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Digestive System Sarcoma

MedGen UID:: 1769713
•Concept ID:: C5421281
•: Neoplastic Process

Definition

A sarcoma that arises from the digestive system. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDigestive System Sarcoma

Disorder of digestive system
- Abnormality of the digestive system
  - Digestive system neoplasm
    - Neoplasm of the gastrointestinal tract
      - Digestive System Soft Tissue Neoplasm
        Digestive System Sarcoma
        Anus sarcoma
        Anal Kaposi Sarcoma
        Anus leiomyosarcoma
        Anus rhabdomyosarcoma
        Colorectal Sarcoma
        Colon sarcoma
        Colon Kaposi sarcoma
        Colon leiomyosarcoma
        Colon Liposarcoma
        Colorectal Angiosarcoma
        Colorectal Kaposi sarcoma
        Rectum Kaposi sarcoma
        Colorectal Leiomyosarcoma
        Rectum leiomyosarcoma
        Rectum sarcoma
        Rectum rhabdomyosarcoma
        Digestive System Kaposi Sarcoma
        Appendix Kaposi Sarcoma
        Esophageal Kaposi Sarcoma
        Extrahepatic Bile Duct Kaposi Sarcoma
        Gallbladder Kaposi Sarcoma
        Gastric Kaposi Sarcoma
        AIDS-Related Gastric Kaposi Sarcoma
        Liver Kaposi Sarcoma
        Small Intestinal Kaposi Sarcoma
        Digestive System Leiomyosarcoma
        Appendix Leiomyosarcoma
        Esophagus leiomyosarcoma
        Extrahepatic bile duct leiomyosarcoma
        Gallbladder leiomyosarcoma
        Gastric leiomyosarcoma
        Liver leiomyosarcoma
        Small intestine leiomyosarcoma
        Childhood Small Intestinal Leiomyosarcoma
        Digestive System Rhabdomyosarcoma
        Esophageal Rhabdomyosarcoma
        Extrahepatic bile duct rhabdomyosarcoma
        Embryonal extrahepatic bile duct rhabdomyosarcoma
        Gallbladder rhabdomyosarcoma
        Liver rhabdomyosarcoma
        EBV-Positive Inflammatory Follicular Dendritic Cell/Fibroblastic Reticular Cell Tumor of the Digestive System
        Esophagus sarcoma
        Esophageal Malignant Peripheral Nerve Sheath Tumor
        Esophageal Synovial Sarcoma
        Esophagus liposarcoma
        Extrahepatic bile duct sarcoma
        Gallbladder sarcoma
        Gallbladder angiosarcoma
        Gastric Sarcoma
        Gastric liposarcoma
        Gastric Malignant Gastrointestinal Stromal Tumor
        Gastric Synovial Sarcoma
        Gastrointestinal Clear Cell Sarcoma/Malignant Gastrointestinal Neuroectodermal Tumor
        Liver sarcoma
        Liver angiosarcoma
        Liver extraskeletal osteosarcoma
        Liver fibrosarcoma
        Liver Synovial Sarcoma
        Undifferentiated embryonal sarcoma of the liver
        Pancreas sarcoma
        Small intestinal sarcoma
        Duodenal Extraskeletal Osteosarcoma
        Small Intestinal Angiosarcoma
        Small intestinal fibrosarcoma

Professional guidelines

PubMed

Gastrointestinal stromal tumours: ESMO-EURACAN Clinical Practice Guidelines for diagnosis, treatment and follow-up.

Casali PG, Abecassis N, Aro HT, Bauer S, Biagini R, Bielack S, Bonvalot S, Boukovinas I, Bovee JVMG, Brodowicz T, Broto JM, Buonadonna A, De Álava E, Dei Tos AP, Del Muro XG, Dileo P, Eriksson M, Fedenko A, Ferraresi V, Ferrari A, Ferrari S, Frezza AM, Gasperoni S, Gelderblom H, Gil T, Grignani G, Gronchi A, Haas RL, Hassan B, Hohenberger P, Issels R, Joensuu H, Jones RL, Judson I, Jutte P, Kaal S, Kasper B, Kopeckova K, Krákorová DA, Le Cesne A, Lugowska I, Merimsky O, Montemurro M, Pantaleo MA, Piana R, Picci P, Piperno-Neumann S, Pousa AL, Reichardt P, Robinson MH, Rutkowski P, Safwat AA, Schöffski P, Sleijfer S, Stacchiotti S, Sundby Hall K, Unk M, Van Coevorden F, van der Graaf WTA, Whelan J, Wardelmann E, Zaikova O, Blay JY; ESMO Guidelines Committee and EURACAN
Ann Oncol 2018 Oct 1;29(Suppl 4):iv68-iv78. doi: 10.1093/annonc/mdy095. PMID: 29846513

Epithelioid Hemangioendothelioma: Update on Diagnosis and Treatment.

Rosenberg A, Agulnik M
Curr Treat Options Oncol 2018 Mar 15;19(4):19. doi: 10.1007/s11864-018-0536-y. PMID: 29546487

Pathogenesis, diagnosis, and management of cholangiocarcinoma.

Ilyas SI, Gores GJ
Gastroenterology 2013 Dec;145(6):1215-29. Epub 2013 Oct 15 doi: 10.1053/j.gastro.2013.10.013. PMID: 24140396 Free PMC Article

See all (77)

Recent clinical studies

Etiology

Surgery for Abdominal Well-Differentiated Liposarcoma.

Mansfield SA, Pollock RE, Grignol VP
Curr Treat Options Oncol 2018 Jan 16;19(1):1. doi: 10.1007/s11864-018-0520-6. PMID: 29335908

Malignant tumours of the small intestine.

Reynolds I, Healy P, Mcnamara DA
Surgeon 2014 Oct;12(5):263-70. Epub 2014 Mar 14 doi: 10.1016/j.surge.2014.02.003. PMID: 24637026

Liver transplantation for malignancies.

Eghtesad B, Aucejo F
J Gastrointest Cancer 2014 Sep;45(3):353-62. doi: 10.1007/s12029-014-9590-2. PMID: 24604263

Pathogenesis, diagnosis, and management of cholangiocarcinoma.

Ilyas SI, Gores GJ
Gastroenterology 2013 Dec;145(6):1215-29. Epub 2013 Oct 15 doi: 10.1053/j.gastro.2013.10.013. PMID: 24140396 Free PMC Article

Gastrointestinal stromal tumors: pathology and prognosis at different sites.

Miettinen M, Lasota J
Semin Diagn Pathol 2006 May;23(2):70-83. doi: 10.1053/j.semdp.2006.09.001. PMID: 17193820

See all (560)

Diagnosis

A Practical Approach to Small Round Cell Tumors Involving the Gastrointestinal Tract and Abdomen.

Thway K, Fisher C
Surg Pathol Clin 2023 Dec;16(4):765-778. Epub 2023 Jul 11 doi: 10.1016/j.path.2023.05.012. PMID: 37863565

Multiple Gastrointestinal Angiosarcoma Mimicking Kaposi's Sarcoma.

Saiki T, Harada A, Suekane H, Torisu T
Intern Med 2023 Sep 1;62(17):2577-2578. Epub 2022 Dec 28 doi: 10.2169/internalmedicine.1177-22. PMID: 36575019 Free PMC Article

Intra-abdominal epithelioid angiosarcoma.

Torres Jurado MJ, López Sánchez J, Quiñones Sampedro JE, Muñoz Bellvís L
Rev Esp Enferm Dig 2022 Dec;114(12):744-745. doi: 10.17235/reed.2022.8878/2022. PMID: 35607922

Ewing's Sarcoma of the Pancreas.

Senussi NH, Falk N, Rustagi T
Clin Gastroenterol Hepatol 2022 Apr;20(4):A21-A22. Epub 2021 Aug 24 doi: 10.1016/j.cgh.2021.08.027. PMID: 34450296

Gastrointestinal Myeloid Sarcoma.

Pasricha TS, Abraczinskas D
N Engl J Med 2020 Aug 27;383(9):858. doi: 10.1056/NEJMicm2001235. PMID: 32846064

See all (1398)

Therapy

Advances in immunology and immunotherapy for mesenchymal gastrointestinal cancers.

Li B, Chen H, Yang S, Chen F, Xu L, Li Y, Li M, Zhu C, Shao F, Zhang X, Deng C, Zeng L, He Y, Zhang C
Mol Cancer 2023 Apr 18;22(1):71. doi: 10.1186/s12943-023-01770-6. PMID: 37072770 Free PMC Article

The hepatic bridge.

Sugarbaker PH
Eur J Surg Oncol 2018 Jul;44(7):1083-1086. Epub 2018 Apr 11 doi: 10.1016/j.ejso.2018.03.031. PMID: 29699839

Epithelioid Hemangioendothelioma: Update on Diagnosis and Treatment.

Rosenberg A, Agulnik M
Curr Treat Options Oncol 2018 Mar 15;19(4):19. doi: 10.1007/s11864-018-0536-y. PMID: 29546487

Testing Limits.

Massarotti EM, Sax PE, Compton L, Levy BD, Loscalzo J
N Engl J Med 2016 Oct 6;375(14):1383-1388. doi: 10.1056/NEJMcps1414259. PMID: 27705260

Liver transplantation for malignancies.

Eghtesad B, Aucejo F
J Gastrointest Cancer 2014 Sep;45(3):353-62. doi: 10.1007/s12029-014-9590-2. PMID: 24604263

See all (487)

Prognosis

Primary parotid liposarcoma.

Košec A, Zurak K, Čupić H, Bedeković V
Eur Ann Otorhinolaryngol Head Neck Dis 2019 Oct;136(5):405-408. Epub 2019 Mar 12 doi: 10.1016/j.anorl.2018.01.013. PMID: 30876853

Malignant tumours of the small intestine.

Reynolds I, Healy P, Mcnamara DA
Surgeon 2014 Oct;12(5):263-70. Epub 2014 Mar 14 doi: 10.1016/j.surge.2014.02.003. PMID: 24637026

Pathogenesis, diagnosis, and management of cholangiocarcinoma.

Ilyas SI, Gores GJ
Gastroenterology 2013 Dec;145(6):1215-29. Epub 2013 Oct 15 doi: 10.1053/j.gastro.2013.10.013. PMID: 24140396 Free PMC Article

Sarcomatoid carcinoma of esophagus.

Raza MA, Mazzara PF
Arch Pathol Lab Med 2011 Jul;135(7):945-8. doi: 10.5858/2010-0074-RSR.1. PMID: 21732788

Cutaneous metastatic disease.

Schwartz RA
J Am Acad Dermatol 1995 Aug;33(2 Pt 1):161-82; quiz 183-6. doi: 10.1016/0190-9622(95)90231-7. PMID: 7622642

See all (734)

Clinical prediction guides

Li Fraumeni Syndrome predisposes to gastro-esophageal junction tumours.

Tjandra D, Boussioutas A
Fam Cancer 2024 Mar;23(1):29-33. Epub 2024 Jan 11 doi: 10.1007/s10689-023-00353-0. PMID: 38206485 Free PMC Article

Pancreatic liposarcoma: a case report.

Tanabe M, Matsui H, Higashi M, Tokumitsu Y, Nagano H, Ito K
Abdom Radiol (NY) 2022 Jun;47(6):1912-1916. Epub 2022 May 4 doi: 10.1007/s00261-022-03522-4. PMID: 35507066

The hepatic bridge.

Sugarbaker PH
Eur J Surg Oncol 2018 Jul;44(7):1083-1086. Epub 2018 Apr 11 doi: 10.1016/j.ejso.2018.03.031. PMID: 29699839

Vinyl chloride and the liver.

Sherman M
J Hepatol 2009 Dec;51(6):1074-81. Epub 2009 Oct 1 doi: 10.1016/j.jhep.2009.09.012. PMID: 19836850

Colorectal neoplasia in ulcerative colitis-recent advances.

Wong NA, Harrison DJ
Histopathology 2001 Sep;39(3):221-34. doi: 10.1046/j.1365-2559.2001.01292.x. PMID: 11532032

See all (370)

Recent systematic reviews

Leiomyosarcoma of the rectum: A systematic review of recent literature.

Annicchiarico A, Montali F, Baldinu M, Casali L, Virgilio E, Costi R
J Surg Oncol 2024 Feb;129(2):365-380. Epub 2023 Oct 10 doi: 10.1002/jso.27481. PMID: 37814590

Lacking Immunotherapy Biomarkers for Biliary Tract Cancer: A Comprehensive Systematic Literature Review and Meta-Analysis.

Frega G, Cossio FP, Banales JM, Cardinale V, Macias RIR, Braconi C, Lamarca A
Cells 2023 Aug 19;12(16) doi: 10.3390/cells12162098. PMID: 37626908 Free PMC Article

Primary Angiosarcoma of the Gastrointestinal Tract: A Systematic Review of the Literature.

Schizas D, Mastoraki A, Giannakodimos I, Giannakodimos A, Ziogou A, Katsaros I, Frountzas M, Koutelidakis I, Vassiliu P, Pikoulis E
J Invest Surg 2022 Feb;35(2):400-408. Epub 2020 Dec 21 doi: 10.1080/08941939.2020.1853283. PMID: 33342318

Liposarcoma of oral cavity: Systematic review of cases reported to date and analysis of prognostic factors.

Pontes FSC, de Souza LL, Vulcão ÉNC, de Abreu MC, Menezes SN, Rezende D, Pontes HAR
Head Neck 2020 Sep;42(9):2626-2634. Epub 2020 Apr 20 doi: 10.1002/hed.26160. PMID: 32309895

Liposarcoma of Hypopharynx and Esophagus: a Unique Entity?

Riva G, Sensini M, Corvino A, Garzaro M, Pecorari G
J Gastrointest Cancer 2016 Jun;47(2):135-42. doi: 10.1007/s12029-016-9808-6. PMID: 26875081

See all (19)

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Digestive System Sarcoma

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Recent systematic reviews

Supplemental Content

Table of contents

Practice guidelines

Related information

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