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Liver neuroendocrine carcinoma

MedGen UID:
474664
•Concept ID:
C3273031
•
Neoplastic Process
Synonyms: Hepatic Neuroendocrine Carcinoma; hepatic neuroendocrine carcinoma; HNEC; liver neuroendocrine cancer; Liver Neuroendocrine Carcinoma; liver neuroendocrine carcinoma; neuroendocrine carcinoma of liver; PHNEC; Primary Hepatic Neuroendocrine Carcinoma; Primary hepatic neuroendocrine carcinoma; primary hepatic neuroendocrine carcinoma; Primary Liver Neuroendocrine Carcinoma; primary liver neuroendocrine carcinoma
SNOMED CT: Primary hepatic neuroendocrine carcinoma (716652006)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
•Concept ID:
CN307044
•
Finding
Source: Orphanet
clinical entity without genetic inheritance.
See: This record
Not genetically inherited (Orphanet)
 
Monarch Initiative: MONDO:0015072
Orphanet: ORPHA100085

Definition

A rare hepatic tumor that may manifest with abdominal pain or fullness, as well as diarrhea or weight loss. More than 10% of cases are asymptomatic and in rare cases a carcinoid syndrome may be observed. The age of onset is variable. The etiology is still unknown but it is thought to arise from Kulchitsky cells originating in the neural crest. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLiver neuroendocrine carcinoma

Professional guidelines

PubMed

Pathologic differential diagnosis of metastatic carcinoma in the liver.
Park JH, Kim JH
Clin Mol Hepatol 2019 Mar;25(1):12-20. Epub 2018 Oct 5 doi: 10.3350/cmh.2018.0067. PMID: 30300991Free PMC Article
Liver Ablation: Best Practice.
Wells SA, Hinshaw JL, Lubner MG, Ziemlewicz TJ, Brace CL, Lee FT Jr
Radiol Clin North Am 2015 Sep;53(5):933-71. doi: 10.1016/j.rcl.2015.05.012. PMID: 26321447Free PMC Article
When should a liver resection be performed in patients with liver metastases from neuroendocrine tumours? A systematic review with practice recommendations.
Lesurtel M, Nagorney DM, Mazzaferro V, Jensen RT, Poston GJ
HPB (Oxford) 2015 Jan;17(1):17-22. Epub 2014 Mar 17 doi: 10.1111/hpb.12225. PMID: 24636662Free PMC Article

Curated

NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Neuroendocrine and Adrenal Tumors, 2023

Supplemental Content

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    Practice guidelines

    • PubMed
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    Curated

    • NCCN, 2023
      NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®), Neuroendocrine and Adrenal Tumors, 2023

    Reviews

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