Vulvar trichoepithelioma

MedGen UID:: 274418
•Concept ID:: C1520100
•: Neoplastic Process

Synonyms:	mammalian vulva trichoblastoma; trichoblastoma of mammalian vulva; Vulvar Trichoblastoma; vulvar trichoblastoma; Vulvar Trichoepithelioma; vulvar trichoepithelioma

Monarch Initiative:	MONDO:0002201

Definition

A benign neoplasm that arises from the vulva and is characterized by the presence of nests of monomorphic basaloid cells forming small cysts that contain keratin. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVVulvar trichoepithelioma

Neoplasm by Special Category
- Benign neoplasm
  - Benign epithelial neoplasm
    - Benign epithelial skin neoplasm
      - Benign Germinative Follicular Epithelium Neoplasm
        Trichoepithelioma
        Vulvar trichoepithelioma

Recent clinical studies

Etiology

Vulvar adnexal lesions: a 32-year, single-institution review from Massachusetts General Hospital.

Baker GM, Selim MA, Hoang MP
Arch Pathol Lab Med 2013 Sep;137(9):1237-46. doi: 10.5858/arpa.2012-0434-OA. PMID: 23991738

See all (1)

Diagnosis

Multiple Facial Trichoepitheliomas and Vulval Cysts: Extending the Phenotypic Spectrum in CYLD Cutaneous Syndrome.

Dubois A, Alonso-Sanchez A, Bajaj V, Husain A, Rajan N
JAMA Dermatol 2017 Aug 1;153(8):826-828. doi: 10.1001/jamadermatol.2017.0321. PMID: 28423152 Free PMC Article

Vulvar trichoblastoma: case report and literature review.

Pina A, Sauthier P, Rahimi K
J Low Genit Tract Dis 2015 Jan;19(1):e10-2. doi: 10.1097/LGT.0000000000000010. PMID: 24477174

Trichoepithelioma of the vulva: report of a case and review of the literature.

Heller J, Roche N, Hameed M
J Low Genit Tract Dis 2009 Jul;13(3):186-7. doi: 10.1097/LGT.0b013e31818e0c57. PMID: 19550218

Trichoepithelioma of the vulva. A report of two cases.

Cho D, Woodruff JD
J Reprod Med 1988 Mar;33(3):317-9. PMID: 3361524

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