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Peripheral nervous system cancer

MedGen UID:: 155556
•Concept ID:: C0751428
•: Neoplastic Process

Synonyms:	Peripheral Nerve Neoplasms, Malignant; Peripheral Nervous System Malignant Neoplasms
SNOMED CT:	Peripheral nerve cancer (254986007); Cancer of peripheral nerve (254986007); Malignant tumor of peripheral nerve (254986007)

Monarch Initiative:	MONDO:0021089

Definition

Malignant growth of cells in the peripheral nervous system (PNS)or Autonomic Nervous System (ANS), without specification as to location [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVPeripheral nervous system cancer

Pathological Conditions, Signs and Symptoms
- Pathological process
  - Disease
    - Neoplasm
      - Malignant neoplastic disease
        Malignant neoplasm of nervous system
        Peripheral nervous system cancer
        Granular cell cancer
        Malignant cutaneous granular cell skin tumor
        Malignant gastric granular cell tumor
        Malignant peripheral nerve sheath tumor
        Adult malignant schwannoma
        Cervical Malignant Peripheral Nerve Sheath Tumor
        Childhood malignant schwannoma
        Epithelioid malignant peripheral nerve sheath tumor
        Epithelioid Malignant Peripheral Nerve Sheath Tumor of the Skin
        Recurrent Epithelioid Malignant Peripheral Nerve Sheath Tumor
        Refractory Epithelioid Malignant Peripheral Nerve Sheath Tumor
        Esophageal Malignant Peripheral Nerve Sheath Tumor
        High Grade Malignant Peripheral Nerve Sheath Tumor
        Intraocular Malignant Peripheral Nerve Sheath Tumor
        Low Grade Malignant Peripheral Nerve Sheath Tumor
        Malignant cardiac peripheral nerve sheath neoplasm
        Malignant glandular tumor of peripheral nerve sheath
        Malignant melanocytic neoplasm of the peripheral nerve sheath
        Malignant melanocytic peripheral nerve sheath tumor of mediastinum
        Melanotic psammomatous malignant peripheral nerve sheath tumor
        Malignant perineurioma
        Malignant Peripheral Nerve Sheath Tumor of the Skin
        Malignant Peripheral Nerve Sheath Tumor with Mesenchymal Differentiation
        Malignant triton tumor
        Mediastinal Malignant Peripheral Nerve Sheath Tumor
        Metastatic Malignant Peripheral Nerve Sheath Tumor
        Advanced Malignant Peripheral Nerve Sheath Tumor
        Locally Advanced Malignant Peripheral Nerve Sheath Tumor
        NF1-Associated Malignant Peripheral Nerve Sheath Tumor
        Penile Malignant Peripheral Nerve Sheath Tumor
        Radiation-Induced Malignant Peripheral Nerve Sheath Tumor
        Recurrent Malignant Peripheral Nerve Sheath Tumor
        Refractory Malignant Peripheral Nerve Sheath Tumor
        Sinonasal Malignant Peripheral Nerve Sheath Tumor
        Sporadic Malignant Peripheral Nerve Sheath Tumor
        Thyroid Gland Malignant Peripheral Nerve Sheath Tumor
        Unresectable Malignant Peripheral Nerve Sheath Tumor
        Metastatic Paraganglioma
        Malignant adrenal gland pheochromocytoma
        Metastatic Adrenal Gland Composite Pheochromocytoma
        Metastatic Extra-Adrenal Paraganglioma
        Malignant carotid body paraganglioma
        Malignant jugulotympanic paraganglioma
        Metastatic Bladder Paraganglioma
        Metastatic Cardiac Paraganglioma
        Metastatic Intrathoracic Paravertebral Paraganglioma
        Peripheral ganglioneuroblastoma
        Adrenal gland ganglioneuroblastoma
        Adrenal Gland Ganglioneuroblastoma, Intermixed
        Adrenal Gland Ganglioneuroblastoma, Nodular
        Mediastinum ganglioneuroblastoma
        Peripheral Neuroblastoma
        Mediastinum neuroblastoma
        Neuroblastoma of the Adrenal Gland and Sympathetic Nervous System
        Adrenal gland neuroblastoma
        Peripheral primitive neuroectodermal tumor
        Askin tumor
        Localized Askin Tumor
        Recurrent Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor
        Localized Peripheral Primitive Neuroectodermal Tumor
        Localized Peripheral Primitive Neuroectodermal Tumor of Bone
        Neuroblastoma
        Cerebral neuroblastoma
        Childhood Neuroblastoma
        Congenital neuroblastoma
        Differentiating neuroblastoma
        Esthesioneuroblastoma
        Extracranial neuroblastoma
        Ganglioneuroblastoma
        Hereditary Neuroblastoma
        High Risk Neuroblastoma
        Localized neuroblastoma
        Metastatic Neuroblastoma
        Neuroblastoma, susceptibility to, 1
        Neuroblastoma, susceptibility to, 2
        Neuroblastoma, susceptibility to, 3
        Poorly Differentiated Neuroblastoma
        Recurrent Neuroblastoma
        Refractory Neuroblastoma
        Regional Neuroblastoma
        Resectable Neuroblastoma
        Retinoblastoma
        Sellar Neuroblastoma
        Stage 1 Neuroblastoma
        Stage 2 Neuroblastoma
        Stage 3 Neuroblastoma
        Stage 4 Neuroblastoma
        Undifferentiated Neuroblastoma
        Unresectable Neuroblastoma
        Peripheral primitive neuroectodermal tumor of bone
        Metastatic Peripheral Primitive Neuroectodermal Tumor of Bone
        Recurrent Peripheral Primitive Neuroectodermal Tumor of Bone
        Peripheral primitive neuroectodermal tumor of soft tissues
        Peripheral Primitive Neuroectodermal Tumor of the Kidney
        Recurrent Peripheral Primitive Neuroectodermal Tumor
        Refractory Peripheral Primitive Neuroectodermal Tumor

Professional guidelines

PubMed

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Med Clin North Am 2019 Nov;103(6):1035-1054. doi: 10.1016/j.mcna.2019.07.004. PMID: 31582003

Health Supervision for Children With Neurofibromatosis Type 1.

Miller DT, Freedenberg D, Schorry E, Ullrich NJ, Viskochil D, Korf BR; COUNCIL ON GENETICS; AMERICAN COLLEGE OF MEDICAL GENETICS AND GENOMICS
Pediatrics 2019 May;143(5) doi: 10.1542/peds.2019-0660. PMID: 31010905

Clinical practice guidelines on the evidence-based use of integrative therapies during and after breast cancer treatment.

Greenlee H, DuPont-Reyes MJ, Balneaves LG, Carlson LE, Cohen MR, Deng G, Johnson JA, Mumber M, Seely D, Zick SM, Boyce LM, Tripathy D
CA Cancer J Clin 2017 May 6;67(3):194-232. Epub 2017 Apr 24 doi: 10.3322/caac.21397. PMID: 28436999 Free PMC Article

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Recent clinical studies

Etiology

Association between sociodemographic variables and delayed patient presentation among surgical neuro-oncology patients in Mexico City: a single institution experience.

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J Neurooncol 2025 Jan;171(1):191-199. Epub 2024 Sep 24 doi: 10.1007/s11060-024-04827-8. PMID: 39316314 Free PMC Article

Inhibition of the SK-N-MC human neuroblastoma cell line in vivo and in vitro by a novel nutrient mixture.

Waheed Roomi M, Kalinovsky T, Roomi NW, Niedzwiecki A, Rath M
Oncol Rep 2013 May;29(5):1714-20. Epub 2013 Feb 27 doi: 10.3892/or.2013.2307. PMID: 23446555 Free PMC Article

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Therapy

Inhibition of the SK-N-MC human neuroblastoma cell line in vivo and in vitro by a novel nutrient mixture.

Waheed Roomi M, Kalinovsky T, Roomi NW, Niedzwiecki A, Rath M
Oncol Rep 2013 May;29(5):1714-20. Epub 2013 Feb 27 doi: 10.3892/or.2013.2307. PMID: 23446555 Free PMC Article

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Prognosis

Inhibition of the SK-N-MC human neuroblastoma cell line in vivo and in vitro by a novel nutrient mixture.

Waheed Roomi M, Kalinovsky T, Roomi NW, Niedzwiecki A, Rath M
Oncol Rep 2013 May;29(5):1714-20. Epub 2013 Feb 27 doi: 10.3892/or.2013.2307. PMID: 23446555 Free PMC Article

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Peripheral nervous system cancer

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Therapy

Prognosis

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