Full Report

Format

Full Report
Summary (Text)
Summary (XML)

Send to:

Choose Destination

File
Clipboard
Collections

Digestive System Rhabdomyosarcoma

MedGen UID:: 1752521
•Concept ID:: C5419974
•: Neoplastic Process

Definition

A rhabdomyosarcoma arising from an anatomic site in the digestive system. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDigestive System Rhabdomyosarcoma

Disorder of digestive system
- Abnormality of the digestive system
  - Digestive system neoplasm
    - Neoplasm of the gastrointestinal tract
      - Digestive System Soft Tissue Neoplasm
        Digestive System Sarcoma
        Digestive System Rhabdomyosarcoma
        Anus rhabdomyosarcoma
        Esophageal Rhabdomyosarcoma
        Extrahepatic bile duct rhabdomyosarcoma
        Embryonal extrahepatic bile duct rhabdomyosarcoma
        Gallbladder rhabdomyosarcoma
        Liver rhabdomyosarcoma
        Rectum rhabdomyosarcoma

Professional guidelines

PubMed

Dedifferentiated and Undifferentiated Melanomas: Report of 35 New Cases With Literature Review and Proposal of Diagnostic Criteria.

Agaimy A, Stoehr R, Hornung A, Popp J, Erdmann M, Heinzerling L, Hartmann A
Am J Surg Pathol 2021 Feb 1;45(2):240-254. doi: 10.1097/PAS.0000000000001645. PMID: 33428337

Radiation enteritis in children. A retrospective review, clinicopathologic correlation, and dietary management.

Donaldson SS, Jundt S, Ricour C, Sarrazin D, Lemerle J, Schweisguth O
Cancer 1975 Apr;35(4):1167-78. doi: 10.1002/1097-0142(197504)35:4<1167::aid-cncr2820350423>3.0.co;2-y. PMID: 163677

L-asparaginase in the treatment of neoplastic diseases in children.

Jaffe N, Traggis D, Das L, Moloney WC, Hann HW, Kim BS, Nair R
Cancer Res 1971 Jul;31(7):942-9. PMID: 4327086

See all (8)

Recent clinical studies

Etiology

A Practical Approach to Small Round Cell Tumors Involving the Gastrointestinal Tract and Abdomen.

Thway K, Fisher C
Surg Pathol Clin 2023 Dec;16(4):765-778. Epub 2023 Jul 11 doi: 10.1016/j.path.2023.05.012. PMID: 37863565

Primitive neuroectodermal tumor in a child with Currarino syndrome.

Çebi MN, Yılmaz G, Çelikdemir G, Özcan R, Ocak S, Celkan TT, Çomunoğlu N
Turk J Pediatr 2022;64(2):385-388. doi: 10.24953/turkjped.2021.264. PMID: 35611429

ERCP with intracholedocal biopsy for the diagnosis of biliary tract rhabdomyosarcoma in children.

Scottoni F, De Angelis P, Dall'Oglio L, Francalanci P, Monti L, de Ville de Goyet J
Pediatr Surg Int 2013 Jun;29(6):659-62. Epub 2013 Feb 17 doi: 10.1007/s00383-013-3282-z. PMID: 23417547

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Hepatic tumors in the pediatric age group: a distinctive clinicopathologic spectrum.

Dehner LP
Perspect Pediatr Pathol 1978;4:217-68. PMID: 215962

See all (60)

Diagnosis

A Practical Approach to Small Round Cell Tumors Involving the Gastrointestinal Tract and Abdomen.

Thway K, Fisher C
Surg Pathol Clin 2023 Dec;16(4):765-778. Epub 2023 Jul 11 doi: 10.1016/j.path.2023.05.012. PMID: 37863565

Primary Gastric Rhabdomyosarcoma.

Nakamura N, Suzuki R, Takahashi Y, Uwamori A, Masuda M, Fukui T, Noda Y, Tsuta K, Naganuma M
Intern Med 2023 Dec 1;62(23):3483-3488. Epub 2023 Apr 21 doi: 10.2169/internalmedicine.1645-23. PMID: 37081684 Free PMC Article

PAX3-NCOA1 alveolar rhabdomyosarcoma of the tongue: A rare entity with challenging diagnosis and management.

Di Carlo D, Chargari C, Scoazec JY, Cotteret S, Felix A, Moalla S, Temam S, Minard-Colin V
Pediatr Blood Cancer 2021 Nov;68(11):e29288. Epub 2021 Aug 23 doi: 10.1002/pbc.29288. PMID: 34424607

Sarcomas of abdominal organs: computed tomography and magnetic resonance imaging findings.

Qiu LL, Yu RS, Chen Y, Zhang Q
Semin Ultrasound CT MR 2011 Oct;32(5):405-21. doi: 10.1053/j.sult.2011.04.003. PMID: 21963162

Pancreatic rhabdomyosarcoma.

Yasuda I, Adachi S, Kasahara S, Asano T, Shirakami Y, Kato T, Shimokawa K, Moriwaki H
Gastrointest Endosc 2004 Sep;60(3):433-4. doi: 10.1016/s0016-5107(04)01705-5. PMID: 15332041

See all (102)

Therapy

Tissue Compatibility of SN-38-Loaded Anticancer Nanofiber Matrices.

Manzanares A, Restrepo-Perdomo CA, Botteri G, Castillo-Ecija H, Pascual-Pasto G, Cano F, Garcia-Alvarez L, Monterrubio C, Ruiz B, Vazquez-Carrera M, Suñol M, Mora J, Tornero JA, Sosnik A, Carcaboso AM
Adv Healthc Mater 2018 Aug;7(15):e1800255. Epub 2018 Jun 11 doi: 10.1002/adhm.201800255. PMID: 29892999

Severe Hepatic Sinusoidal Obstruction Syndrome in a Child Receiving Vincristine, Actinomycin-D, and Cyclophosphamide for Rhabdomyosarcoma: Successful Treatment with Defibrotide.

Choi A, Kang YK, Lim S, Kim DH, Lim JS, Lee JA
Cancer Res Treat 2016 Oct;48(4):1443-1447. Epub 2016 Mar 30 doi: 10.4143/crt.2016.096. PMID: 27034141 Free PMC Article

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Botryoid rhabdomyosarcoma of the biliary tract in children: a unique case report.

Zampieri N, Camoglio F, Corroppolo M, Cecchetto M, Ornis S, Ottolenghi A
Eur J Cancer Care (Engl) 2006 Dec;15(5):463-6. doi: 10.1111/j.1365-2354.2006.00683.x. PMID: 17177904

Perianal rhabdomyosarcoma in childhood.

Srouji MN, Donaldson MH, Chatten J, Koblenzer CS
Cancer 1976 Aug;38(2):1008-12. doi: 10.1002/1097-0142(197608)38:2<1008::aid-cncr2820380253>3.0.co;2-i. PMID: 824044

See all (50)

Prognosis

Point-of-Care Ultrasound for Gastric Volume Measurement in a Pediatric Patient-Look Beyond the Antrum: A Case Report.

Narayanasamy S, Weethee JB, Rao DS, Mecoli MD
A A Pract 2024 Jul 1;18(7):e01824. Epub 2024 Jul 18 doi: 10.1213/XAA.0000000000001824. PMID: 39023194

PAX3-NCOA1 alveolar rhabdomyosarcoma of the tongue: A rare entity with challenging diagnosis and management.

Di Carlo D, Chargari C, Scoazec JY, Cotteret S, Felix A, Moalla S, Temam S, Minard-Colin V
Pediatr Blood Cancer 2021 Nov;68(11):e29288. Epub 2021 Aug 23 doi: 10.1002/pbc.29288. PMID: 34424607

Successful outcome following resection of metachronous pancreatic metastasis from a rhabdomyosarcoma.

Monge M, Chiavelli H, Pinson J, Papet E, Schwarz L, Tuech JJ
Acta Chir Belg 2021 Oct;121(5):354-356. Epub 2020 Feb 7 doi: 10.1080/00015458.2020.1722927. PMID: 31994975

Perianal rhabdomyosarcoma: report of a case in an infant and review of the literature.

Gökdemir G, Ekmen S, Gungor S, Singer R
Pediatr Dermatol 2013 Jan-Feb;30(1):97-9. Epub 2012 Feb 22 doi: 10.1111/j.1525-1470.2011.01684.x. PMID: 22352996

Hepatic tumors in the pediatric age group: a distinctive clinicopathologic spectrum.

Dehner LP
Perspect Pediatr Pathol 1978;4:217-68. PMID: 215962

See all (59)

Clinical prediction guides

Point-of-Care Ultrasound for Gastric Volume Measurement in a Pediatric Patient-Look Beyond the Antrum: A Case Report.

Narayanasamy S, Weethee JB, Rao DS, Mecoli MD
A A Pract 2024 Jul 1;18(7):e01824. Epub 2024 Jul 18 doi: 10.1213/XAA.0000000000001824. PMID: 39023194

Prevalence of malignant neoplastic oral lesions among children and adolescents: A systematic review and meta-analysis.

de Paula DS, Nóbrega Malta CE, de Brito WH, Mota Lemos JV, Cetira Fillho EL, Gurgel Costa FW, Nunes Alves APN, de Barros Silva PG
Int J Paediatr Dent 2021 Jul;31(4):504-519. Epub 2021 Mar 15 doi: 10.1111/ipd.12765. PMID: 33289182

Dental and craniofacial alterations in long-term survivors of childhood head and neck rhabdomyosarcoma.

Mattos VD, Ferman S, Magalhães DMA, Antunes HS, Lourenço SQC
Oral Surg Oral Med Oral Pathol Oral Radiol 2019 Apr;127(4):272-281. Epub 2018 Dec 21 doi: 10.1016/j.oooo.2018.12.012. PMID: 30685390

Salivary gland-sparing prophylactic pilocarpine treatment has no effect on tumor regrowth after irradiation.

Licht R, Kampinga HH, Coppes RP
Radiat Res 2002 May;157(5):596-8. doi: 10.1667/0033-7587(2002)157[0596:sgsppt]2.0.co;2. PMID: 11966326

Necrotizing sialometaplasia obscuring an underlying malignancy: report of a case.

Poulson TC, Greer RO Jr, Ryser RW
J Oral Maxillofac Surg 1986 Jul;44(7):570-4. doi: 10.1016/s0278-2391(86)80100-8. PMID: 3459842

See all (28)