F, Aikawa S, Doi H, Kotani M, Lin H, Ohno K, Tanaka A, Yamada H, Uyama E
J Hum Genet 2002;47(4):176-83. doi: 10.1007/s100380200020. PMID: 12166653
Philippart M, Carrel RE, Landing BH
Neurochem Res 1995 Nov;20(11):1323-8. doi: 10.1007/BF00992507. PMID: 8786818

Clinical prediction guides

Pereira CS, Ribeiro H, Pérez-Cabezas B, Cardoso MT, Alegrete N, Gaspar A, Leão-Teles E, Macedo MF
Mol Genet Metab 2018 Sep;125(1-2):161-167. Epub 2018 Jul 18 doi: 10.1016/j.ymgme.2018.07.005. PMID: 30030044
Clarke JT, Mahuran DJ, Sathe S, Kolodny EH, Rigat BA, Raiman JA, Tropak MB
Mol Genet Metab 2011 Jan;102(1):6-12. Epub 2010 Sep 17 doi: 10.1016/j.ymgme.2010.09.004. PMID: 20926324Free PMC Article
Masciullo M, Santoro M, Modoni A, Ricci E, Guitton J, Tonali P, Silvestri G
J Inherit Metab Dis 2010 Dec;33 Suppl 3:S355-61. Epub 2010 Sep 4 doi: 10.1007/s10545-010-9186-3. PMID: 20821051
Kornfeld M
Clin Neuropathol 2008 Sep-Oct;27(5):302-8. doi: 10.5414/npp27302. PMID: 18808061
Tropak MB, Mahuran D
FEBS J 2007 Oct;274(19):4951-61. doi: 10.1111/j.1742-4658.2007.06040.x. PMID: 17894780Free PMC Article

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