Analysis of cochleas of animals carrying a mutator allele of the mitochondrial (mt) Polg DNA polymerase. Accumulation of mtDNA mutations is associated with age-related hearing loss. Results provide insight into the role of mtDNA mutations in the pathogenesis of age-related hearing loss.
Someya S, Yamasoba T, Kujoth GC, Pugh TD et al. The role of mtDNA mutations in the pathogenesis of age-related hearing loss in mice carrying a mutator DNA polymerase gamma. Neurobiol Aging 2008 Jul;29(7):1080-92. PMID: 17363114