U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Anterior urethral valve

MedGen UID:
609136
Concept ID:
C0431755
Congenital Abnormality
Synonyms: Congenital anterior urethral valve; Congenital urethral diverticulum
SNOMED CT: Congenital anterior urethral valve (253907008); Congenital urethral diverticulum (253907008); Anterior urethral valve (253907008)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Orphanet: ORPHA435372

Definition

A rare, congenital, fetal lower urinary tract obstruction (LUTO) anomaly occurring in males and characterized by a posteriorly directed semilunar fold arising from the floor of the anterior urethra and causing urethral obstruction during micturition. The valves may be located anywhere distal to the membranous urethra. Clinical presentation is highly variable, depending on age and degree of urinary obstruction, and includes urinary incontinence, urinary retention, weak urinary stream, post-micturitional dribbling, bulging on the ventral penis, urinary tract infection, and urosepsis. [from ORDO]

Term Hierarchy

Professional guidelines

PubMed

Daniel J, Stewart AM, Blair DW
Br J Urol 1968 Oct;40(5):589-91. doi: 10.1111/j.1464-410x.1968.tb11855.x. PMID: 5683574

Recent clinical studies

Etiology

Rawat J, Singh S, Pandey A, Singh S
J Pediatr Surg 2023 Feb;58(2):263-265. Epub 2022 Oct 21 doi: 10.1016/j.jpedsurg.2022.10.036. PMID: 36376124
Menon P, Rao KLN
J Pediatr Urol 2022 Oct;18(5):663.e1-663.e9. Epub 2022 Sep 5 doi: 10.1016/j.jpurol.2022.08.024. PMID: 36123286
Jain P, Prasad A, Jain S
J Pediatr Urol 2021 Feb;17(1):101.e1-101.e9. Epub 2020 Nov 4 doi: 10.1016/j.jpurol.2020.11.002. PMID: 33229229
Kajbafzadeh AM, Hosseini Sharifi SH, Keihani S, Soltani MH, Tajali A, Salavati A, Payabvash S, Mehdizadeh M
Int J Urol 2015 May;22(5):514-9. Epub 2015 Feb 16 doi: 10.1111/iju.12712. PMID: 25689730
Prakash J, Dalela D, Goel A, Singh V, Kumar M, Garg M, Mandal S, Sankhwar SN, Paul S, Singh BP
J Pediatr Urol 2013 Dec;9(6 Pt B):1183-7. Epub 2013 Jun 10 doi: 10.1016/j.jpurol.2013.05.006. PMID: 23764376

Diagnosis

Rawat J, Singh S, Pandey A, Singh S
J Pediatr Surg 2023 Feb;58(2):263-265. Epub 2022 Oct 21 doi: 10.1016/j.jpedsurg.2022.10.036. PMID: 36376124
Menon P, Rao KLN
J Pediatr Urol 2022 Oct;18(5):663.e1-663.e9. Epub 2022 Sep 5 doi: 10.1016/j.jpurol.2022.08.024. PMID: 36123286
Jain P, Prasad A, Jain S
J Pediatr Urol 2021 Feb;17(1):101.e1-101.e9. Epub 2020 Nov 4 doi: 10.1016/j.jpurol.2020.11.002. PMID: 33229229
Reddy D, Shekar P A
Urology 2020 Jun;140:159-161. Epub 2020 Feb 19 doi: 10.1016/j.urology.2020.02.006. PMID: 32087211
Perlman S, Borovitz Y, Ben-Meir D, Hazan Y, Nagar R, Bardin R, Brusilov M, Dekel B, Achiron R, Gilboa Y
Prenat Diagn 2020 Jan;40(2):191-196. Epub 2019 Nov 26 doi: 10.1002/pd.5582. PMID: 31654578

Therapy

Prakash J, Dalela D, Goel A, Singh V, Kumar M, Garg M, Mandal S, Sankhwar SN, Paul S, Singh BP
J Pediatr Urol 2013 Dec;9(6 Pt B):1183-7. Epub 2013 Jun 10 doi: 10.1016/j.jpurol.2013.05.006. PMID: 23764376
Nayyar R, Chavda S, Singh P, Gupta NP
Afr J Paediatr Surg 2011 Jan-Apr;8(1):89-91. doi: 10.4103/0189-6725.78938. PMID: 21478596

Prognosis

Menon P, Rao KLN
J Pediatr Urol 2022 Oct;18(5):663.e1-663.e9. Epub 2022 Sep 5 doi: 10.1016/j.jpurol.2022.08.024. PMID: 36123286
Berte N, Vrillon I, Larmure O, Gomola V, Ayav C, Mazeaud C, Lemelle JL
Prog Urol 2018 Oct;28(12):596-602. Epub 2018 Jul 3 doi: 10.1016/j.purol.2018.06.005. PMID: 29980359
Kajbafzadeh AM, Hosseini Sharifi SH, Keihani S, Soltani MH, Tajali A, Salavati A, Payabvash S, Mehdizadeh M
Int J Urol 2015 May;22(5):514-9. Epub 2015 Feb 16 doi: 10.1111/iju.12712. PMID: 25689730
Obara W, Konda R, Seo T, Ishikawa K, Kinjo M, Fujioka T
Int J Urol 2006 Apr;13(4):395-6. doi: 10.1111/j.1442-2042.2006.01315.x. PMID: 16734857

Clinical prediction guides

Berte N, Vrillon I, Larmure O, Gomola V, Ayav C, Mazeaud C, Lemelle JL
Prog Urol 2018 Oct;28(12):596-602. Epub 2018 Jul 3 doi: 10.1016/j.purol.2018.06.005. PMID: 29980359
Confer SD, Galati V, Frimberger D, Kropp BP
J Pediatr Urol 2010 Oct;6(5):459-62. doi: 10.1016/j.jpurol.2009.06.017. PMID: 20837325

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...