Table 4.

Recommended Surveillance for Individuals with BPES

System/ConcernEvaluationFrequency
Eyelid
malformation 		Ophthalmic follow upBased on person's age, past procedures, & results of visual acuity testing
POI
  • Endocrinologic & gynecologic follow up to monitor ovarian status
  • Assess effects of hormone replacement therapy for adjustments as needed.
  • Psychological follow up
Individualized, but at least annually

POI = primary ovarian insufficiency

From: Blepharophimosis, Ptosis, and Epicanthus Inversus Syndrome

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