Table 6.

Recommended Surveillance for Individuals with Isolated and Classic Cutis Marmorata Telangiectatica Congenita

System/ConcernEvaluationFrequency
Skin Close monitoring for early signs of impending ulceration of skinAs determined at initial eval
Musculoskeletal Monitoring of limb length & girthAnnually until skeletal maturity
Assessment for pain, weakness, & temperature dysregulationAt each visit
Eyes Ophthalmologic eval to incl measurement of intraocular pressure & consideration of peripheral retinal vascular imagingEvery 6 mos until age 4 yrs, then annually (throughout lifetime) 1 or when there is ocular pain or visible corneal clouding
Self-esteem Monitoring of coping skills related to visible differencesAnnually starting at school age

From: Isolated and Classic Cutis Marmorata Telangiectatica Congenita

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