Neoplasm of the adrenal gland

MedGen UID:: 1352
•Concept ID:: C0001624
•: Neoplastic Process

Synonym:	Adrenal gland neoplasm
SNOMED CT:	Neoplasm of adrenal gland (127021009); Adrenal tumor (127021009); Tumor of adrenal gland (127021009)

HPO:	HP:0100631
Monarch Initiative:	MONDO:0021227
Orphanet:	ORPHA100091

Definition

A tumor (abnormal growth of tissue) of the adrenal gland. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVNeoplasm of the adrenal gland

Pathological Conditions, Signs and Symptoms
- Pathological process
  - Disease
    - Disorder by Site
      - Disorder of endocrine system
        Disorder of adrenal gland
        Neoplasm of the adrenal gland
        Adrenal cortex carcinoma
        Adrenal Cortical Carcinoma by AJCC v7 Stage
        Stage I Adrenal Cortical Carcinoma AJCC v7
        Stage II Adrenal Cortical Carcinoma AJCC v7
        Stage III Adrenal Cortical Carcinoma AJCC v7
        Stage IV Adrenal Cortical Carcinoma AJCC v7
        Adrenal Cortical Carcinoma by AJCC v8 Stage
        Stage I Adrenal Cortical Carcinoma AJCC v8
        Stage II Adrenal Cortical Carcinoma AJCC v8
        Stage III Adrenal Cortical Carcinoma AJCC v8
        Stage IV Adrenal Cortical Carcinoma AJCC v8
        Adrenal Cortical Low Grade Carcinoma
        Adrenal Cortical Sarcomatoid Carcinoma
        Metastatic Adrenal Cortical Carcinoma
        Locally Advanced Adrenal Cortical Carcinoma
        Recurrent Adrenal Cortical Carcinoma
        Unresectable Adrenal Cortical Carcinoma
        Adrenal cortex neoplasm
        Adrenal Cortical Sex Cord-Stromal Tumor
        Adrenocortical adenoma
        Adrenal Cortical Clear Cell Adenoma
        Adrenal Cortical Compact Cell Adenoma
        Adrenal Cortical Glomerulosa Cell Adenoma
        Adrenal Cortical Mixed Cell Adenoma
        Adrenal Cortical Oncocytic Adenoma
        Aldosterone-producing adrenal cortex adenoma
        Cortisol-producing adrenal cortex adenoma
        Non-functioning adrenal cortex adenoma
        Non-secretory adrenocortical adenoma
        Pigmented Adrenal Cortical Adenoma
        Secretory adrenocortical adenoma
        Sex hormone-producing adrenal cortex adenoma
        Benign Adrenal Cortical Neoplasm
        Adrenal Cortical Adenomatoid Tumor
        Malignant tumor of adrenal cortex
        Metastatic Carcinoma in the Adrenal Cortex
        Adrenal gland cancer
        Adrenal Gland Lymphoma
        Adrenal Gland Sarcoma
        Adrenal Gland Angiosarcoma
        Adrenal medulla cancer
        Adrenal gland ganglioneuroblastoma
        Adrenal gland neuroblastoma
        Malignant adrenal gland pheochromocytoma
        Metastatic carcinoma in the adrenal medulla
        Adrenal leiomyoma
        Benign neoplasm of adrenal gland
        Benign neoplasm of adrenal medulla
        Adrenal Gland Ganglioneuroma
        Adrenal Gland Schwannoma
        Benign adrenal gland pheochromocytoma
        Carney complex
        Carney complex type 2
        Carney complex, type 1
        Familial hyperaldosteronism type II
        Multiple endocrine neoplasia type 2A
        Multiple endocrine neoplasia type 2B
        Multiple endocrine neoplasia, type 1
        Neoplasm of the adrenal medulla
        Adrenal pheochromocytoma
        Adrenal Gland Composite Pheochromocytoma
        Childhood adrenal gland pheochromocytoma
        Hereditary Adrenal Gland Pheochromocytoma
        Recurrent Adrenal Gland Pheochromocytoma
        Refractory Adrenal Gland Pheochromocytoma
        Regional Adrenal Gland Pheochromocytoma
        Unresectable Adrenal Gland Pheochromocytoma
        Pituitary dermoid and epidermoid cysts
        Von Hippel-Lindau syndrome

Professional guidelines

PubMed

European Society of Endocrinology clinical practice guidelines on the management of adrenal incidentalomas, in collaboration with the European Network for the Study of Adrenal Tumors.

Fassnacht M, Tsagarakis S, Terzolo M, Tabarin A, Sahdev A, Newell-Price J, Pelsma I, Marina L, Lorenz K, Bancos I, Arlt W, Dekkers OM
Eur J Endocrinol 2023 Jul 20;189(1):G1-G42. doi: 10.1093/ejendo/lvad066. PMID: 37318239

Personalized Management of Pheochromocytoma and Paraganglioma.

Nölting S, Bechmann N, Taieb D, Beuschlein F, Fassnacht M, Kroiss M, Eisenhofer G, Grossman A, Pacak K
Endocr Rev 2022 Mar 9;43(2):199-239. doi: 10.1210/endrev/bnab019. PMID: 34147030 Free PMC Article

Management of Neuroblastoma in Pediatric Patients.

Croteau N, Nuchtern J, LaQuaglia MP
Surg Oncol Clin N Am 2021 Apr;30(2):291-304. Epub 2021 Feb 10 doi: 10.1016/j.soc.2020.11.010. PMID: 33706901

See all (1216)

Recent clinical studies

Diagnosis

Adrenal myelolipoma: a comprehensive review.

Decmann Á, Perge P, Tóth M, Igaz P
Endocrine 2018 Jan;59(1):7-15. Epub 2017 Nov 21 doi: 10.1007/s12020-017-1473-4. PMID: 29164520

Adrenocortical carcinoma presenting with a peritoneal effusion.

Arvanitis LD, Pitelka LA, Gattuso P
Diagn Cytopathol 2010 Jul;38(7):514-6. doi: 10.1002/dc.21261. PMID: 19941369

See all (2)

Clinical prediction guides

Whole-genome and transcriptome analysis of advanced adrenocortical cancer highlights multiple alterations affecting epigenome and DNA repair pathways.

Lavoie JM, Csizmok V, Williamson LM, Culibrk L, Wang G, Marra MA, Laskin J, Jones SJM, Renouf DJ, Kollmannsberger CK
Cold Spring Harb Mol Case Stud 2022 Apr;8(3) Epub 2022 Apr 28 doi: 10.1101/mcs.a006148. PMID: 35483882 Free PMC Article

Adrenal myelolipoma: a comprehensive review.

Decmann Á, Perge P, Tóth M, Igaz P
Endocrine 2018 Jan;59(1):7-15. Epub 2017 Nov 21 doi: 10.1007/s12020-017-1473-4. PMID: 29164520

See all (2)

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Neoplasm of the adrenal gland

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Diagnosis

Clinical prediction guides

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Practice guidelines

Consumer resources

Reviews

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