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Childhood Malignant Small Intestinal Neoplasm

MedGen UID:
856663
•Concept ID:
C3897069
•
Neoplastic Process

Definition

A rare malignant small intestinal neoplasm that occurs during childhood. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood Malignant Small Intestinal Neoplasm

Professional guidelines

PubMed

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
The spectrum of celiac disease: epidemiology, clinical aspects and treatment.
Tack GJ, Verbeek WH, Schreurs MW, Mulder CJ
Nat Rev Gastroenterol Hepatol 2010 Apr;7(4):204-13. Epub 2010 Mar 9 doi: 10.1038/nrgastro.2010.23. PMID: 20212505
Small bowel enterocyte abnormalities caused by methotrexate treatment in acute lymphoblastic leukaemia of childhood.
Gwavava NJ, Pinkerton CR, Glasgow JF, Sloan JM, Bridges JM
J Clin Pathol 1981 Jul;34(7):790-5. doi: 10.1136/jcp.34.7.790. PMID: 6943149Free PMC Article

Recent clinical studies

Etiology

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
Clinical aspects of the phosphate transporters NaPi-IIa and NaPi-IIb: mutations and disease associations.
Lederer E, Wagner CA
Pflugers Arch 2019 Jan;471(1):137-148. Epub 2018 Dec 13 doi: 10.1007/s00424-018-2246-5. PMID: 30542787
Coffee and cancer risk: a summary overview.
Alicandro G, Tavani A, La Vecchia C
Eur J Cancer Prev 2017 Sep;26(5):424-432. doi: 10.1097/CEJ.0000000000000341. PMID: 28288025
Intussusception in adults.
Balik AA, Ozturk G, Aydinli B, Alper F, Gumus H, Yildirgan MI, Basoglu M
Acta Chir Belg 2006 Jul-Aug;106(4):409-12. doi: 10.1080/00015458.2006.11679917. PMID: 17017694
Juvenile polyposis.
Desai DC, Neale KF, Talbot IC, Hodgson SV, Phillips RK
Br J Surg 1995 Jan;82(1):14-7. doi: 10.1002/bjs.1800820106. PMID: 7881943

Diagnosis

Clinical Guidelines for Diagnosis and Management of Peutz-Jeghers Syndrome in Children and Adults.
Yamamoto H, Sakamoto H, Kumagai H, Abe T, Ishiguro S, Uchida K, Kawasaki Y, Saida Y, Sano Y, Takeuchi Y, Tajika M, Nakajima T, Banno K, Funasaka Y, Hori S, Yamaguchi T, Yoshida T, Ishikawa H, Iwama T, Okazaki Y, Saito Y, Matsuura N, Mutoh M, Tomita N, Akiyama T, Yamamoto T, Ishida H, Nakayama Y
Digestion 2023;104(5):335-347. Epub 2023 Apr 13 doi: 10.1159/000529799. PMID: 37054692
Malignant rhabdoid tumor of the small intestine in adults: a brief review of the literature and report of a case.
Voglino C, Scheiterle M, Di Mare G, Mariani F, De Stefano A, Ginori A, De Franco L, Ferrara F
Surg Today 2015 Jul;45(7):924-8. Epub 2014 Jun 25 doi: 10.1007/s00595-014-0955-8. PMID: 24957511
Colorectal polyps in childhood.
Thakkar K, Fishman DS, Gilger MA
Curr Opin Pediatr 2012 Oct;24(5):632-7. doi: 10.1097/MOP.0b013e328357419f. PMID: 22890064
Vascular, polypoid, and other lesions of the small bowel.
Yano T, Yamamoto H
Best Pract Res Clin Gastroenterol 2009;23(1):61-74. doi: 10.1016/j.bpg.2008.12.001. PMID: 19258187
Gastrointestinal bleeding in infancy and childhood.
Vinton NE
Gastroenterol Clin North Am 1994 Mar;23(1):93-122. PMID: 8132302

Therapy

Coffee and cancer risk: a summary overview.
Alicandro G, Tavani A, La Vecchia C
Eur J Cancer Prev 2017 Sep;26(5):424-432. doi: 10.1097/CEJ.0000000000000341. PMID: 28288025
Colorectal polyps in childhood.
Thakkar K, Fishman DS, Gilger MA
Curr Opin Pediatr 2012 Oct;24(5):632-7. doi: 10.1097/MOP.0b013e328357419f. PMID: 22890064
The emerging pathogenic and therapeutic importance of the anaplastic lymphoma kinase gene.
Kelleher FC, McDermott R
Eur J Cancer 2010 Sep;46(13):2357-68. Epub 2010 May 5 doi: 10.1016/j.ejca.2010.04.006. PMID: 20451371
Oesophageal replacement in children.
Arul GS, Parikh D
Ann R Coll Surg Engl 2008 Jan;90(1):7-12. doi: 10.1308/003588408X242222. PMID: 18201490Free PMC Article
Tobacco use and cancer causation: association by tumour type.
Kuper H, Boffetta P, Adami HO
J Intern Med 2002 Sep;252(3):206-24. doi: 10.1046/j.1365-2796.2002.01022.x. PMID: 12270001

Prognosis

Malignant rhabdoid tumor of the small intestine in adults: a brief review of the literature and report of a case.
Voglino C, Scheiterle M, Di Mare G, Mariani F, De Stefano A, Ginori A, De Franco L, Ferrara F
Surg Today 2015 Jul;45(7):924-8. Epub 2014 Jun 25 doi: 10.1007/s00595-014-0955-8. PMID: 24957511
Paediatric intestinal cancer and polyposis due to bi-allelic PMS2 mutations: case series, review and follow-up guidelines.
Herkert JC, Niessen RC, Olderode-Berends MJ, Veenstra-Knol HE, Vos YJ, van der Klift HM, Scheenstra R, Tops CM, Karrenbeld A, Peters FT, Hofstra RM, Kleibeuker JH, Sijmons RH
Eur J Cancer 2011 May;47(7):965-82. Epub 2011 Mar 4 doi: 10.1016/j.ejca.2011.01.013. PMID: 21376568
Vascular, polypoid, and other lesions of the small bowel.
Yano T, Yamamoto H
Best Pract Res Clin Gastroenterol 2009;23(1):61-74. doi: 10.1016/j.bpg.2008.12.001. PMID: 19258187
Multifocal atrophic gastritis and gastric carcinoma.
Faraji EI, Frank BB
Gastroenterol Clin North Am 2002 Jun;31(2):499-516. doi: 10.1016/s0889-8553(02)00008-0. PMID: 12134615
Non-Hodgkin's lymphomas in Asia.
Shih LY, Liang DC
Hematol Oncol Clin North Am 1991 Oct;5(5):983-1001. PMID: 1938764

Clinical prediction guides

Italian cancer figures--Report 2015: The burden of rare cancers in Italy.
AIRTUM Working Group, Busco S, Buzzoni C, Mallone S, Trama A, Castaing M, Bella F, Amodio R, Bizzoco S, Cassetti T, Cirilli C, Cusimano R, De Angelis R, Fusco M, Gatta G, Gennaro V, Giacomin A, Giorgi Rossi P, Mangone L, Mannino S, Rossi S, Pierannunzio D, Tavilla A, Tognazzo S, Tumino R, Vicentini M, Vitale MF, Crocetti E, Dal Maso L
Epidemiol Prev 2016 Jan-Feb;40(1 Suppl 2):1-120. doi: 10.19191/EP16.1S2.P001.035. PMID: 26951748
A completely isolated intestinal duplication cyst mimicking ovarian cyst torsion in an adult.
Park JY, Her KH, Kim BS, Maeng YH
World J Gastroenterol 2014 Jan 14;20(2):603-6. doi: 10.3748/wjg.v20.i2.603. PMID: 24574732Free PMC Article
Diversity of the clinical presentation of the MMR gene biallelic mutations.
Bougeard G, Olivier-Faivre L, Baert-Desurmont S, Tinat J, Martin C, Bouvignies E, Vasseur S, Huet F, Couillault G, Vabres P, Le Pessot F, Chapusot C, Malka D, Bressac-de Paillerets B, Tosi M, Frebourg T
Fam Cancer 2014 Mar;13(1):131-5. doi: 10.1007/s10689-013-9676-1. PMID: 24068316
Comparison of short bowel syndrome acquired early in life and during adolescence.
Bruzoni M, Sudan DL, Cusick RA, Thompson JS
Transplantation 2008 Jul 15;86(1):63-6. doi: 10.1097/TP.0b013e3181734995. PMID: 18622279
Peutz-Jeghers syndrome: case report and literature review.
Georgescu EF, Stănescu L, Simionescu C, Georgescu I, Ionescu R, Florescu G
Rom J Morphol Embryol 2008;49(2):241-5. PMID: 18516333

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