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Aortic arch syndrome

MedGen UID:
1616
•Concept ID:
C0003490
•
Disease or Syndrome
Synonyms: Aortic Arch Syndrome; Aortic Arch Syndromes; Syndrome, Aortic Arch; Syndromes, Aortic Arch
SNOMED CT: Aortic arch syndrome (359789008)

Definition

A syndrome resulting from structural defects of the arteries that arise from the aortic arch. Signs and symptoms include weakness, dizziness, arm numbness, blurred vision and transient ischemic attacks. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAortic arch syndrome

Professional guidelines

PubMed

Branchial arteritis in the aortic arch syndrome. A roentgen and differential diagnostic study.
EDLING NP, NYSTROM B, SELDINGER SI
Acta Radiol (Stockh) 1961 Jun;55:417-32. doi: 10.3109/00016926109175138. PMID: 13725722

Recent clinical studies

Etiology

Stroke and Transient Ischemic Attack in Takayasu's Arteritis: A Systematic Review and Meta-analysis.
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269
Large-vessel involvement in giant cell arteritis and polymyalgia rheumatica.
Muratore F, Pazzola G, Pipitone N, Boiardi L, Salvarani C
Clin Exp Rheumatol 2014 May-Jun;32(3 Suppl 82):S106-11. Epub 2014 May 15 PMID: 24854380
MRI and FDG-PET in the assessment of inflammatory aortic arch syndrome in complicated courses of giant cell arteritis.
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Disease pattern in cranial and large-vessel giant cell arteritis.
Brack A, Martinez-Taboada V, Stanson A, Goronzy JJ, Weyand CM
Arthritis Rheum 1999 Feb;42(2):311-7. doi: 10.1002/1529-0131(199902)42:2<311::AID-ANR14>3.0.CO;2-F. PMID: 10025926
Extrathoracic management of aortic arch syndrome.
Criado FJ
Br J Surg 1982 Jun;69 Suppl:S45-51. doi: 10.1002/bjs.1800691316. PMID: 7044468

Diagnosis

Extracranial giant cell arteritis: A narrative review.
Lensen KD, Voskuyl AE, Comans EF, van der Laken CJ, Smulders YM
Neth J Med 2016 Jun;74(5):182-92. PMID: 27323671
Polymyalgia rheumatica and giant-cell arteritis.
Salvarani C, Cantini F, Hunder GG
Lancet 2008 Jul 19;372(9634):234-45. doi: 10.1016/S0140-6736(08)61077-6. PMID: 18640460
Congenital aortic thrombosis with complete obliteration of the aortic arch and the great vessels.
Ahmadi A, Fürste HO, Pringsheim W, Spillner G, Keller KM, Böhm N, Schmidt-Redemann B
Thorac Cardiovasc Surg 1983 Aug;31(4):256-9. doi: 10.1055/s-2007-1021992. PMID: 6195766
Aortic arch syndrome.
Thompson BW, Read RC, Campbell GS
Arch Surg 1969 May;98(5):607-11. doi: 10.1001/archsurg.1969.01340110099010. PMID: 5778697
Aortic arch syndrome.
Shah HS, Shah RM
J Assoc Physicians India 1968 Dec;16(12):949-54. PMID: 4889946

Therapy

Extracranial giant cell arteritis: A narrative review.
Lensen KD, Voskuyl AE, Comans EF, van der Laken CJ, Smulders YM
Neth J Med 2016 Jun;74(5):182-92. PMID: 27323671
Stroke and Transient Ischemic Attack in Takayasu's Arteritis: A Systematic Review and Meta-analysis.
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269
Polymyalgia rheumatica and giant-cell arteritis.
Salvarani C, Cantini F, Hunder GG
Lancet 2008 Jul 19;372(9634):234-45. doi: 10.1016/S0140-6736(08)61077-6. PMID: 18640460
MRI and FDG-PET in the assessment of inflammatory aortic arch syndrome in complicated courses of giant cell arteritis.
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Extrathoracic management of aortic arch syndrome.
Criado FJ
Br J Surg 1982 Jun;69 Suppl:S45-51. doi: 10.1002/bjs.1800691316. PMID: 7044468

Prognosis

Extracranial giant cell arteritis: A narrative review.
Lensen KD, Voskuyl AE, Comans EF, van der Laken CJ, Smulders YM
Neth J Med 2016 Jun;74(5):182-92. PMID: 27323671
Large-vessel involvement in giant cell arteritis and polymyalgia rheumatica.
Muratore F, Pazzola G, Pipitone N, Boiardi L, Salvarani C
Clin Exp Rheumatol 2014 May-Jun;32(3 Suppl 82):S106-11. Epub 2014 May 15 PMID: 24854380
Polymyalgia rheumatica and giant-cell arteritis.
Salvarani C, Cantini F, Hunder GG
Lancet 2008 Jul 19;372(9634):234-45. doi: 10.1016/S0140-6736(08)61077-6. PMID: 18640460
MRI and FDG-PET in the assessment of inflammatory aortic arch syndrome in complicated courses of giant cell arteritis.
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Giant cell arteritis and its variants.
Gerber NJ
Eur Neurol 1984;23(6):410-20. doi: 10.1159/000115723. PMID: 6510442

Clinical prediction guides

Stroke and Transient Ischemic Attack in Takayasu's Arteritis: A Systematic Review and Meta-analysis.
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269
MRI and FDG-PET in the assessment of inflammatory aortic arch syndrome in complicated courses of giant cell arteritis.
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Takayasu's disease and atherosclerosis.
Jorens PG, Williame LM, Tombeur JP, Kockx MM, Parizel GA, Zeyen TG
J Cardiovasc Surg (Torino) 1991 May-Jun;32(3):373-5. PMID: 1676030
Observations on continuous murmurs over partially obstructed arteries; an explanation for the continuous murmur found in the aortic arch syndrome.
MYERS JD, MURDAUGH HV, MCINTOSH HD, BLAISDELL RK
AMA Arch Intern Med 1956 Jun;97(6):726-37. doi: 10.1001/archinte.1956.00250240078007. PMID: 13312714

Recent systematic reviews

Stroke and Transient Ischemic Attack in Takayasu's Arteritis: A Systematic Review and Meta-analysis.
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269

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