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Abnormal renal glomerulus morphology

MedGen UID:: 871392
•Concept ID:: C4025889
•: Anatomical Abnormality

Synonyms:	Abnormality of renal glomerulus morphology; Morphologic abnormality of the renal glomerulus

HPO:	HP:0000095

Definition

A structural anomaly of the glomerulus. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVAbnormal renal glomerulus morphology

Abnormality of the urinary system
- Abnormality of the upper urinary tract
  - Abnormality of the kidney
    - Abnormal renal morphology
      - Abnormal nephron morphology
        Abnormal renal corpuscle morphology
        Abnormal renal glomerulus morphology
        Abnormal glomerular capillary morphology
        Abnormal glomerular capillary lumen morphology
        Deflation of the glomerular tuft
        Glomerular capillary collapse
        Glomerular capillary congestion
        Glomerular capillary microaneurysm
        Glomerular fibrin thrombus
        Glomerular hyaline pseudothrombus
        Glomerular karyhorrhectic debris
        Glomerular lipoprotein thrombus
        Abnormal glomerular endothelial cell morphology
        Glomerular endothelial tubuloreticular inclusion
        Glomerular endotheliosis
        Loss of glomerular endothelial cell fenestration
        Glomerular capillary wall duplication with cellular interposition
        Glomerular capillary wall duplication without cellular interposition
        Glomerular endocapillary hypercellularity
        Glomerular endocapillary leukocyte hypercellularity
        Glomerular fibrinoid necrosis
        Thickening of glomerular capillary wall
        Abnormal glomerular mesangium morphology
        Abnormal glomerular mesangial cellularity
        Mesangial cell loss
        Mesangial hypercellularity
        Abnormal glomerular mesangial matrix morphology
        Global mesangial sclerosis
        Mesangial matrix expansion
        Mesangiolysis
        Nodular mesangiosclerosis
        Diffuse mesangial sclerosis
        Mesangial fibril deposition
        Mesangial amyloid deposition
        Mesangial fibrillary deposits
        Mesangial immunotactoid deposits
        Mesangial microfibril deposition
        Mesangial hyaline deposition
        Mesangial Immune complex deposition
        Paramesangial deposits
        Glomerular deposits
        Glomerular C3 deposition
        Glomerular capillary wire loop deposits
        Glomerular fibronectin deposits
        Glomerular subendothelial electron-dense deposits
        Glomerular subepithelial deposits
        Abnormal glomerular basement membrane morphology
        Fibrillar glomerular subepithelial deposits
        Glomerular hyaline subepithelial deposits
        Glomerular subepithelial immune-complex deposits
        IgA deposition in the glomerulus
        Glomerular extracapillary hypercellularity
        Glomerular immune-complex deposition
        Glomerular PLA2R immune-complex deposition
        Glomerular sclerosis
        Focal segmental glomerulosclerosis
        Chronic rejection of renal transplant
        Focal Segmental Glomerulosclerosis Cellular Variant
        Focal Segmental Glomerulosclerosis Collapsing Variant
        Focal Segmental Glomerulosclerosis Perihilar Variant
        Focal Segmental Glomerulosclerosis Tip Lesion Variant
        Focal Segmental Glomerulosclerosis, Not Otherwise Specified
        HIV-associated nephropathy
        Inherited focal segmental glomerulosclerosis
        Obesity Related Glomerulopathy
        Primary focal segmental glomerulosclerosis
        Secondary Focal Segmental Glomerulosclerosis
        Global glomerulosclerosis
        Glomerular obsolescence
        Segmental glomerulosclerosis
        Perihilar segmental glomerulosclerosis
        Segmental glomerulosclerosis away from the vascular and tubular poles
        Tip variant segmental glomerulosclerosis
        Glomerulomegaly
        Glomerulopathy
        Collapsing Glomerulopathy
        Glomerulocystic Disease
        Idiopathic Membranous Glomerulopathy
        Membranous Nephropathy - Secondary
        Primary Collapsing Glomerulopathy
        Secondary Collapsing Glomerulopathy
        Tip Lesion Glomerulopathy
        Multiple glomerular cysts
        Obliterative abnormality of the renal glomerulus
        Glomerular hyalinosis
        Glomerular hyalinosis at the tubular pole
        Glomerular hyalinosis away from the vascular and tubular poles
        Perihilar glomerular hyalinosis
        Renal juxtaglomerular cell hypertrophy/hyperplasia

Conditions with this feature

Hypotrichosis-lymphedema-telangiectasia-renal defect syndrome

MedGen UID:: 1373459
•Concept ID:: C4317151
•: Disease or Syndrome

Hypotrichosis-lymphedema-telangiectasia-renal defect syndrome is an autosomal dominant disorder characterized by these 4 features, which begin in early childhood and are progressive (summary by Moalem et al., 2015).

See: Condition Record

Hypotrichosis-lymphedema-telangiectasia-renal defect syndrome

Professional guidelines

PubMed

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